Bookmarks
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Communicating cavernous biliary ectasia
Definitions
- Congenital, nonobstructive, saccular, multisegmental dilatation of large intrahepatic bile ducts (IHBDs)
IMAGING
General Features
Ultrasonographic Findings
Radiographic Findings
CT Findings
MR Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Karaosmanoglu AD et al: Congenital and hereditary cystic diseases of the abdomen. Insights Imaging. 11(1):90, 2020
- Rivas A et al: Prenatal MR imaging features of Caroli syndrome in association with autosomal recessive polycystic kidney disease. Radiol Case Rep. 14(2):265-68, 2019
- Hwang MJ et al: Diffuse-type Caroli disease with characteristic central dot sign complicated by multiple intrahepatic and common bile duct stones. Clin Endosc. 50(4):400-3, 2017
- Gunay-Aygun M et al: Characteristics of congenital hepatic fibrosis in a large cohort of patients with autosomal recessive polycystic kidney disease. Gastroenterology. 144(1):112-21, 2013
- Lefere M et al: Caroli disease: review of eight cases with emphasis on magnetic resonance imaging features. Eur J Gastroenterol Hepatol. 23(7):578-85, 2011
- Venkatanarasimha N et al: Imaging features of ductal plate malformations in adults. Clin Radiol. 66(11):1086-93, 2011
- Ananthakrishnan AN et al: Caroli's disease: identification and treatment strategy. Curr Gastroenterol Rep. 9(2):151-5, 2007
- Yonem O et al: Clinical characteristics of Caroli's syndrome. World J Gastroenterol. 13(13):1934-7, 2007
- Madjov R et al: Caroli's disease. Report of 5 cases and review of literature. Hepatogastroenterology. 52(62):606-9, 2005
- Sgro M et al: Caroli's disease: prenatal diagnosis, postnatal outcome and genetic analysis. Ultrasound Obstet Gynecol. 23(1):73-6, 2004
- Levy AD et al: Caroli's disease: radiologic spectrum with pathologic correlation. AJR Am J Roentgenol. 179(4):1053-7, 2002
- Fulcher AS et al: Case 38: Caroli disease and renal tubular ectasia. Radiology. 220(3):720-3, 2001
- Mortele KJ et al: Cystic focal liver lesions in the adult: differential CT and MR imaging features. Radiographics. 21(4):895-910, 2001
- Akin O et al: An unusual sonographic finding in Caroli's disease. AJR Am J Roentgenol. 171(4):1167, 1998
- Gorka W et al: Value of Doppler sonography in the assessment of patients with Caroli's disease. J Clin Ultrasound. 26(6):283-7, 1998
- Miller WJ et al: Imaging findings in Caroli's disease. AJR Am J Roentgenol. 165(2):333-7, 1995
- Rizzo RJ et al: Congenital abnormalities of the pancreas and biliary tree in adults. Radiographics. 15(1):49-68; quiz 147-8, 1995
- Choi BI et al: Caroli disease: central dot sign in CT. Radiology. 174(1):161-3, 1990
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Communicating cavernous biliary ectasia
Definitions
- Congenital, nonobstructive, saccular, multisegmental dilatation of large intrahepatic bile ducts (IHBDs)
IMAGING
General Features
Ultrasonographic Findings
Radiographic Findings
CT Findings
MR Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Karaosmanoglu AD et al: Congenital and hereditary cystic diseases of the abdomen. Insights Imaging. 11(1):90, 2020
- Rivas A et al: Prenatal MR imaging features of Caroli syndrome in association with autosomal recessive polycystic kidney disease. Radiol Case Rep. 14(2):265-68, 2019
- Hwang MJ et al: Diffuse-type Caroli disease with characteristic central dot sign complicated by multiple intrahepatic and common bile duct stones. Clin Endosc. 50(4):400-3, 2017
- Gunay-Aygun M et al: Characteristics of congenital hepatic fibrosis in a large cohort of patients with autosomal recessive polycystic kidney disease. Gastroenterology. 144(1):112-21, 2013
- Lefere M et al: Caroli disease: review of eight cases with emphasis on magnetic resonance imaging features. Eur J Gastroenterol Hepatol. 23(7):578-85, 2011
- Venkatanarasimha N et al: Imaging features of ductal plate malformations in adults. Clin Radiol. 66(11):1086-93, 2011
- Ananthakrishnan AN et al: Caroli's disease: identification and treatment strategy. Curr Gastroenterol Rep. 9(2):151-5, 2007
- Yonem O et al: Clinical characteristics of Caroli's syndrome. World J Gastroenterol. 13(13):1934-7, 2007
- Madjov R et al: Caroli's disease. Report of 5 cases and review of literature. Hepatogastroenterology. 52(62):606-9, 2005
- Sgro M et al: Caroli's disease: prenatal diagnosis, postnatal outcome and genetic analysis. Ultrasound Obstet Gynecol. 23(1):73-6, 2004
- Levy AD et al: Caroli's disease: radiologic spectrum with pathologic correlation. AJR Am J Roentgenol. 179(4):1053-7, 2002
- Fulcher AS et al: Case 38: Caroli disease and renal tubular ectasia. Radiology. 220(3):720-3, 2001
- Mortele KJ et al: Cystic focal liver lesions in the adult: differential CT and MR imaging features. Radiographics. 21(4):895-910, 2001
- Akin O et al: An unusual sonographic finding in Caroli's disease. AJR Am J Roentgenol. 171(4):1167, 1998
- Gorka W et al: Value of Doppler sonography in the assessment of patients with Caroli's disease. J Clin Ultrasound. 26(6):283-7, 1998
- Miller WJ et al: Imaging findings in Caroli's disease. AJR Am J Roentgenol. 165(2):333-7, 1995
- Rizzo RJ et al: Congenital abnormalities of the pancreas and biliary tree in adults. Radiographics. 15(1):49-68; quiz 147-8, 1995
- Choi BI et al: Caroli disease: central dot sign in CT. Radiology. 174(1):161-3, 1990
