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Angiomyolipoma
Alexander J. Towbin, MD; David B. Larson, MD, MBA
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Pathology

          • Clinical Issues

            TERMINOLOGY

            • Abbreviations

              • Angiomyolipoma (AML)
              • Tuberous sclerosis complex (TSC)
            • Definitions

              • Benign hamartomatous tumor consisting of abnormal blood vessels (angio), smooth muscle (myo), & fat (lipoma)
            • Associated Syndromes

              • Almost always associated with TSC in children

            IMAGING

            • General Features

              • CT Findings

                • MR Findings

                  • Ultrasonographic Findings

                    • Angiographic Findings

                      • Imaging Recommendations

                        DIFFERENTIAL DIAGNOSIS

                          PATHOLOGY

                          • General Features

                            • Gross Pathologic & Surgical Features

                              • Microscopic Features

                                CLINICAL ISSUES

                                • Presentation

                                  • Demographics

                                    • Natural History & Prognosis

                                      • Treatment

                                        DIAGNOSTIC CHECKLIST

                                        • Image Interpretation Pearls

                                          Selected References

                                          1. Manoukian SB et al: Comprehensive imaging manifestations of tuberous sclerosis. AJR Am J Roentgenol. 204(5):933-43, 2015
                                          2. Kingswood JC et al: The effect of everolimus on renal angiomyolipoma in patients with tuberous sclerosis complex being treated for subependymal giant cell astrocytoma: subgroup results from the randomized, placebo-controlled, Phase 3 trial EXIST-1. Nephrol Dial Transplant. 29(6):1203-10, 2014
                                          3. Tsai JD et al: Association between the growth rate of renal cysts/angiomyolipomas and age in the patients with tuberous sclerosis complex. Int Urol Nephrol. 46(9):1685-90, 2014
                                          4. Krueger DA et al: Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol. 49(4):255-65, 2013
                                          5. Meraj R et al: Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment. Semin Respir Crit Care Med. 33(5):486-97, 2012
                                          6. Baskin HJ Jr: The pathogenesis and imaging of the tuberous sclerosis complex. Pediatr Radiol. 38(9):936-52, 2008
                                          7. Hadley DA et al: Conservative treatment of renal angiomyolipomas in patients with tuberous sclerosis. Clin Nephrol. 65(1):22-7, 2006
                                          8. Fricke BL et al: Frequency and imaging appearance of hepatic angiomyolipomas in pediatric and adult patients with tuberous sclerosis. AJR Am J Roentgenol. 182(4):1027-30, 2004
                                          9. Casper KA et al: Tuberous sclerosis complex: renal imaging findings. Radiology. 225(2):451-6, 2002
                                          10. Yamakado K et al: Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture. Radiology. 225(1):78-82, 2002
                                          Related Anatomy
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                                          Related Differential Diagnoses
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                                          References
                                          Tables

                                          Tables

                                          KEY FACTS

                                          • Terminology

                                            • Imaging

                                              • Top Differential Diagnoses

                                                • Pathology

                                                  • Clinical Issues

                                                    TERMINOLOGY

                                                    • Abbreviations

                                                      • Angiomyolipoma (AML)
                                                      • Tuberous sclerosis complex (TSC)
                                                    • Definitions

                                                      • Benign hamartomatous tumor consisting of abnormal blood vessels (angio), smooth muscle (myo), & fat (lipoma)
                                                    • Associated Syndromes

                                                      • Almost always associated with TSC in children

                                                    IMAGING

                                                    • General Features

                                                      • CT Findings

                                                        • MR Findings

                                                          • Ultrasonographic Findings

                                                            • Angiographic Findings

                                                              • Imaging Recommendations

                                                                DIFFERENTIAL DIAGNOSIS

                                                                  PATHOLOGY

                                                                  • General Features

                                                                    • Gross Pathologic & Surgical Features

                                                                      • Microscopic Features

                                                                        CLINICAL ISSUES

                                                                        • Presentation

                                                                          • Demographics

                                                                            • Natural History & Prognosis

                                                                              • Treatment

                                                                                DIAGNOSTIC CHECKLIST

                                                                                • Image Interpretation Pearls

                                                                                  Selected References

                                                                                  1. Manoukian SB et al: Comprehensive imaging manifestations of tuberous sclerosis. AJR Am J Roentgenol. 204(5):933-43, 2015
                                                                                  2. Kingswood JC et al: The effect of everolimus on renal angiomyolipoma in patients with tuberous sclerosis complex being treated for subependymal giant cell astrocytoma: subgroup results from the randomized, placebo-controlled, Phase 3 trial EXIST-1. Nephrol Dial Transplant. 29(6):1203-10, 2014
                                                                                  3. Tsai JD et al: Association between the growth rate of renal cysts/angiomyolipomas and age in the patients with tuberous sclerosis complex. Int Urol Nephrol. 46(9):1685-90, 2014
                                                                                  4. Krueger DA et al: Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol. 49(4):255-65, 2013
                                                                                  5. Meraj R et al: Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment. Semin Respir Crit Care Med. 33(5):486-97, 2012
                                                                                  6. Baskin HJ Jr: The pathogenesis and imaging of the tuberous sclerosis complex. Pediatr Radiol. 38(9):936-52, 2008
                                                                                  7. Hadley DA et al: Conservative treatment of renal angiomyolipomas in patients with tuberous sclerosis. Clin Nephrol. 65(1):22-7, 2006
                                                                                  8. Fricke BL et al: Frequency and imaging appearance of hepatic angiomyolipomas in pediatric and adult patients with tuberous sclerosis. AJR Am J Roentgenol. 182(4):1027-30, 2004
                                                                                  9. Casper KA et al: Tuberous sclerosis complex: renal imaging findings. Radiology. 225(2):451-6, 2002
                                                                                  10. Yamakado K et al: Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture. Radiology. 225(1):78-82, 2002