Fibromatoses: Variety of benign fibroblastic proliferations and fibroblastic soft tissue neoplasms
Categorized by anatomic location and patient age
Superficial (slow growing and small)
Palmar fibromatosis (Dupuytren contracture)
Plantar fibromatosis (Ledderhose disease)
Penile fibromatosis (Peyronie disease)
Knuckle pads
Calcifying aponeurotic fibroma (children)
Lipofibromatosis (children)
Inclusion body fibromatosis (children)
Deep (fast growing and large)
Desmoid-type fibromatosis (Intraabdominal or extraabdominal)
Abdominal wall fibromatosis
Fibromatosis colli (children)
Myofibroma (children)
Myofibromatosis (children)
Associated Syndromes
Gardner syndrome
10% of affected patients develop desmoid-type fibromatosis (usually intraabdominal, small, and multiple)
Tend to follow surgery (within 4 years after colectomy)
High rate of recurrent disease after surgical resection
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Image-Guided Biopsy
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
George V et al: Chronic fibrosing conditions in abdominal imaging. Radiographics. 33(4):1053-80, 2013
Nam SJ et al: Imaging of primary chest wall tumors with radiologic-pathologic correlation. Radiographics. 31(3):749-70, 2011
Souza FF et al: Case report. PET/CT appearance of desmoid tumour of the chest wall. Br J Radiol. 83(986):e39-42, 2010
Bölke E et al: Chest wall and intrathoracic desmoid tumors: surgical experience and review of the literature. Eur J Med Res. 14(6):240-3, 2009
Murphey MD et al: From the archives of the AFIP: musculoskeletal fibromatoses: radiologic-pathologic correlation. Radiographics. 29(7):2143-73, 2009
Datir A et al: MRI of soft-tissue masses: the relationship between lesion size, depth, and diagnosis. Clin Radiol. 63(4):373-8; discussion 379-80, 2008
Kreuzberg B et al: Diagnostic problems of abdominal desmoid tumors in various locations. Eur J Radiol. 62(2):180-5, 2007
Lee JC et al: Aggressive fibromatosis: MRI features with pathologic correlation. AJR Am J Roentgenol. 186(1):247-54, 2006
Mendenhall WM et al: Aggressive fibromatosis. Am J Clin Oncol. 28(2):211-5, 2005
Robbin MR et al: Imaging of musculoskeletal fibromatosis. Radiographics. 21(3):585-600, 2001
Siegel MJ: Magnetic resonance imaging of musculoskeletal soft tissue masses. Radiol Clin North Am. 39(4):701-20, 2001
Hartman TE et al: MR imaging of extraabdominal desmoids: differentiation from other neoplasms. AJR Am J Roentgenol. 158(3):581-5, 1992
Casillas J et al: Imaging of intra- and extraabdominal desmoid tumors. Radiographics. 11(6):959-68, 1991
Quinn SF et al: MR imaging in fibromatosis: results in 26 patients with pathologic correlation. AJR Am J Roentgenol. 156(3):539-42, 1991
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Desmoid
Desmoid tumor
Musculoaponeurotic fibromatosis
Aggressive fibromatosis
Deep fibromatosis
Definitions
Fibromatoses: Variety of benign fibroblastic proliferations and fibroblastic soft tissue neoplasms
Categorized by anatomic location and patient age
Superficial (slow growing and small)
Palmar fibromatosis (Dupuytren contracture)
Plantar fibromatosis (Ledderhose disease)
Penile fibromatosis (Peyronie disease)
Knuckle pads
Calcifying aponeurotic fibroma (children)
Lipofibromatosis (children)
Inclusion body fibromatosis (children)
Deep (fast growing and large)
Desmoid-type fibromatosis (Intraabdominal or extraabdominal)
Abdominal wall fibromatosis
Fibromatosis colli (children)
Myofibroma (children)
Myofibromatosis (children)
Associated Syndromes
Gardner syndrome
10% of affected patients develop desmoid-type fibromatosis (usually intraabdominal, small, and multiple)
Tend to follow surgery (within 4 years after colectomy)
High rate of recurrent disease after surgical resection
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Image-Guided Biopsy
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
George V et al: Chronic fibrosing conditions in abdominal imaging. Radiographics. 33(4):1053-80, 2013
Nam SJ et al: Imaging of primary chest wall tumors with radiologic-pathologic correlation. Radiographics. 31(3):749-70, 2011
Souza FF et al: Case report. PET/CT appearance of desmoid tumour of the chest wall. Br J Radiol. 83(986):e39-42, 2010
Bölke E et al: Chest wall and intrathoracic desmoid tumors: surgical experience and review of the literature. Eur J Med Res. 14(6):240-3, 2009
Murphey MD et al: From the archives of the AFIP: musculoskeletal fibromatoses: radiologic-pathologic correlation. Radiographics. 29(7):2143-73, 2009
Datir A et al: MRI of soft-tissue masses: the relationship between lesion size, depth, and diagnosis. Clin Radiol. 63(4):373-8; discussion 379-80, 2008
Kreuzberg B et al: Diagnostic problems of abdominal desmoid tumors in various locations. Eur J Radiol. 62(2):180-5, 2007
Lee JC et al: Aggressive fibromatosis: MRI features with pathologic correlation. AJR Am J Roentgenol. 186(1):247-54, 2006
Mendenhall WM et al: Aggressive fibromatosis. Am J Clin Oncol. 28(2):211-5, 2005
Robbin MR et al: Imaging of musculoskeletal fibromatosis. Radiographics. 21(3):585-600, 2001
Siegel MJ: Magnetic resonance imaging of musculoskeletal soft tissue masses. Radiol Clin North Am. 39(4):701-20, 2001
Hartman TE et al: MR imaging of extraabdominal desmoids: differentiation from other neoplasms. AJR Am J Roentgenol. 158(3):581-5, 1992
Casillas J et al: Imaging of intra- and extraabdominal desmoid tumors. Radiographics. 11(6):959-68, 1991
Quinn SF et al: MR imaging in fibromatosis: results in 26 patients with pathologic correlation. AJR Am J Roentgenol. 156(3):539-42, 1991
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