Cor triatriatum dexter: Analogous abnormality in right atrium
Definitions
Cor triatriatum sinister: Fibromuscular diaphragm or membrane dividing left atrium into 2 chambers
Posterior (proximal or accessory) chamber receives all or part of pulmonary veins
Anterior (distal or left atrium) chamber connects to left atrial appendage (LAA) and mitral valve
Communication between chambers through defect of varying size in membrane
Accessory chamber may connect to right atrium only or have total anomalous venous return/connection (TAPVR/C)
Cor triatriatum dexter: Analogous abnormality in right atrium; due to persistence of right valve of sinus venosus
2 right atrial chambers
Sinus venarum receiving superior vena cava (SVC) and inferior vena cava (IVC)
Trabeculated portion connecting to tricuspid valve
May mimic Ebstein anomaly
IMAGING
General Features
CT Findings
MR Findings
Echocardiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Treatment
Selected References
Diestro JDB et al: Cor triatriatum and stroke. BMJ Case Rep. 2017, 2017
Li WW et al: Cathether-based interventional strategies for cor triatriatum in the adult - feasibility study through a hybrid approach. BMC Cardiovasc Disord. 15:68, 2015
Barrea C et al: Images in cardiovascular medicine: cor triatriatum dexter mimicking Ebstein disease. Circulation. 120(11):e86-8, 2009
Thakrar A et al: Cor triatriatum: the utility of cardiovascular imaging. Can J Cardiol. 23(2):143-5, 2007
Modi KA et al: Diagnosis and surgical correction of cor triatriatum in an adult: combined use of transesophageal and contrast echocardiography, and a review of literature. Echocardiography. 23(6):506-9, 2006
Sarikouch S et al: Adult congenital heart disease: cor triatriatum dextrum. J Thorac Cardiovasc Surg. 132(1):164-5, 2006
Slight RD et al: Cor-triatriatum sinister presenting in the adult as mitral stenosis: an analysis of factors which may be relevant in late presentation. Heart Lung Circ. 14(1):8-12, 2005
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
TERMINOLOGY
Synonyms
Usually refers to cor triatriatum sinister
Cor triatriatum dexter: Analogous abnormality in right atrium
Definitions
Cor triatriatum sinister: Fibromuscular diaphragm or membrane dividing left atrium into 2 chambers
Posterior (proximal or accessory) chamber receives all or part of pulmonary veins
Anterior (distal or left atrium) chamber connects to left atrial appendage (LAA) and mitral valve
Communication between chambers through defect of varying size in membrane
Accessory chamber may connect to right atrium only or have total anomalous venous return/connection (TAPVR/C)
Cor triatriatum dexter: Analogous abnormality in right atrium; due to persistence of right valve of sinus venosus
2 right atrial chambers
Sinus venarum receiving superior vena cava (SVC) and inferior vena cava (IVC)
Trabeculated portion connecting to tricuspid valve
May mimic Ebstein anomaly
IMAGING
General Features
CT Findings
MR Findings
Echocardiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Treatment
Selected References
Diestro JDB et al: Cor triatriatum and stroke. BMJ Case Rep. 2017, 2017
Li WW et al: Cathether-based interventional strategies for cor triatriatum in the adult - feasibility study through a hybrid approach. BMC Cardiovasc Disord. 15:68, 2015
Barrea C et al: Images in cardiovascular medicine: cor triatriatum dexter mimicking Ebstein disease. Circulation. 120(11):e86-8, 2009
Thakrar A et al: Cor triatriatum: the utility of cardiovascular imaging. Can J Cardiol. 23(2):143-5, 2007
Modi KA et al: Diagnosis and surgical correction of cor triatriatum in an adult: combined use of transesophageal and contrast echocardiography, and a review of literature. Echocardiography. 23(6):506-9, 2006
Sarikouch S et al: Adult congenital heart disease: cor triatriatum dextrum. J Thorac Cardiovasc Surg. 132(1):164-5, 2006
Slight RD et al: Cor-triatriatum sinister presenting in the adult as mitral stenosis: an analysis of factors which may be relevant in late presentation. Heart Lung Circ. 14(1):8-12, 2005
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