link
Bookmarks
Cochlear Nerve and Cochlear Nerve Canal Aplasia-Hypoplasia
Caroline D. Robson, MBChB
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Log inSubscribe
0
4
5
6

KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Pathology

          • Clinical Issues

            • Diagnostic Checklist

              TERMINOLOGY

              • Abbreviations

                • Cochlear nerve canal (CNC)
              • Synonyms

                • Cochlear aperture stenosis or atresia
              • Definitions

                • CNC hypoplasia-aplasia: Narrowing or absence of CNC
                • Cochlear nerve deficiency (CND): CN hypoplasia or absence (aplasia)

              IMAGING

              • General Features

                • Imaging Recommendations

                  • CT Findings

                    • MR Findings

                      DIFFERENTIAL DIAGNOSIS

                        PATHOLOGY

                        • General Features

                          CLINICAL ISSUES

                          • Presentation

                            • Demographics

                              • Treatment

                                DIAGNOSTIC CHECKLIST

                                • Consider

                                  • Image Interpretation Pearls

                                    • Reporting Tips

                                      Selected References

                                      1. Birman CS et al: Cochlear implant outcomes in cochlea nerve aplasia and hypoplasia. Otol Neurotol. 37(5):438-45, 2016
                                      2. Nixon JN et al: Temporal bone and cranial nerve findings in pontine tegmental cap dysplasia. Neuroradiology. 58(2):179-87, 2016
                                      3. Wilkins A et al: Frequent association of cochlear nerve canal stenosis with pediatric sensorineural hearing loss. Arch Otolaryngol Head Neck Surg. 138(4):383-8, 2012
                                      4. Miyasaka M et al: CT and MR imaging for pediatric cochlear implantation: emphasis on the relationship between the cochlear nerve canal and the cochlear nerve. Pediatr Radiol. 40(9):1509-16, 2010
                                      5. Laury AM et al: Etiology of unilateral neural hearing loss in children. Int J Pediatr Otorhinolaryngol. 73(3):417-27, 2009
                                      6. Sennaroglu L et al: Preliminary results of auditory brainstem implantation in prelingually deaf children with inner ear malformations including severe stenosis of the cochlear aperture and aplasia of the cochlear nerve. Otol Neurotol. 30(6):708-15, 2009
                                      7. Kono T: Computed tomographic features of the bony canal of the cochlear nerve in pediatric patients with unilateral sensorineural hearing loss. Radiat Med. 26(3):115-9, 2008
                                      8. Adunka OF et al: Value of computed tomography in the evaluation of children with cochlear nerve deficiency. Otol Neurotol. 28(5):597-604, 2007
                                      9. Ito K et al: Isolated cochlear nerve hypoplasia with various internal auditory meatus deformities in children. Ann Otol Rhinol Laryngol. 116(7):520-4, 2007
                                      10. Komatsubara S et al: Evaluation of cochlear nerve imaging in severe congenital sensorineural hearing loss. ORL J Otorhinolaryngol Relat Spec. 69(3):198-202, 2007
                                      11. Colletti V et al: Auditory brainstem implant (ABI): new frontiers in adults and children. Otolaryngol Head Neck Surg. 133(1):126-38, 2005
                                      12. Glastonbury CM et al: Imaging findings of cochlear nerve deficiency. AJNR Am J Neuroradiol. 23(4):635-43, 2002
                                      13. Stjernholm C et al: Dimensions of the cochlear nerve canal: a radioanatomic investigation. Acta Otolaryngol. 122(1):43-8, 2002
                                      14. Fatterpekar GM et al: Hypoplasia of the bony canal for the cochlear nerve in patients with congenital sensorineural hearing loss: initial observations. Radiology. 215(1):243-6, 2000
                                      15. Casselman JW et al: Aplasia and hypoplasia of the vestibulocochlear nerve: diagnosis with MR imaging. Radiology. 202(3):773-81, 1997
                                      Related Anatomy
                                      Loading...
                                      Related Differential Diagnoses
                                      Loading...
                                      References
                                      Tables

