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Cor Triatriatum
Suhny Abbara, MD, FACR, FSCCT; Cameron Hassani, MD
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        TERMINOLOGY

        • Synonyms

          • Usually refers to cor triatriatum sinister
          • Cor triatriatum dexter: Analogous abnormality in right atrium
        • Definitions

          • Cor triatriatum sinister: Fibromuscular diaphragm or membrane dividing left atrium into 2 chambers
            • Posterior (proximal or accessory) chamber receives all or part of pulmonary veins
            • Anterior (distal or left atrium) chamber connects to left atrial appendage (LAA) and mitral valve
            • Communication between chambers through defect of varying size in membrane
            • Accessory chamber may connect to right atrium only or have total anomalous venous return/connection (TAPVR/C)
          • Cor triatriatum dexter: Analogous abnormality in right atrium; due to persistence of right valve of sinus venosus
            • 2 right atrial chambers
              • Sinus venarum receiving superior vena cava (SVC) and inferior vena cava (IVC)
              • Trabeculated portion connecting to tricuspid valve
            • May mimic Ebstein anomaly

        IMAGING

        • General Features

          • CT Findings

            • MR Findings

              • Echocardiographic Findings

                • Imaging Recommendations

                  DIFFERENTIAL DIAGNOSIS

                    PATHOLOGY

                    • General Features

                      • Staging, Grading, & Classification

                        CLINICAL ISSUES

                        • Presentation

                          • Demographics

                            • Treatment

                              Selected References

                              1. Diestro JDB et al: Cor triatriatum and stroke. BMJ Case Rep. 2017, 2017
                              2. Li WW et al: Cathether-based interventional strategies for cor triatriatum in the adult - feasibility study through a hybrid approach. BMC Cardiovasc Disord. 15:68, 2015
                              3. Barrea C et al: Images in cardiovascular medicine: cor triatriatum dexter mimicking Ebstein disease. Circulation. 120(11):e86-8, 2009
                              4. Thakrar A et al: Cor triatriatum: the utility of cardiovascular imaging. Can J Cardiol. 23(2):143-5, 2007
                              5. Modi KA et al: Diagnosis and surgical correction of cor triatriatum in an adult: combined use of transesophageal and contrast echocardiography, and a review of literature. Echocardiography. 23(6):506-9, 2006
                              6. Sarikouch S et al: Adult congenital heart disease: cor triatriatum dextrum. J Thorac Cardiovasc Surg. 132(1):164-5, 2006
                              7. Slight RD et al: Cor-triatriatum sinister presenting in the adult as mitral stenosis: an analysis of factors which may be relevant in late presentation. Heart Lung Circ. 14(1):8-12, 2005
                              Related Anatomy
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                              Related Differential Diagnoses
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                              References
                              Tables

                              Tables

                              KEY FACTS

                              • Terminology

                                • Imaging

                                  • Top Differential Diagnoses

                                    TERMINOLOGY

                                    • Synonyms

                                      • Usually refers to cor triatriatum sinister
                                      • Cor triatriatum dexter: Analogous abnormality in right atrium
                                    • Definitions

                                      • Cor triatriatum sinister: Fibromuscular diaphragm or membrane dividing left atrium into 2 chambers
                                        • Posterior (proximal or accessory) chamber receives all or part of pulmonary veins
                                        • Anterior (distal or left atrium) chamber connects to left atrial appendage (LAA) and mitral valve
                                        • Communication between chambers through defect of varying size in membrane
                                        • Accessory chamber may connect to right atrium only or have total anomalous venous return/connection (TAPVR/C)
                                      • Cor triatriatum dexter: Analogous abnormality in right atrium; due to persistence of right valve of sinus venosus
                                        • 2 right atrial chambers
                                          • Sinus venarum receiving superior vena cava (SVC) and inferior vena cava (IVC)
                                          • Trabeculated portion connecting to tricuspid valve
                                        • May mimic Ebstein anomaly

                                    IMAGING

                                    • General Features

                                      • CT Findings

                                        • MR Findings

                                          • Echocardiographic Findings

                                            • Imaging Recommendations

                                              DIFFERENTIAL DIAGNOSIS

                                                PATHOLOGY

                                                • General Features

                                                  • Staging, Grading, & Classification

                                                    CLINICAL ISSUES

                                                    • Presentation

                                                      • Demographics

                                                        • Treatment

                                                          Selected References

                                                          1. Diestro JDB et al: Cor triatriatum and stroke. BMJ Case Rep. 2017, 2017
                                                          2. Li WW et al: Cathether-based interventional strategies for cor triatriatum in the adult - feasibility study through a hybrid approach. BMC Cardiovasc Disord. 15:68, 2015
                                                          3. Barrea C et al: Images in cardiovascular medicine: cor triatriatum dexter mimicking Ebstein disease. Circulation. 120(11):e86-8, 2009
                                                          4. Thakrar A et al: Cor triatriatum: the utility of cardiovascular imaging. Can J Cardiol. 23(2):143-5, 2007
                                                          5. Modi KA et al: Diagnosis and surgical correction of cor triatriatum in an adult: combined use of transesophageal and contrast echocardiography, and a review of literature. Echocardiography. 23(6):506-9, 2006
                                                          6. Sarikouch S et al: Adult congenital heart disease: cor triatriatum dextrum. J Thorac Cardiovasc Surg. 132(1):164-5, 2006
                                                          7. Slight RD et al: Cor-triatriatum sinister presenting in the adult as mitral stenosis: an analysis of factors which may be relevant in late presentation. Heart Lung Circ. 14(1):8-12, 2005