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KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Cystic fibrosis (CF)
Synonyms
- Mucoviscidosis, fibrocystic disease of pancreas
Definitions
- Autosomal recessive multisystem disorder caused by dysfunctional chloride ion transport across epithelial surfaces → thickening of secretions (e.g., mucus, digestive fluids, sweat)
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Reporting Tips
Selected References
- Berkhout MC et al: CT-abnormalities, bacteriology and symptoms of sinonasal disease in children with Cystic Fibrosis. J Cyst Fibros. ePub, 2016
- Ferris H et al: Computed tomography dose optimisation in cystic fibrosis: a review. World J Radiol. 8(4):331-41, 2016
- Kuo W et al: Multicentre chest computed tomography standardisation in children and adolescents with cystic fibrosis: the way forward. Eur Respir J. ePub, 2016
- Murphy KP et al: Imaging of cystic fibrosis and pediatric bronchiectasis. AJR Am J Roentgenol. 206(3):448-54, 2016
- Mets OM et al: Emphysema is common in lungs of cystic fibrosis lung transplantation patients: a histopathological and computed tomography Study. PLoS One. 10(6):e0128062, 2015
- Sanders DB et al: Chest computed tomography predicts the frequency of pulmonary exacerbations in children with cystic fibrosis. Ann Am Thorac Soc. 12(1):64-9, 2015
- van Beek EJ: Personalizing medicine. Quantification of cystic fibrosis using computed tomography. Am J Respir Crit Care Med. 191(10):1098-9, 2015
- Wielpütz MO et al: Imaging modalities in cystic fibrosis: emerging role of MRI. Curr Opin Pulm Med. 21(6):609-16, 2015
- Xu H et al: [Allergic bronchopulmonary aspergillosis: a report of four cases with literature review.] Zhonghua Er Ke Za Zhi. 53(7):532-6, 2015
- Calder AD et al: Scoring of chest CT in children with cystic fibrosis: state of the art. Pediatr Radiol. 44(12):1496-506, 2014
- Locke LW et al: Quantitative imaging of airway liquid absorption in cystic fibrosis. Eur Respir J. 44(3):675-84, 2014
- Fleck R et al: Aortopulmonary collateral flow in cystic fibrosis assessed with phase-contrast MRI. Pediatr Radiol. 43(10):1279-86, 2013
- Vidal V et al: Bronchial artery embolization in adults with cystic fibrosis: impact on the clinical course and survival. J Vasc Interv Radiol. 17(6):953-8, 2006
- Grum CM et al: Chest radiographic findings in cystic fibrosis. Semin Respir Infect. 7(3):193-209, 1992
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Cystic fibrosis (CF)
Synonyms
- Mucoviscidosis, fibrocystic disease of pancreas
Definitions
- Autosomal recessive multisystem disorder caused by dysfunctional chloride ion transport across epithelial surfaces → thickening of secretions (e.g., mucus, digestive fluids, sweat)
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Reporting Tips
Selected References
- Berkhout MC et al: CT-abnormalities, bacteriology and symptoms of sinonasal disease in children with Cystic Fibrosis. J Cyst Fibros. ePub, 2016
- Ferris H et al: Computed tomography dose optimisation in cystic fibrosis: a review. World J Radiol. 8(4):331-41, 2016
- Kuo W et al: Multicentre chest computed tomography standardisation in children and adolescents with cystic fibrosis: the way forward. Eur Respir J. ePub, 2016
- Murphy KP et al: Imaging of cystic fibrosis and pediatric bronchiectasis. AJR Am J Roentgenol. 206(3):448-54, 2016
- Mets OM et al: Emphysema is common in lungs of cystic fibrosis lung transplantation patients: a histopathological and computed tomography Study. PLoS One. 10(6):e0128062, 2015
- Sanders DB et al: Chest computed tomography predicts the frequency of pulmonary exacerbations in children with cystic fibrosis. Ann Am Thorac Soc. 12(1):64-9, 2015
- van Beek EJ: Personalizing medicine. Quantification of cystic fibrosis using computed tomography. Am J Respir Crit Care Med. 191(10):1098-9, 2015
- Wielpütz MO et al: Imaging modalities in cystic fibrosis: emerging role of MRI. Curr Opin Pulm Med. 21(6):609-16, 2015
- Xu H et al: [Allergic bronchopulmonary aspergillosis: a report of four cases with literature review.] Zhonghua Er Ke Za Zhi. 53(7):532-6, 2015
- Calder AD et al: Scoring of chest CT in children with cystic fibrosis: state of the art. Pediatr Radiol. 44(12):1496-506, 2014
- Locke LW et al: Quantitative imaging of airway liquid absorption in cystic fibrosis. Eur Respir J. 44(3):675-84, 2014
- Fleck R et al: Aortopulmonary collateral flow in cystic fibrosis assessed with phase-contrast MRI. Pediatr Radiol. 43(10):1279-86, 2013
- Vidal V et al: Bronchial artery embolization in adults with cystic fibrosis: impact on the clinical course and survival. J Vasc Interv Radiol. 17(6):953-8, 2006
- Grum CM et al: Chest radiographic findings in cystic fibrosis. Semin Respir Infect. 7(3):193-209, 1992
