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Chest
Diagnosis
Connective Tissue Disorders, Immunological Diseases, and Vasculitis
Pulmonary Edema, Hemorrhage, and Vasculitis
Behcet Syndrome
Behcet Syndrome
John P. Lichtenberger, III, MD
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Behçet disease, Silk Road disease
Definitions
Chronic systemic inflammatory disease characterized by oral & genital mucosal ulcers & uveitis
Thoracic disease includes
Vascular aneurysms ± luminal thrombus
Lung & airway disease
Pleural nodules & effusions
Mediastinal lymphadenopathy, fibrosis
IMAGING
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Ceylan N et al: Pulmonary and vascular manifestations of Behcet disease: imaging findings. AJR Am J Roentgenol. 194(2):W158-64, 2010
Chae EJ et al: Radiologic and clinical findings of Behçet disease: comprehensive review of multisystemic involvement. Radiographics. 28(5):e31, 2008
Uzun O et al: Pulmonary vasculitis in behcet disease: a cumulative analysis. Chest. 127(6):2243-53, 2005
Hiller N et al: Thoracic manifestations of Behçet disease at CT. Radiographics. 24(3):801-8, 2004
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Behçet disease, Silk Road disease
Definitions
Chronic systemic inflammatory disease characterized by oral & genital mucosal ulcers & uveitis
Thoracic disease includes
Vascular aneurysms ± luminal thrombus
Lung & airway disease
Pleural nodules & effusions
Mediastinal lymphadenopathy, fibrosis
IMAGING
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Ceylan N et al: Pulmonary and vascular manifestations of Behcet disease: imaging findings. AJR Am J Roentgenol. 194(2):W158-64, 2010
Chae EJ et al: Radiologic and clinical findings of Behçet disease: comprehensive review of multisystemic involvement. Radiographics. 28(5):e31, 2008
Uzun O et al: Pulmonary vasculitis in behcet disease: a cumulative analysis. Chest. 127(6):2243-53, 2005
Hiller N et al: Thoracic manifestations of Behçet disease at CT. Radiographics. 24(3):801-8, 2004
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