link
Bookmarks
Atypical Teratoid/Rhabdoid Tumor
Luke L. Linscott, MD
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Log inSubscribe
0
14
2
4

KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Pathology

          • Clinical Issues

            • Diagnostic Checklist

              TERMINOLOGY

              • Synonyms

                • Malignant rhabdoid tumor of brain
                • Intracranial rhabdoid tumor
              • Definitions

                • Atypical teratoid/rhabdoid tumor (AT/RT): Malignant embryonal tumor of CNS in early childhood
                  • Closely related to renal & soft tissue rhabdoid tumors

              IMAGING

              • General Features

                • CT Findings

                  • MR Findings

                    • Imaging Recommendations

                      DIFFERENTIAL DIAGNOSIS

                        PATHOLOGY

                        • General Features

                          • Staging, Grading, & Classification

                            • Gross Pathologic & Surgical Features

                              • Microscopic Features

                                CLINICAL ISSUES

                                • Presentation

                                  • Demographics

                                    • Natural History & Prognosis

                                      • Treatment

                                        DIAGNOSTIC CHECKLIST

                                        • Consider

                                          Selected References

                                          1. DiPatri AJ Jr et al: Atypical teratoid rhabdoid tumors of the posterior fossa in children. Childs Nerv Syst. 31(10):1717-28, 2015
                                          2. Ho DM et al: Integrated genomics has identified a new AT/RT-like yet INI1-positive brain tumor subtype among primary pediatric embryonal tumors. BMC Med Genomics. 8:32, 2015
                                          3. Lau CS et al: Atypical teratoid rhabdoid tumors: a population-based clinical outcomes study involving 174 patients from the Surveillance, Epidemiology, and End Results database (1973-2010). Cancer Manag Res. 7:301-9, 2015
                                          4. Verma V et al: Atypical teratoid rhabdoid tumor: long-term survival after chemoradiotherapy. Childs Nerv Syst. 31(8):1393-9, 2015
                                          5. Ostrom QT et al: CBTRUS statistical report: primary brain and central nervous system tumors diagnosed in the United States in 2007-2011. Neuro Oncol. 16 Suppl 4:iv1-63, 2014
                                          6. Slavc I et al: Atypical teratoid rhabdoid tumor: improved long-term survival with an intensive multimodal therapy and delayed radiotherapy. The Medical University of Vienna Experience 1992-2012. Cancer Med. 3(1):91-100, 2014
                                          7. Au Yong KJ et al: How specific is the MRI appearance of supratentorial atypical teratoid rhabdoid tumors? Pediatr Radiol. 43(3):347-54, 2013
                                          8. Bruggers CS et al: Magnetic resonance imaging spectroscopy in pediatric atypical teratoid rhabdoid tumors of the brain. J Pediatr Hematol Oncol. 36(6):341-5, 2013
                                          9. Perreault S et al: Relapse patterns in pediatric embryonal central nervous system tumors. J Neurooncol. 115(2):209-15, 2013
                                          10. Lafay-Cousin L et al: Central nervous system atypical teratoid rhabdoid tumours: the Canadian Paediatric Brain Tumour Consortium experience. Eur J Cancer. 48(3):353-9, 2012
                                          11. Koral K et al: Imaging characteristics of atypical teratoid-rhabdoid tumor in children compared with medulloblastoma. AJR Am J Roentgenol. 190(3):809-14, 2008
                                          12. Warmuth-Metz M et al: CT and MR imaging in atypical teratoid/rhabdoid tumors of the central nervous system. Neuroradiology. 50(5):447-52, 2008
                                          13. Meyers SP et al: Primary intracranial atypical teratoid/rhabdoid tumors of infancy and childhood: MRI features and patient outcomes. AJNR Am J Neuroradiol. 27(5):962-71, 2006
                                          14. Parmar H et al: Imaging findings in primary intracranial atypical teratoid/rhabdoid tumors. Pediatr Radiol. 36(2):126-32, 2006
                                          15. Fenton LZ et al: Atypical teratoid/rhabdoid tumor of the central nervous system in children: an atypical series and review. Pediatr Radiol. 33(8):554-8, 2003
                                          Related Anatomy
                                          Loading...
                                          Related Differential Diagnoses
                                          Loading...
                                          References
                                          Tables