                                      Tables

                                      KEY FACTS

                                      • Terminology

                                        • Imaging

                                          • Top Differential Diagnoses

                                            • Pathology

                                              • Clinical Issues

                                                • Diagnostic Checklist

                                                  TERMINOLOGY

                                                  • Abbreviations

                                                    • Cochlear nerve canal (CNC)
                                                  • Synonyms

                                                    • Cochlear aperture stenosis or atresia
                                                  • Definitions

                                                    • CNC hypoplasia-aplasia: Narrowing or absence of CNC
                                                    • Cochlear nerve deficiency (CND): CN hypoplasia or absence (aplasia)

                                                  IMAGING

                                                  • General Features

                                                    • Imaging Recommendations

                                                      • CT Findings

                                                        • MR Findings

                                                          DIFFERENTIAL DIAGNOSIS

                                                            PATHOLOGY

                                                            • General Features

                                                              CLINICAL ISSUES

                                                              • Presentation

                                                                • Demographics

                                                                  • Treatment

                                                                    DIAGNOSTIC CHECKLIST

                                                                    • Consider

                                                                      • Image Interpretation Pearls

                                                                        • Reporting Tips

                                                                          Selected References

                                                                          1. Birman CS et al: Cochlear implant outcomes in cochlea nerve aplasia and hypoplasia. Otol Neurotol. 37(5):438-45, 2016
                                                                          2. Nixon JN et al: Temporal bone and cranial nerve findings in pontine tegmental cap dysplasia. Neuroradiology. 58(2):179-87, 2016
                                                                          3. Wilkins A et al: Frequent association of cochlear nerve canal stenosis with pediatric sensorineural hearing loss. Arch Otolaryngol Head Neck Surg. 138(4):383-8, 2012
                                                                          4. Miyasaka M et al: CT and MR imaging for pediatric cochlear implantation: emphasis on the relationship between the cochlear nerve canal and the cochlear nerve. Pediatr Radiol. 40(9):1509-16, 2010
                                                                          5. Laury AM et al: Etiology of unilateral neural hearing loss in children. Int J Pediatr Otorhinolaryngol. 73(3):417-27, 2009
                                                                          6. Sennaroglu L et al: Preliminary results of auditory brainstem implantation in prelingually deaf children with inner ear malformations including severe stenosis of the cochlear aperture and aplasia of the cochlear nerve. Otol Neurotol. 30(6):708-15, 2009
                                                                          7. Kono T: Computed tomographic features of the bony canal of the cochlear nerve in pediatric patients with unilateral sensorineural hearing loss. Radiat Med. 26(3):115-9, 2008
                                                                          8. Adunka OF et al: Value of computed tomography in the evaluation of children with cochlear nerve deficiency. Otol Neurotol. 28(5):597-604, 2007
                                                                          9. Ito K et al: Isolated cochlear nerve hypoplasia with various internal auditory meatus deformities in children. Ann Otol Rhinol Laryngol. 116(7):520-4, 2007
                                                                          10. Komatsubara S et al: Evaluation of cochlear nerve imaging in severe congenital sensorineural hearing loss. ORL J Otorhinolaryngol Relat Spec. 69(3):198-202, 2007
                                                                          11. Colletti V et al: Auditory brainstem implant (ABI): new frontiers in adults and children. Otolaryngol Head Neck Surg. 133(1):126-38, 2005
                                                                          12. Glastonbury CM et al: Imaging findings of cochlear nerve deficiency. AJNR Am J Neuroradiol. 23(4):635-43, 2002
                                                                          13. Stjernholm C et al: Dimensions of the cochlear nerve canal: a radioanatomic investigation. Acta Otolaryngol. 122(1):43-8, 2002
                                                                          14. Fatterpekar GM et al: Hypoplasia of the bony canal for the cochlear nerve in patients with congenital sensorineural hearing loss: initial observations. Radiology. 215(1):243-6, 2000
                                                                          15. Casselman JW et al: Aplasia and hypoplasia of the vestibulocochlear nerve: diagnosis with MR imaging. Radiology. 202(3):773-81, 1997