Choledochal cyst (CC): Congenital cystic dilatation of extrahepatic ± intrahepatic bile ducts
CC is "incomplete" obstruction
Cystic biliary atresia (CBA): Extrahepatic bile duct terminates blindly at caudal end
Complete biliary obstruction
CBA seen in 13-44% with CC
Biliary atresia (BA): Progressive fibroobliterative disease of intrahepatic + extrahepatic bile ducts
IMAGING
General Features
Ultrasonographic Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Hattori K et al: Cyst size in fetuses with biliary cystic malformation: an exploration of the etiology of congenital biliary dilatation. Pediatr Gastroenterol Hepatol Nutr. 23(6):531-8, 2020
Mahalik SK et al: Cystic biliary atresia or atretic choledochal cyst: a continuum in infantile obstructive cholangiopathy. Fetal Pediatr Pathol. 38(6):477-83, 2019
Sanna E et al: Fetal abdominal cysts: antenatal course and postnatal outcomes. J Perinat Med. 47(4):418-21, 2019
Tang J et al: Differentiation between cystic biliary atresia and choledochal cyst: a retrospective analysis. J Paediatr Child Health. 54(4):383-9, 2018
Weng R et al: Prenatal diagnosis and prognosis assessment of congenital choledochal cyst in 21 cases. J Obstet Gynaecol. 36(3):324-7, 2016
Cong X et al: Evaluation and screening ultrasonic signs in the diagnosis of fetal biliary cystic malformation. J Matern Fetal Neonatal Med. 28(17):2100-5, 2015
Jensen KK et al: Antenatal sonographic diagnosis of choledochal cyst: case report and imaging review. J Clin Ultrasound. 43(9):581-3, 2015
Khalil A et al: Outcome of first-trimester fetal abdominal cysts: cohort study and review of the literature. Ultrasound Obstet Gynecol. 43(4):413-9, 2014
Diao M et al: Timing of surgery for prenatally diagnosed asymptomatic choledochal cysts: a prospective randomized study. J Pediatr Surg. 47(3):506-12, 2012
Ruiz-Elizalde AR et al: A practical algorithm for accurate diagnosis and treatment of perinatally identified biliary ductal dilation: three cases that underscore the importance of an individualised approach. J Matern Fetal Neonatal Med. 22(7):622-8, 2009
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Definitions
Choledochal cyst (CC): Congenital cystic dilatation of extrahepatic ± intrahepatic bile ducts
CC is "incomplete" obstruction
Cystic biliary atresia (CBA): Extrahepatic bile duct terminates blindly at caudal end
Complete biliary obstruction
CBA seen in 13-44% with CC
Biliary atresia (BA): Progressive fibroobliterative disease of intrahepatic + extrahepatic bile ducts
IMAGING
General Features
Ultrasonographic Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Hattori K et al: Cyst size in fetuses with biliary cystic malformation: an exploration of the etiology of congenital biliary dilatation. Pediatr Gastroenterol Hepatol Nutr. 23(6):531-8, 2020
Mahalik SK et al: Cystic biliary atresia or atretic choledochal cyst: a continuum in infantile obstructive cholangiopathy. Fetal Pediatr Pathol. 38(6):477-83, 2019
Sanna E et al: Fetal abdominal cysts: antenatal course and postnatal outcomes. J Perinat Med. 47(4):418-21, 2019
Tang J et al: Differentiation between cystic biliary atresia and choledochal cyst: a retrospective analysis. J Paediatr Child Health. 54(4):383-9, 2018
Weng R et al: Prenatal diagnosis and prognosis assessment of congenital choledochal cyst in 21 cases. J Obstet Gynaecol. 36(3):324-7, 2016
Cong X et al: Evaluation and screening ultrasonic signs in the diagnosis of fetal biliary cystic malformation. J Matern Fetal Neonatal Med. 28(17):2100-5, 2015
Jensen KK et al: Antenatal sonographic diagnosis of choledochal cyst: case report and imaging review. J Clin Ultrasound. 43(9):581-3, 2015
Khalil A et al: Outcome of first-trimester fetal abdominal cysts: cohort study and review of the literature. Ultrasound Obstet Gynecol. 43(4):413-9, 2014
Diao M et al: Timing of surgery for prenatally diagnosed asymptomatic choledochal cysts: a prospective randomized study. J Pediatr Surg. 47(3):506-12, 2012
Ruiz-Elizalde AR et al: A practical algorithm for accurate diagnosis and treatment of perinatally identified biliary ductal dilation: three cases that underscore the importance of an individualised approach. J Matern Fetal Neonatal Med. 22(7):622-8, 2009
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