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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Angiomyolipoma (AML)
Definitions
- Benign hamartomatous tumor consisting of abnormal blood vessels (angio), smooth muscle (myo), & fat (lipoma)
Associated Syndromes
- Almost always associated with tuberous sclerosis complex (TSC) in children
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Kingswood JC et al: Renal angiomyolipoma in patients with tuberous sclerosis complex: findings from the TuberOus SClerosis registry to increase disease Awareness. Nephrol Dial Transplant. 34(3):502-8, 2019
- Jóźwiak S et al: Liver angiomyolipomas in tuberous sclerosis complex-their incidence and course. Pediatr Neurol. 78:20-6, 2018
- Morin CE et al: Thoracoabdominal imaging of tuberous sclerosis. Pediatr Radiol. 48(9):1307-23, 2018
- Chung EM et al: Renal tumors of childhood: radiologic-pathologic correlation part 2. The 2nd decade: from the Radiologic Pathology Archives. Radiographics. 37(5):1538-58, 2017
- Cockerell I et al: Prevalence of renal angiomyolipomas and spontaneous bleeding related to angiomyolipomas in tuberous sclerosis complex patients in France and Norway: a questionnaire study. Urology. 104:70-6, 2017
- Manoukian SB et al: Comprehensive imaging manifestations of tuberous sclerosis. AJR Am J Roentgenol. 204(5):933-43, 2015
- Kingswood JC et al: The effect of everolimus on renal angiomyolipoma in patients with tuberous sclerosis complex being treated for subependymal giant cell astrocytoma: subgroup results from the randomized, placebo-controlled, phase 3 trial EXIST-1. Nephrol Dial Transplant. 29(6):1203-10, 2014
- Krueger DA et al: Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol. 49(4):255-65, 2013
- Baskin HJ Jr: The pathogenesis and imaging of the tuberous sclerosis complex. Pediatr Radiol. 38(9):936-52, 2008
- Hadley DA et al: Conservative treatment of renal angiomyolipomas in patients with tuberous sclerosis. Clin Nephrol. 65(1):22-7, 2006
- Fricke BL et al: Frequency and imaging appearance of hepatic angiomyolipomas in pediatric and adult patients with tuberous sclerosis. AJR Am J Roentgenol. 182(4):1027-30, 2004
- Casper KA et al: Tuberous sclerosis complex: renal imaging findings. Radiology. 225(2):451-6, 2002
- Yamakado K et al: Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture. Radiology. 225(1):78-82, 2002
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Angiomyolipoma (AML)
Definitions
- Benign hamartomatous tumor consisting of abnormal blood vessels (angio), smooth muscle (myo), & fat (lipoma)
Associated Syndromes
- Almost always associated with tuberous sclerosis complex (TSC) in children
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Kingswood JC et al: Renal angiomyolipoma in patients with tuberous sclerosis complex: findings from the TuberOus SClerosis registry to increase disease Awareness. Nephrol Dial Transplant. 34(3):502-8, 2019
- Jóźwiak S et al: Liver angiomyolipomas in tuberous sclerosis complex-their incidence and course. Pediatr Neurol. 78:20-6, 2018
- Morin CE et al: Thoracoabdominal imaging of tuberous sclerosis. Pediatr Radiol. 48(9):1307-23, 2018
- Chung EM et al: Renal tumors of childhood: radiologic-pathologic correlation part 2. The 2nd decade: from the Radiologic Pathology Archives. Radiographics. 37(5):1538-58, 2017
- Cockerell I et al: Prevalence of renal angiomyolipomas and spontaneous bleeding related to angiomyolipomas in tuberous sclerosis complex patients in France and Norway: a questionnaire study. Urology. 104:70-6, 2017
- Manoukian SB et al: Comprehensive imaging manifestations of tuberous sclerosis. AJR Am J Roentgenol. 204(5):933-43, 2015
- Kingswood JC et al: The effect of everolimus on renal angiomyolipoma in patients with tuberous sclerosis complex being treated for subependymal giant cell astrocytoma: subgroup results from the randomized, placebo-controlled, phase 3 trial EXIST-1. Nephrol Dial Transplant. 29(6):1203-10, 2014
- Krueger DA et al: Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol. 49(4):255-65, 2013
- Baskin HJ Jr: The pathogenesis and imaging of the tuberous sclerosis complex. Pediatr Radiol. 38(9):936-52, 2008
- Hadley DA et al: Conservative treatment of renal angiomyolipomas in patients with tuberous sclerosis. Clin Nephrol. 65(1):22-7, 2006
- Fricke BL et al: Frequency and imaging appearance of hepatic angiomyolipomas in pediatric and adult patients with tuberous sclerosis. AJR Am J Roentgenol. 182(4):1027-30, 2004
- Casper KA et al: Tuberous sclerosis complex: renal imaging findings. Radiology. 225(2):451-6, 2002
- Yamakado K et al: Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture. Radiology. 225(1):78-82, 2002
