Cystic fibrosis (CF): Autosomal recessive multisystem disorder caused by dysfunctional chloride ion transport across epithelial surfaces
Presenting symptoms of CF in infants & young children are most commonly GI related
IMAGING
General Features
Radiographic Findings
Fluoroscopic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Levitte S et al: Clinical use of shear-wave elastography for detecting liver fibrosis in children and adolescents with cystic fibrosis. Pediatr Radiol. 51(8):1369-77, 2021
Konrad J et al: Changing paradigms in the treatment of gastrointestinal complications of cystic fibrosis in the era of cystic fibrosis transmembrane conductance regulator modulators. Paediatr Respir Rev. ePub, 2020
Toledano MB et al: The emerging burden of liver disease in cystic fibrosis patients: a UK nationwide study. PLoS One. 14(4):e0212779, 2019
Dos Santos ALM et al: cystic fibrosis: clinical phenotypes in children and adolescents. Pediatr Gastroenterol Hepatol Nutr. 21(4):306-14, 2018
Assis DN et al: Gastrointestinal disorders in cystic fibrosis. Clin Chest Med. 37(1):109-18, 2016
Demeyer S et al: Beyond pancreatic insufficiency and liver disease in cystic fibrosis. Eur J Pediatr. 175(7):881-94, 2016
Kelly T et al: Gastrointestinal manifestations of cystic fibrosis. Dig Dis Sci. 60(7):1903-13, 2015
Lavelle LP et al: Cystic fibrosis below the diaphragm: abdominal findings in adult patients. Radiographics. 35(3):680-95, 2015
Leung DH et al: Baseline ultrasound and clinical correlates in children with cystic fibrosis. J Pediatr. 167(4):862-868.e2, 2015
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
TERMINOLOGY
Definitions
Cystic fibrosis (CF): Autosomal recessive multisystem disorder caused by dysfunctional chloride ion transport across epithelial surfaces
Presenting symptoms of CF in infants & young children are most commonly GI related
IMAGING
General Features
Radiographic Findings
Fluoroscopic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Levitte S et al: Clinical use of shear-wave elastography for detecting liver fibrosis in children and adolescents with cystic fibrosis. Pediatr Radiol. 51(8):1369-77, 2021
Konrad J et al: Changing paradigms in the treatment of gastrointestinal complications of cystic fibrosis in the era of cystic fibrosis transmembrane conductance regulator modulators. Paediatr Respir Rev. ePub, 2020
Toledano MB et al: The emerging burden of liver disease in cystic fibrosis patients: a UK nationwide study. PLoS One. 14(4):e0212779, 2019
Dos Santos ALM et al: cystic fibrosis: clinical phenotypes in children and adolescents. Pediatr Gastroenterol Hepatol Nutr. 21(4):306-14, 2018
Assis DN et al: Gastrointestinal disorders in cystic fibrosis. Clin Chest Med. 37(1):109-18, 2016
Demeyer S et al: Beyond pancreatic insufficiency and liver disease in cystic fibrosis. Eur J Pediatr. 175(7):881-94, 2016
Kelly T et al: Gastrointestinal manifestations of cystic fibrosis. Dig Dis Sci. 60(7):1903-13, 2015
Lavelle LP et al: Cystic fibrosis below the diaphragm: abdominal findings in adult patients. Radiographics. 35(3):680-95, 2015
Leung DH et al: Baseline ultrasound and clinical correlates in children with cystic fibrosis. J Pediatr. 167(4):862-868.e2, 2015
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