                                          Tables

                                          KEY FACTS

                                          • Terminology

                                            • Imaging

                                              • Top Differential Diagnoses

                                                • Pathology

                                                  • Clinical Issues

                                                    • Diagnostic Checklist

                                                      TERMINOLOGY

                                                      • Synonyms

                                                        • Malignant rhabdoid tumor of brain
                                                        • Intracranial rhabdoid tumor
                                                      • Definitions

                                                        • Atypical teratoid/rhabdoid tumor (AT/RT): Malignant embryonal tumor of CNS in early childhood
                                                          • Closely related to renal & soft tissue rhabdoid tumors

                                                      IMAGING

                                                      • General Features

                                                        • CT Findings

                                                          • MR Findings

                                                            • Imaging Recommendations

                                                              DIFFERENTIAL DIAGNOSIS

                                                                PATHOLOGY

                                                                • General Features

                                                                  • Staging, Grading, & Classification

                                                                    • Gross Pathologic & Surgical Features

                                                                      • Microscopic Features

                                                                        CLINICAL ISSUES

                                                                        • Presentation

                                                                          • Demographics

                                                                            • Natural History & Prognosis

                                                                              • Treatment

                                                                                DIAGNOSTIC CHECKLIST

                                                                                • Consider

                                                                                  Selected References

                                                                                  1. DiPatri AJ Jr et al: Atypical teratoid rhabdoid tumors of the posterior fossa in children. Childs Nerv Syst. 31(10):1717-28, 2015
                                                                                  2. Ho DM et al: Integrated genomics has identified a new AT/RT-like yet INI1-positive brain tumor subtype among primary pediatric embryonal tumors. BMC Med Genomics. 8:32, 2015
                                                                                  3. Lau CS et al: Atypical teratoid rhabdoid tumors: a population-based clinical outcomes study involving 174 patients from the Surveillance, Epidemiology, and End Results database (1973-2010). Cancer Manag Res. 7:301-9, 2015
                                                                                  4. Verma V et al: Atypical teratoid rhabdoid tumor: long-term survival after chemoradiotherapy. Childs Nerv Syst. 31(8):1393-9, 2015
                                                                                  5. Ostrom QT et al: CBTRUS statistical report: primary brain and central nervous system tumors diagnosed in the United States in 2007-2011. Neuro Oncol. 16 Suppl 4:iv1-63, 2014
                                                                                  6. Slavc I et al: Atypical teratoid rhabdoid tumor: improved long-term survival with an intensive multimodal therapy and delayed radiotherapy. The Medical University of Vienna Experience 1992-2012. Cancer Med. 3(1):91-100, 2014
                                                                                  7. Au Yong KJ et al: How specific is the MRI appearance of supratentorial atypical teratoid rhabdoid tumors? Pediatr Radiol. 43(3):347-54, 2013
                                                                                  8. Bruggers CS et al: Magnetic resonance imaging spectroscopy in pediatric atypical teratoid rhabdoid tumors of the brain. J Pediatr Hematol Oncol. 36(6):341-5, 2013
                                                                                  9. Perreault S et al: Relapse patterns in pediatric embryonal central nervous system tumors. J Neurooncol. 115(2):209-15, 2013
                                                                                  10. Lafay-Cousin L et al: Central nervous system atypical teratoid rhabdoid tumours: the Canadian Paediatric Brain Tumour Consortium experience. Eur J Cancer. 48(3):353-9, 2012
                                                                                  11. Koral K et al: Imaging characteristics of atypical teratoid-rhabdoid tumor in children compared with medulloblastoma. AJR Am J Roentgenol. 190(3):809-14, 2008
                                                                                  12. Warmuth-Metz M et al: CT and MR imaging in atypical teratoid/rhabdoid tumors of the central nervous system. Neuroradiology. 50(5):447-52, 2008
                                                                                  13. Meyers SP et al: Primary intracranial atypical teratoid/rhabdoid tumors of infancy and childhood: MRI features and patient outcomes. AJNR Am J Neuroradiol. 27(5):962-71, 2006
                                                                                  14. Parmar H et al: Imaging findings in primary intracranial atypical teratoid/rhabdoid tumors. Pediatr Radiol. 36(2):126-32, 2006
                                                                                  15. Fenton LZ et al: Atypical teratoid/rhabdoid tumor of the central nervous system in children: an atypical series and review. Pediatr Radiol. 33(8):554-8, 2003