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Gastrointestinal
Diagnosis
Abdominal Manifestations of Systemic Conditions
Metabolic or Inherited
Amyloidosis
Amyloidosis
Siva P. Raman, MD
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KEY FACTS
Terminology
Imaging
Clinical Issues
TERMINOLOGY
Synonyms
Systemic amyloidosis
Definitions
Group of diseases characterized by deposition of abnormal protein (amyloid) in various tissues
May be systemic (involving multiple organs in 80%) or localized (in single organ or tissue in 20%)
Classified based on type of protein being deposited
AL and AA proteins by far most common
30 different amyloidogenic proteins in humans
Primary: Due to monoclonal plasma cell dyscrasia (associated with no other underlying disease)
Secondary: Develops in setting of number of different chronic inflammatory diseases
IMAGING
General Features
Fluoroscopic Findings
Imaging Recommendations
CT Findings
MR Findings
Ultrasonographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Alkukhun A et al: Mesenteric amyloidosis: radiologic imaging with pathologic correlation. J Clin Imaging Sci. 10:24, 2020
Özcan HN et al: Imaging for abdominal involvement in amyloidosis. Diagn Interv Radiol. 23(4):282-5, 2017
Czeyda-Pommersheim F et al: Amyloidosis: modern cross-sectional imaging. Radiographics. 35(5):1381-92, 2015
Loizos S et al: Amyloidosis: review and imaging findings. Semin Ultrasound CT MR. 35(3):225-39, 2014
Sachchithanantham S et al: Imaging in systemic amyloidosis. Br Med Bull. 107:41-56, 2013
Andrade MJ: Lower urinary tract dysfunction in familial amyloidotic polyneuropathy, Portuguese type. Neurourol Urodyn. 28(1):26-32, 2009
Hirohata M et al: Non-steroidal anti-inflammatory drugs as anti-amyloidogenic compounds. Curr Pharm Des. 14(30):3280-94, 2008
Georgiades CS et al: Amyloidosis: review and CT manifestations. Radiographics. 24(2):405-16, 2004
Kim SH et al: Abdominal amyloidosis: spectrum of radiological findings. Clin Radiol. 58(8):610-20, 2003
Urban BA et al: CT evaluation of amyloidosis: spectrum of disease. Radiographics. 13(6):1295-308, 1993
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Clinical Issues
TERMINOLOGY
Synonyms
Systemic amyloidosis
Definitions
Group of diseases characterized by deposition of abnormal protein (amyloid) in various tissues
May be systemic (involving multiple organs in 80%) or localized (in single organ or tissue in 20%)
Classified based on type of protein being deposited
AL and AA proteins by far most common
30 different amyloidogenic proteins in humans
Primary: Due to monoclonal plasma cell dyscrasia (associated with no other underlying disease)
Secondary: Develops in setting of number of different chronic inflammatory diseases
IMAGING
General Features
Fluoroscopic Findings
Imaging Recommendations
CT Findings
MR Findings
Ultrasonographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Alkukhun A et al: Mesenteric amyloidosis: radiologic imaging with pathologic correlation. J Clin Imaging Sci. 10:24, 2020
Özcan HN et al: Imaging for abdominal involvement in amyloidosis. Diagn Interv Radiol. 23(4):282-5, 2017
Czeyda-Pommersheim F et al: Amyloidosis: modern cross-sectional imaging. Radiographics. 35(5):1381-92, 2015
Loizos S et al: Amyloidosis: review and imaging findings. Semin Ultrasound CT MR. 35(3):225-39, 2014
Sachchithanantham S et al: Imaging in systemic amyloidosis. Br Med Bull. 107:41-56, 2013
Andrade MJ: Lower urinary tract dysfunction in familial amyloidotic polyneuropathy, Portuguese type. Neurourol Urodyn. 28(1):26-32, 2009
Hirohata M et al: Non-steroidal anti-inflammatory drugs as anti-amyloidogenic compounds. Curr Pharm Des. 14(30):3280-94, 2008
Georgiades CS et al: Amyloidosis: review and CT manifestations. Radiographics. 24(2):405-16, 2004
Kim SH et al: Abdominal amyloidosis: spectrum of radiological findings. Clin Radiol. 58(8):610-20, 2003
Urban BA et al: CT evaluation of amyloidosis: spectrum of disease. Radiographics. 13(6):1295-308, 1993
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