Almost always associated with tuberous sclerosis complex (TSC) in children
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Kingswood JC et al: Renal angiomyolipoma in patients with tuberous sclerosis complex: findings from the TuberOus SClerosis registry to increase disease Awareness. Nephrol Dial Transplant. 34(3):502-8, 2019
Jóźwiak S et al: Liver angiomyolipomas in tuberous sclerosis complex-their incidence and course. Pediatr Neurol. 78:20-6, 2018
Morin CE et al: Thoracoabdominal imaging of tuberous sclerosis. Pediatr Radiol. 48(9):1307-23, 2018
Chung EM et al: Renal tumors of childhood: radiologic-pathologic correlation part 2. The 2nd decade: from the Radiologic Pathology Archives. Radiographics. 37(5):1538-58, 2017
Cockerell I et al: Prevalence of renal angiomyolipomas and spontaneous bleeding related to angiomyolipomas in tuberous sclerosis complex patients in France and Norway: a questionnaire study. Urology. 104:70-6, 2017
Manoukian SB et al: Comprehensive imaging manifestations of tuberous sclerosis. AJR Am J Roentgenol. 204(5):933-43, 2015
Kingswood JC et al: The effect of everolimus on renal angiomyolipoma in patients with tuberous sclerosis complex being treated for subependymal giant cell astrocytoma: subgroup results from the randomized, placebo-controlled, phase 3 trial EXIST-1. Nephrol Dial Transplant. 29(6):1203-10, 2014
Krueger DA et al: Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol. 49(4):255-65, 2013
Baskin HJ Jr: The pathogenesis and imaging of the tuberous sclerosis complex. Pediatr Radiol. 38(9):936-52, 2008
Hadley DA et al: Conservative treatment of renal angiomyolipomas in patients with tuberous sclerosis. Clin Nephrol. 65(1):22-7, 2006
Fricke BL et al: Frequency and imaging appearance of hepatic angiomyolipomas in pediatric and adult patients with tuberous sclerosis. AJR Am J Roentgenol. 182(4):1027-30, 2004
Casper KA et al: Tuberous sclerosis complex: renal imaging findings. Radiology. 225(2):451-6, 2002
Yamakado K et al: Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture. Radiology. 225(1):78-82, 2002
Almost always associated with tuberous sclerosis complex (TSC) in children
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Kingswood JC et al: Renal angiomyolipoma in patients with tuberous sclerosis complex: findings from the TuberOus SClerosis registry to increase disease Awareness. Nephrol Dial Transplant. 34(3):502-8, 2019
Jóźwiak S et al: Liver angiomyolipomas in tuberous sclerosis complex-their incidence and course. Pediatr Neurol. 78:20-6, 2018
Morin CE et al: Thoracoabdominal imaging of tuberous sclerosis. Pediatr Radiol. 48(9):1307-23, 2018
Chung EM et al: Renal tumors of childhood: radiologic-pathologic correlation part 2. The 2nd decade: from the Radiologic Pathology Archives. Radiographics. 37(5):1538-58, 2017
Cockerell I et al: Prevalence of renal angiomyolipomas and spontaneous bleeding related to angiomyolipomas in tuberous sclerosis complex patients in France and Norway: a questionnaire study. Urology. 104:70-6, 2017
Manoukian SB et al: Comprehensive imaging manifestations of tuberous sclerosis. AJR Am J Roentgenol. 204(5):933-43, 2015
Kingswood JC et al: The effect of everolimus on renal angiomyolipoma in patients with tuberous sclerosis complex being treated for subependymal giant cell astrocytoma: subgroup results from the randomized, placebo-controlled, phase 3 trial EXIST-1. Nephrol Dial Transplant. 29(6):1203-10, 2014
Krueger DA et al: Tuberous sclerosis complex surveillance and management: recommendations of the 2012 International Tuberous Sclerosis Complex Consensus Conference. Pediatr Neurol. 49(4):255-65, 2013
Baskin HJ Jr: The pathogenesis and imaging of the tuberous sclerosis complex. Pediatr Radiol. 38(9):936-52, 2008
Hadley DA et al: Conservative treatment of renal angiomyolipomas in patients with tuberous sclerosis. Clin Nephrol. 65(1):22-7, 2006
Fricke BL et al: Frequency and imaging appearance of hepatic angiomyolipomas in pediatric and adult patients with tuberous sclerosis. AJR Am J Roentgenol. 182(4):1027-30, 2004
Casper KA et al: Tuberous sclerosis complex: renal imaging findings. Radiology. 225(2):451-6, 2002
Yamakado K et al: Renal angiomyolipoma: relationships between tumor size, aneurysm formation, and rupture. Radiology. 225(1):78-82, 2002
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