Very rare, highly aggressive class of sarcomas that arise from aortic wall or intima and carry poor prognosis
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Vacirca A et al: Predictors of survival in malignant aortic tumors. J Vasc Surg. 71(5):1771-80, 2020
Arzanauskaite M et al: Primary tumors of the aorta and pulmonary arteries: insights from cardiovascular magnetic resonance. JACC Cardiovasc Imaging. 12(10):2065-70, 2019
Rusthoven CG et al: Sarcomas of the aorta: a systematic review and pooled analysis of published reports. Ann Vasc Surg. 28(2):515-25, 2014
von Falck C et al: Imaging features of primary sarcomas of the great vessels in CT, MRI and PET/CT: a single-center experience. BMC Med Imaging. 13(1):25, 2013
Garg N et al: Intimal sarcoma in an inflammatory aneurysm after endovascular aneurysm repair. J Vasc Surg. 55(4):1134-7, 2012
Bendel EC et al: Imaging sarcomas of the great vessels and heart. Semin Ultrasound CT MR. 32(5):377-404, 2011
Rusthoven C et al: High-grade undifferentiated pleomorphic sarcoma of the aortic arch: a case of endovascular therapy for embolic prophylaxis and review of the literature. Vasc Endovascular Surg. 44(5):385-91, 2010
Nicotera SP et al: Postoperative outcomes in intimal aortic angiosarcoma: a case report and review of the literature. J Vasc Surg. 50(1):186-9, 2009
Simpson WL Jr et al: Pulmonary artery and aortic sarcomas: cross-sectional imaging. J Thorac Imaging. 15(4):290-4, 2000
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Primary malignant tumors of aorta (PMTA)
Definitions
Very rare, highly aggressive class of sarcomas that arise from aortic wall or intima and carry poor prognosis
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Vacirca A et al: Predictors of survival in malignant aortic tumors. J Vasc Surg. 71(5):1771-80, 2020
Arzanauskaite M et al: Primary tumors of the aorta and pulmonary arteries: insights from cardiovascular magnetic resonance. JACC Cardiovasc Imaging. 12(10):2065-70, 2019
Rusthoven CG et al: Sarcomas of the aorta: a systematic review and pooled analysis of published reports. Ann Vasc Surg. 28(2):515-25, 2014
von Falck C et al: Imaging features of primary sarcomas of the great vessels in CT, MRI and PET/CT: a single-center experience. BMC Med Imaging. 13(1):25, 2013
Garg N et al: Intimal sarcoma in an inflammatory aneurysm after endovascular aneurysm repair. J Vasc Surg. 55(4):1134-7, 2012
Bendel EC et al: Imaging sarcomas of the great vessels and heart. Semin Ultrasound CT MR. 32(5):377-404, 2011
Rusthoven C et al: High-grade undifferentiated pleomorphic sarcoma of the aortic arch: a case of endovascular therapy for embolic prophylaxis and review of the literature. Vasc Endovascular Surg. 44(5):385-91, 2010
Nicotera SP et al: Postoperative outcomes in intimal aortic angiosarcoma: a case report and review of the literature. J Vasc Surg. 50(1):186-9, 2009
Simpson WL Jr et al: Pulmonary artery and aortic sarcomas: cross-sectional imaging. J Thorac Imaging. 15(4):290-4, 2000
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