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Chest
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Interstitial, Diffuse, and Inhalational Lung Disease
Metabolic Diseases and Miscellaneous Conditions
Birt-Hogg-Dubé Syndrome
Birt-Hogg-Dubé Syndrome
Melissa L. Rosado de Christenson, MD, FACR
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Clinical Issues

          • Diagnostic Checklist

            TERMINOLOGY

            • Definitions

              • Rare inherited disorder characterized by triad of lung cysts (often complicated with pneumothorax) and renal and cutaneous lesions

            IMAGING

            • General Features

              • Radiographic Findings

                • CT Findings

                  • Imaging Recommendations

                    DIFFERENTIAL DIAGNOSIS

                      PATHOLOGY

                      • General Features

                        • Gross Pathologic & Surgical Features

                          • Microscopic Features

                            CLINICAL ISSUES

                            • Presentation

                              • Demographics

                                DIAGNOSTIC CHECKLIST

                                • Consider

                                  Selected References

                                  1. Dal Sasso AA et al: Birt-Hogg-Dubé syndrome. State-of-the-art review with emphasis on pulmonary involvement. Respir Med. 109(3):289-96, 2015
                                  2. Jawad H et al: Cystic interstitial lung diseases: recognizing the common and uncommon entities. Curr Probl Diagn Radiol. 43(3):115-27, 2014
                                  3. Furuya M et al: Birt-Hogg-Dube syndrome: clinicopathological features of the lung. J Clin Pathol. 66(3):178-86, 2013
                                  4. Tobino K et al: Characteristics of pulmonary cysts in Birt-Hogg-Dubé syndrome: thin-section CT findings of the chest in 12 patients. Eur J Radiol. 77(3):403-9, 2011
                                  Related Anatomy
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                                  Related Differential Diagnoses
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                                  References
                                  Tables

                                  Tables

                                  KEY FACTS

                                  • Terminology

                                    • Imaging

                                      • Top Differential Diagnoses

                                        • Clinical Issues

                                          • Diagnostic Checklist

                                            TERMINOLOGY

                                            • Definitions

                                              • Rare inherited disorder characterized by triad of lung cysts (often complicated with pneumothorax) and renal and cutaneous lesions

                                            IMAGING

                                            • General Features

                                              • Radiographic Findings

                                                • CT Findings

                                                  • Imaging Recommendations

                                                    DIFFERENTIAL DIAGNOSIS

                                                      PATHOLOGY

                                                      • General Features

                                                        • Gross Pathologic & Surgical Features

                                                          • Microscopic Features

                                                            CLINICAL ISSUES

                                                            • Presentation

                                                              • Demographics

                                                                DIAGNOSTIC CHECKLIST

                                                                • Consider

                                                                  Selected References

                                                                  1. Dal Sasso AA et al: Birt-Hogg-Dubé syndrome. State-of-the-art review with emphasis on pulmonary involvement. Respir Med. 109(3):289-96, 2015
                                                                  2. Jawad H et al: Cystic interstitial lung diseases: recognizing the common and uncommon entities. Curr Probl Diagn Radiol. 43(3):115-27, 2014
                                                                  3. Furuya M et al: Birt-Hogg-Dube syndrome: clinicopathological features of the lung. J Clin Pathol. 66(3):178-86, 2013
                                                                  4. Tobino K et al: Characteristics of pulmonary cysts in Birt-Hogg-Dubé syndrome: thin-section CT findings of the chest in 12 patients. Eur J Radiol. 77(3):403-9, 2011