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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Desmoid
- Desmoid tumor
- Musculoaponeurotic fibromatosis
- Aggressive fibromatosis
- Deep fibromatosis
Definitions
- Fibromatoses: Variety of benign fibroblastic proliferations and fibroblastic soft tissue neoplasms
- Categorized by anatomic location and patient age
- Superficial (slow growing and small)
- Palmar fibromatosis (Dupuytren contracture)
- Plantar fibromatosis (Ledderhose disease)
- Penile fibromatosis (Peyronie disease)
- Knuckle pads
- Calcifying aponeurotic fibroma (children)
- Lipofibromatosis (children)
- Inclusion body fibromatosis (children)
- Deep (fast growing and large)
- Desmoid-type fibromatosis (Intraabdominal or extraabdominal)
- Abdominal wall fibromatosis
- Fibromatosis colli (children)
- Myofibroma (children)
- Myofibromatosis (children)
- Superficial (slow growing and small)
Associated Syndromes
- Gardner syndrome
- 10% of affected patients develop desmoid-type fibromatosis (usually intraabdominal, small, and multiple)
- Tend to follow surgery (within 4 years after colectomy)
- High rate of recurrent disease after surgical resection
- Gardner syndrome
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Image-Guided Biopsy
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- George V et al: Chronic fibrosing conditions in abdominal imaging. Radiographics. 33(4):1053-80, 2013
- Nam SJ et al: Imaging of primary chest wall tumors with radiologic-pathologic correlation. Radiographics. 31(3):749-70, 2011
- Souza FF et al: Case report. PET/CT appearance of desmoid tumour of the chest wall. Br J Radiol. 83(986):e39-42, 2010
- Bölke E et al: Chest wall and intrathoracic desmoid tumors: surgical experience and review of the literature. Eur J Med Res. 14(6):240-3, 2009
- Murphey MD et al: From the archives of the AFIP: musculoskeletal fibromatoses: radiologic-pathologic correlation. Radiographics. 29(7):2143-73, 2009
- Datir A et al: MRI of soft-tissue masses: the relationship between lesion size, depth, and diagnosis. Clin Radiol. 63(4):373-8; discussion 379-80, 2008
- Kreuzberg B et al: Diagnostic problems of abdominal desmoid tumors in various locations. Eur J Radiol. 62(2):180-5, 2007
- Lee JC et al: Aggressive fibromatosis: MRI features with pathologic correlation. AJR Am J Roentgenol. 186(1):247-54, 2006
- Mendenhall WM et al: Aggressive fibromatosis. Am J Clin Oncol. 28(2):211-5, 2005
- Robbin MR et al: Imaging of musculoskeletal fibromatosis. Radiographics. 21(3):585-600, 2001
- Siegel MJ: Magnetic resonance imaging of musculoskeletal soft tissue masses. Radiol Clin North Am. 39(4):701-20, 2001
- Hartman TE et al: MR imaging of extraabdominal desmoids: differentiation from other neoplasms. AJR Am J Roentgenol. 158(3):581-5, 1992
- Casillas J et al: Imaging of intra- and extraabdominal desmoid tumors. Radiographics. 11(6):959-68, 1991
- Quinn SF et al: MR imaging in fibromatosis: results in 26 patients with pathologic correlation. AJR Am J Roentgenol. 156(3):539-42, 1991
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Desmoid
- Desmoid tumor
- Musculoaponeurotic fibromatosis
- Aggressive fibromatosis
- Deep fibromatosis
Definitions
- Fibromatoses: Variety of benign fibroblastic proliferations and fibroblastic soft tissue neoplasms
- Categorized by anatomic location and patient age
- Superficial (slow growing and small)
- Palmar fibromatosis (Dupuytren contracture)
- Plantar fibromatosis (Ledderhose disease)
- Penile fibromatosis (Peyronie disease)
- Knuckle pads
- Calcifying aponeurotic fibroma (children)
- Lipofibromatosis (children)
- Inclusion body fibromatosis (children)
- Deep (fast growing and large)
- Desmoid-type fibromatosis (Intraabdominal or extraabdominal)
- Abdominal wall fibromatosis
- Fibromatosis colli (children)
- Myofibroma (children)
- Myofibromatosis (children)
- Superficial (slow growing and small)
Associated Syndromes
- Gardner syndrome
- 10% of affected patients develop desmoid-type fibromatosis (usually intraabdominal, small, and multiple)
- Tend to follow surgery (within 4 years after colectomy)
- High rate of recurrent disease after surgical resection
- Gardner syndrome
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Image-Guided Biopsy
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- George V et al: Chronic fibrosing conditions in abdominal imaging. Radiographics. 33(4):1053-80, 2013
- Nam SJ et al: Imaging of primary chest wall tumors with radiologic-pathologic correlation. Radiographics. 31(3):749-70, 2011
- Souza FF et al: Case report. PET/CT appearance of desmoid tumour of the chest wall. Br J Radiol. 83(986):e39-42, 2010
- Bölke E et al: Chest wall and intrathoracic desmoid tumors: surgical experience and review of the literature. Eur J Med Res. 14(6):240-3, 2009
- Murphey MD et al: From the archives of the AFIP: musculoskeletal fibromatoses: radiologic-pathologic correlation. Radiographics. 29(7):2143-73, 2009
- Datir A et al: MRI of soft-tissue masses: the relationship between lesion size, depth, and diagnosis. Clin Radiol. 63(4):373-8; discussion 379-80, 2008
- Kreuzberg B et al: Diagnostic problems of abdominal desmoid tumors in various locations. Eur J Radiol. 62(2):180-5, 2007
- Lee JC et al: Aggressive fibromatosis: MRI features with pathologic correlation. AJR Am J Roentgenol. 186(1):247-54, 2006
- Mendenhall WM et al: Aggressive fibromatosis. Am J Clin Oncol. 28(2):211-5, 2005
- Robbin MR et al: Imaging of musculoskeletal fibromatosis. Radiographics. 21(3):585-600, 2001
- Siegel MJ: Magnetic resonance imaging of musculoskeletal soft tissue masses. Radiol Clin North Am. 39(4):701-20, 2001
- Hartman TE et al: MR imaging of extraabdominal desmoids: differentiation from other neoplasms. AJR Am J Roentgenol. 158(3):581-5, 1992
- Casillas J et al: Imaging of intra- and extraabdominal desmoid tumors. Radiographics. 11(6):959-68, 1991
- Quinn SF et al: MR imaging in fibromatosis: results in 26 patients with pathologic correlation. AJR Am J Roentgenol. 156(3):539-42, 1991
