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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Congenital nasal pyriform aperture stenosis (CNPAS)
Definitions
- Pyriform aperture (PA): Single triangular bony opening of anterior skull to nasal passages
- Anterior nasal passages separated by septal cartilage
- CNPAS: Narrowing of single bony opening by characteristic bilateral maxillary bony anomalies
- Pyriform aperture (PA): Single triangular bony opening of anterior skull to nasal passages
IMAGING
General Features
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Smith MM et al: Pediatric nasal obstruction. Otolaryngol Clin North Am. 51(5):971-85, 2018
- Ginat DT et al: CT and MRI of congenital nasal lesions in syndromic conditions. Pediatr Radiol. 45(7):1056-65, 2015
- Wormald R et al: Congenital nasal pyriform aperture stenosis 5.7 mm or less is associated with surgical intervention: a pooled case series. Int J Pediatr Otorhinolaryngol. 79(11):1802-5, 2015
- Wine TM et al: Congenital nasal pyriform aperture stenosis: is there a role for nasal dilation? JAMA Otolaryngol Head Neck Surg. 140(4):352-6, 2014
- Devambez M et al: Congenital nasal pyriform aperture stenosis: diagnosis and management. Cleft Palate Craniofac J. 46(3):262-7, 2009
- Sultan B et al: Congenital nasal pyriform aperture stenosis: feeding evaluation and management. Int J Pediatr Otorhinolaryngol. 73(8):1080-4, 2009
- Tate JR et al: Congenital nasal pyriform aperture stenosis. Otolaryngol Clin North Am. 42(3):521-5, 2009
- Osovsky M et al: Congenital pyriform aperture stenosis. Pediatr Radiol. 37(1):97-9, 2007
- Hall RK: Solitary median maxillary central incisor (SMMCI) syndrome. Orphanet J Rare Dis. 1:12, 2006
- Vercruysse JP et al: Congenital nasal pyriform aperture stenosis: a rare cause of neonatal nasal obstruction. J Pediatr Surg. 41(4):e5-7, 2006
- Bignault A et al: Congenital nasal piriform aperture stenosis. AJNR Am J Neuroradiol. 15(5):877-8, 1994
- Ey EH et al: Bony inlet stenosis as a cause of nasal airway obstruction. Radiology. 168(2):477-9, 1988
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Congenital nasal pyriform aperture stenosis (CNPAS)
Definitions
- Pyriform aperture (PA): Single triangular bony opening of anterior skull to nasal passages
- Anterior nasal passages separated by septal cartilage
- CNPAS: Narrowing of single bony opening by characteristic bilateral maxillary bony anomalies
- Pyriform aperture (PA): Single triangular bony opening of anterior skull to nasal passages
IMAGING
General Features
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Smith MM et al: Pediatric nasal obstruction. Otolaryngol Clin North Am. 51(5):971-85, 2018
- Ginat DT et al: CT and MRI of congenital nasal lesions in syndromic conditions. Pediatr Radiol. 45(7):1056-65, 2015
- Wormald R et al: Congenital nasal pyriform aperture stenosis 5.7 mm or less is associated with surgical intervention: a pooled case series. Int J Pediatr Otorhinolaryngol. 79(11):1802-5, 2015
- Wine TM et al: Congenital nasal pyriform aperture stenosis: is there a role for nasal dilation? JAMA Otolaryngol Head Neck Surg. 140(4):352-6, 2014
- Devambez M et al: Congenital nasal pyriform aperture stenosis: diagnosis and management. Cleft Palate Craniofac J. 46(3):262-7, 2009
- Sultan B et al: Congenital nasal pyriform aperture stenosis: feeding evaluation and management. Int J Pediatr Otorhinolaryngol. 73(8):1080-4, 2009
- Tate JR et al: Congenital nasal pyriform aperture stenosis. Otolaryngol Clin North Am. 42(3):521-5, 2009
- Osovsky M et al: Congenital pyriform aperture stenosis. Pediatr Radiol. 37(1):97-9, 2007
- Hall RK: Solitary median maxillary central incisor (SMMCI) syndrome. Orphanet J Rare Dis. 1:12, 2006
- Vercruysse JP et al: Congenital nasal pyriform aperture stenosis: a rare cause of neonatal nasal obstruction. J Pediatr Surg. 41(4):e5-7, 2006
- Bignault A et al: Congenital nasal piriform aperture stenosis. AJNR Am J Neuroradiol. 15(5):877-8, 1994
- Ey EH et al: Bony inlet stenosis as a cause of nasal airway obstruction. Radiology. 168(2):477-9, 1988
