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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
TERMINOLOGY
Synonyms
- Adult-onset Still disease (AOSD), Wissler-Fanconi syndrome
Definitions
- Systemic inflammatory disease, featuring triad
- Quotidian fevers (spiking, daily)
- Evanescent rash
- Chronic oligoarthritis or polyarthritis
- Considered adult continuum of systemic juvenile idiopathic arthritis (SJIA)
- Systemic inflammatory disease, featuring triad
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
Diagnostic Criteria (After Yamaguchi)
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Mitrovic S et al: Clinical phenotypes of adult-onset still's disease: new insights from pathophysiology and literature findings. J Clin Med. 10(12):2633, 2021
- Zhou X et al: FDG PET/CT used in identifying adult-onset Still's disease in connective tissue diseases. Clin Rheumatol. 39(9):2735-42, 2020
- Lebrun D et al: Validation of the Fautrel classification criteria for adult-onset Still's disease. Semin Arthritis Rheum. 47(4):578-85, 2018
- Dong MJ et al: 18F-FDG PET/CT in patients with adult-onset Still's disease. Clin Rheumatol. 34(12):2047-56, 2015
- Kadavath S et al: Adult-onset Still's disease-pathogenesis, clinical manifestations, and new treatment options. Ann Med. 47(1):6-14, 2015
- Manzini CU et al: Elevated troponin serum levels in adult onset Still's disease. Case Rep Rheumatol. 2015:732095, 2015
- Hayem F: Is Still's disease an autoinflammatory syndrome? Joint Bone Spine. 76(1):7-9, 2009
- Jadhav P et al: Myocarditis in adult onset Stills disease. Int J Rheum Dis. 12(3):272-4, 2009
- Lee SW et al: The mid-range of the adjusted level of ferritin can predict the chronic course in patients with adult onset Still's disease. J Rheumatol. 36(1):156-62, 2009
- Efthimiou P et al: Autoinflammatory syndromes and infections: pathogenetic and clinical implications. Clin Exp Rheumatol. 26(1 Suppl 48):S53-61, 2008
- Fautrel B: Adult-onset Still disease. Best Pract Res Clin Rheumatol. 22(5):773-92, 2008
- Kontzias A et al: Adult-onset Still's disease: pathogenesis, clinical manifestations and therapeutic advances. Drugs. 68(3):319-37, 2008
- Singh S et al: Adult onset Still's disease: a study of 14 cases. Clin Rheumatol. 27(1):35-9, 2008
- Yamaguchi M et al: Preliminary criteria for classification of adult Still's disease. J Rheumatol. 19(3):424-30, 1992
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
TERMINOLOGY
Synonyms
- Adult-onset Still disease (AOSD), Wissler-Fanconi syndrome
Definitions
- Systemic inflammatory disease, featuring triad
- Quotidian fevers (spiking, daily)
- Evanescent rash
- Chronic oligoarthritis or polyarthritis
- Considered adult continuum of systemic juvenile idiopathic arthritis (SJIA)
- Systemic inflammatory disease, featuring triad
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
Diagnostic Criteria (After Yamaguchi)
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Mitrovic S et al: Clinical phenotypes of adult-onset still's disease: new insights from pathophysiology and literature findings. J Clin Med. 10(12):2633, 2021
- Zhou X et al: FDG PET/CT used in identifying adult-onset Still's disease in connective tissue diseases. Clin Rheumatol. 39(9):2735-42, 2020
- Lebrun D et al: Validation of the Fautrel classification criteria for adult-onset Still's disease. Semin Arthritis Rheum. 47(4):578-85, 2018
- Dong MJ et al: 18F-FDG PET/CT in patients with adult-onset Still's disease. Clin Rheumatol. 34(12):2047-56, 2015
- Kadavath S et al: Adult-onset Still's disease-pathogenesis, clinical manifestations, and new treatment options. Ann Med. 47(1):6-14, 2015
- Manzini CU et al: Elevated troponin serum levels in adult onset Still's disease. Case Rep Rheumatol. 2015:732095, 2015
- Hayem F: Is Still's disease an autoinflammatory syndrome? Joint Bone Spine. 76(1):7-9, 2009
- Jadhav P et al: Myocarditis in adult onset Stills disease. Int J Rheum Dis. 12(3):272-4, 2009
- Lee SW et al: The mid-range of the adjusted level of ferritin can predict the chronic course in patients with adult onset Still's disease. J Rheumatol. 36(1):156-62, 2009
- Efthimiou P et al: Autoinflammatory syndromes and infections: pathogenetic and clinical implications. Clin Exp Rheumatol. 26(1 Suppl 48):S53-61, 2008
- Fautrel B: Adult-onset Still disease. Best Pract Res Clin Rheumatol. 22(5):773-92, 2008
- Kontzias A et al: Adult-onset Still's disease: pathogenesis, clinical manifestations and therapeutic advances. Drugs. 68(3):319-37, 2008
- Singh S et al: Adult onset Still's disease: a study of 14 cases. Clin Rheumatol. 27(1):35-9, 2008
- Yamaguchi M et al: Preliminary criteria for classification of adult Still's disease. J Rheumatol. 19(3):424-30, 1992
