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Cerebral Hemiatrophy
Surjith Vattoth, MD, FRCRKaren L. Salzman, MD, FACR
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Pathology

          • Clinical Issues

            • Diagnostic Checklist

              TERMINOLOGY

              • Abbreviations

                • Cerebral hemiatrophy (CH)
              • Synonyms

                • Dyke-Davidoff-Masson syndrome (DDMS)
              • Definitions

                • Syndrome of hemiplegia, seizures, facial asymmetry, and intellectual disability
                • Originally described in 1933 by Dyke, Davidoff, and Masson on skull radiographs and pneumoencephalograms

              IMAGING

              • General Features

                • Ultrasonographic Findings

                  • Imaging Recommendations

                    • Radiographic Findings

                      • CT Findings

                        • MR Findings

                          DIFFERENTIAL DIAGNOSIS

                            PATHOLOGY

                            • General Features

                              CLINICAL ISSUES

                              • Presentation

                                • Demographics

                                  • Treatment

                                    DIAGNOSTIC CHECKLIST

                                    • Image Interpretation Pearls

                                      Selected References

                                      1. Sharawat IK et al: Dyke-Davidoff-Masson syndrome: unusual cause of hemiplegic cerebral palsy. BMJ Case Rep. 12(4), 2019
                                      2. Kalaskar R et al: Classical oral manifestations of Dyke-Davidoff-Masson syndrome: a case report with review of the literature. J Korean Assoc Oral Maxillofac Surg. 44(4):198-203, 2018
                                      3. Tan AP et al: Clinico-radiological approach to cerebral hemiatrophy. Childs Nerv Syst. 34(12):2377-2390, 2018
                                      4. Aggarwal A et al: Hemiatrophy of brain: antenatal ultrasonography and MRI/postnatal MRI diagnosis with the introduction of "shifted falx sign". J Med Ultrason (2001). 44(1):147-151, 2017
                                      5. Biçici V et al: Dyke-Davidoff-Masson syndrome in adulthood: A 50-year diagnostic delay. Neurology. 83(12):1121, 2014
                                      6. Park KI et al: Dyke-davidoff-masson syndrome: cases of two brothers and literature review. J Epilepsy Res. 4(1):24-7, 2014
                                      7. Slon V et al: Dyke-Davidoff-Masson syndrome in a 6,000-year old skull. Neuroradiology. 54(12):1413-5, 2012
                                      8. Atalar MH et al: Cerebral hemiatrophy (Dyke-Davidoff-Masson syndrome) in childhood: clinicoradiological analysis of 19 cases. Pediatr Int. 49(1):70-5, 2007
                                      9. Unal O et al: Left hemisphere and male sex dominance of cerebral hemiatrophy (Dyke-Davidoff-Masson Syndrome). Clin Imaging. 28(3):163-5, 2004
                                      Related Anatomy
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                                      Related Differential Diagnoses
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                                      References
                                      Tables

                                      Tables

                                      KEY FACTS

                                      • Terminology

                                        • Imaging

                                          • Top Differential Diagnoses

                                            • Pathology

                                              • Clinical Issues

                                                • Diagnostic Checklist

                                                  TERMINOLOGY

                                                  • Abbreviations

                                                    • Cerebral hemiatrophy (CH)
                                                  • Synonyms

                                                    • Dyke-Davidoff-Masson syndrome (DDMS)
                                                  • Definitions

                                                    • Syndrome of hemiplegia, seizures, facial asymmetry, and intellectual disability
                                                    • Originally described in 1933 by Dyke, Davidoff, and Masson on skull radiographs and pneumoencephalograms

                                                  IMAGING

                                                  • General Features

                                                    • Ultrasonographic Findings

                                                      • Imaging Recommendations

                                                        • Radiographic Findings

                                                          • CT Findings

                                                            • MR Findings

                                                              DIFFERENTIAL DIAGNOSIS

                                                                PATHOLOGY

                                                                • General Features

                                                                  CLINICAL ISSUES

                                                                  • Presentation

                                                                    • Demographics

                                                                      • Treatment

                                                                        DIAGNOSTIC CHECKLIST

                                                                        • Image Interpretation Pearls

                                                                          Selected References

                                                                          1. Sharawat IK et al: Dyke-Davidoff-Masson syndrome: unusual cause of hemiplegic cerebral palsy. BMJ Case Rep. 12(4), 2019
                                                                          2. Kalaskar R et al: Classical oral manifestations of Dyke-Davidoff-Masson syndrome: a case report with review of the literature. J Korean Assoc Oral Maxillofac Surg. 44(4):198-203, 2018
                                                                          3. Tan AP et al: Clinico-radiological approach to cerebral hemiatrophy. Childs Nerv Syst. 34(12):2377-2390, 2018
                                                                          4. Aggarwal A et al: Hemiatrophy of brain: antenatal ultrasonography and MRI/postnatal MRI diagnosis with the introduction of "shifted falx sign". J Med Ultrason (2001). 44(1):147-151, 2017
                                                                          5. Biçici V et al: Dyke-Davidoff-Masson syndrome in adulthood: A 50-year diagnostic delay. Neurology. 83(12):1121, 2014
                                                                          6. Park KI et al: Dyke-davidoff-masson syndrome: cases of two brothers and literature review. J Epilepsy Res. 4(1):24-7, 2014
                                                                          7. Slon V et al: Dyke-Davidoff-Masson syndrome in a 6,000-year old skull. Neuroradiology. 54(12):1413-5, 2012
                                                                          8. Atalar MH et al: Cerebral hemiatrophy (Dyke-Davidoff-Masson syndrome) in childhood: clinicoradiological analysis of 19 cases. Pediatr Int. 49(1):70-5, 2007
                                                                          9. Unal O et al: Left hemisphere and male sex dominance of cerebral hemiatrophy (Dyke-Davidoff-Masson Syndrome). Clin Imaging. 28(3):163-5, 2004