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Chest
Diagnosis
Developmental Abnormalities
Airways
Bronchial Atresia
Bronchial Atresia
Tyler H. Ternes, MD
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Bronchial atresia (BA)
Synonyms
Congenital bronchial atresia (CBA)
Definitions
Congenital focal atresia of subsegmental, segmental, or lobar bronchus
Normal distal bronchial tree
Mucocele: Mucoid impaction distal to BA
Synonym: Bronchocele
IMAGING
General Features
Radiographic Findings
CT Findings
Nuclear Medicine Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Diagnosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Kuwabara G et al: Congenital bronchial atresia complicated by a lung abscess due to Aspergillus fumigatus: a case report. BMC Pulm Med. 21(1):2, 2021
Cherian SV et al: Developmental lung anomalies in adults: a pictorial review. respir Med. 155:86-96, 2019
Masroujeh R et al: Endobronchial treatment of bronchial atresia. Am J Respir Crit Care Med. 200(3):e25-6, 2019
Alamo L et al: Imaging findings of bronchial atresia in fetuses, neonates and infants. Pediatr Radiol. 46(3):383-90, 2016
Heidinger BH et al: Imaging of large airways disorders. AJR Am J Roentgenol. 205(1):41-56, 2015
Kong X et al: Xenon-enhanced dual-energy CT lung ventilation imaging: techniques and clinical applications. AJR Am J Roentgenol. 202(2):309-17, 2014
Primetis E et al: Congenital bronchial atresia with a calcified mucocele. Respiration. 81(6):511-2, 2011
Biyyam DR et al: Congenital lung abnormalities: embryologic features, prenatal diagnosis, and postnatal radiologic-pathologic correlation. Radiographics. 30(6):1721-38, 2010
Daltro P et al: Congenital chest malformations: a multimodality approach with emphasis on fetal MR imaging. Radiographics. 30(2):385-95, 2010
Desir A et al: Congenital abnormalities of intrathoracic airways. Radiol Clin North Am. 47(2):203-25, 2009
Gipson MG et al: Bronchial atresia. Radiographics. 29(5):1531-5, 2009
Martinez S et al: Mucoid impactions: finger-in-glove sign and other CT and radiographic features. Radiographics. 28(5):1369-82, 2008
Kamata S et al: Case of congenital bronchial atresia detected by fetal ultrasound. Pediatr Pulmonol. 35(3):227-9, 2003
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Bronchial atresia (BA)
Synonyms
Congenital bronchial atresia (CBA)
Definitions
Congenital focal atresia of subsegmental, segmental, or lobar bronchus
Normal distal bronchial tree
Mucocele: Mucoid impaction distal to BA
Synonym: Bronchocele
IMAGING
General Features
Radiographic Findings
CT Findings
Nuclear Medicine Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Diagnosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Kuwabara G et al: Congenital bronchial atresia complicated by a lung abscess due to Aspergillus fumigatus: a case report. BMC Pulm Med. 21(1):2, 2021
Cherian SV et al: Developmental lung anomalies in adults: a pictorial review. respir Med. 155:86-96, 2019
Masroujeh R et al: Endobronchial treatment of bronchial atresia. Am J Respir Crit Care Med. 200(3):e25-6, 2019
Alamo L et al: Imaging findings of bronchial atresia in fetuses, neonates and infants. Pediatr Radiol. 46(3):383-90, 2016
Heidinger BH et al: Imaging of large airways disorders. AJR Am J Roentgenol. 205(1):41-56, 2015
Kong X et al: Xenon-enhanced dual-energy CT lung ventilation imaging: techniques and clinical applications. AJR Am J Roentgenol. 202(2):309-17, 2014
Primetis E et al: Congenital bronchial atresia with a calcified mucocele. Respiration. 81(6):511-2, 2011
Biyyam DR et al: Congenital lung abnormalities: embryologic features, prenatal diagnosis, and postnatal radiologic-pathologic correlation. Radiographics. 30(6):1721-38, 2010
Daltro P et al: Congenital chest malformations: a multimodality approach with emphasis on fetal MR imaging. Radiographics. 30(2):385-95, 2010
Desir A et al: Congenital abnormalities of intrathoracic airways. Radiol Clin North Am. 47(2):203-25, 2009
Gipson MG et al: Bronchial atresia. Radiographics. 29(5):1531-5, 2009
Martinez S et al: Mucoid impactions: finger-in-glove sign and other CT and radiographic features. Radiographics. 28(5):1369-82, 2008
Kamata S et al: Case of congenital bronchial atresia detected by fetal ultrasound. Pediatr Pulmonol. 35(3):227-9, 2003
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