link
Bookmarks
Desmoplastic Fibroma
Behrang Amini, MD, PhD; Stephanie A. Bernard, MD; B. J. Manaster, MD, PhD, FACR
To access 4,300 diagnoses written by the world's leading experts in radiology.Try it free - 15 days
0
3
24
0

KEY FACTS

  • Terminology

    • Imaging

      • Clinical Issues

        TERMINOLOGY

        • Synonyms

          • Not recommended: desmoid tumor of bone
        • Definitions

          • Extremely rare, locally aggressive lesion with bland spindle cells in background of abundant collagen

        IMAGING

        • General Features

          • Imaging Recommendations

            • Radiographic Findings

              • CT Findings

                • MR Findings

                  DIFFERENTIAL DIAGNOSIS

                    PATHOLOGY

                    • General Features

                      • Gross Pathologic & Surgical Features

                        • Microscopic Features

                          CLINICAL ISSUES

                          • Presentation

                            • Demographics

                              • Natural History & Prognosis

                                • Treatment

                                  DIAGNOSTIC CHECKLIST

                                  • Consider

                                    Selected References

                                    1. Kahraman D et al: Desmoplastic fibroma of the jaw bones: a series of twenty-two cases. J Bone Oncol. 26:100333, 2021
                                    2. Suurmeijer AJH et al: Tumours of soft tissue and bone. In Fletcher CDM et al: WHO Classification of Tumours: Soft Tissue and Bone Tumours. IARC Press. 422-3, 2020
                                    3. Fahmy MD et al: Desmoplastic fibroma associated with tuberous sclerosis: case report and literature review. Oral Surg Oral Med Oral Pathol Oral Radiol. 128(2):e92-9, 2019
                                    4. Xu Y et al: Desmoplastic fibroma of the femur with atypical image findings: a case report. Medicine (Baltimore). 97(52):e13787, 2018
                                    5. Okubo T et al: Desmoplastic fibroma of the rib with cystic change: a case report and literature review. Skeletal Radiol. 43(5):703-8, 2014
                                    6. Yin H et al: Desmoplastic fibroma of the spine: a series of 12 cases and outcomes. Spine J. 14(8):1622-8, 2014
                                    7. Wadhwa V et al: Incidental lesion in the femoral metaphysis. Desmoplastic fibroma of the bone. Skeletal Radiol. 42(12):1739-40, 1775-6, 2013
                                    8. Apaydin M et al: Desmoplastic fibroma in humerus. J Med Imaging Radiat Oncol. 52(5):489-90, 2008
                                    9. Rastogi S et al: Desmoplastic fibroma: a report of three cases at unusual locations. Joint Bone Spine. 75(2):222-5, 2008
                                    10. Callahan KS et al: Desmoplastic fibroma of bone with extensive cartilaginous metaplasia. Ann Diagn Pathol. 10(6):343-6, 2006
                                    11. Frick MA et al: Imaging findings in desmoplastic fibroma of bone: distinctive T2 characteristics. AJR Am J Roentgenol. 184(6):1762-7, 2005
                                    12. Hauben EI et al: Desmoplastic fibroma of bone: an immunohistochemical study including beta-catenin expression and mutational analysis for beta-catenin. Hum Pathol. 36(9):1025-30, 2005
                                    13. Bahk WJ et al: Desmoid tumor of bone with enchondromatous nodules, mistaken for chondrosarcoma. Skeletal Radiol. 32(4):223-6, 2003
                                    14. Takazawa K et al: Osteosarcoma arising from desmoplastic fibroma treated 16 years earlier: a case report. J Orthop Sci. 8(6):864-8, 2003
                                    15. Crim JR et al: Desmoplastic fibroma of bone: radiographic analysis. Radiology. 172(3):827-32, 1989
                                    Related Anatomy
                                    Loading...
                                    Related Differential Diagnoses
                                    Loading...
                                    References
                                    Tables

                                    Tables

                                    KEY FACTS

                                    • Terminology

                                      • Imaging

                                        • Clinical Issues

                                          TERMINOLOGY

                                          • Synonyms

                                            • Not recommended: desmoid tumor of bone
                                          • Definitions

                                            • Extremely rare, locally aggressive lesion with bland spindle cells in background of abundant collagen

                                          IMAGING

                                          • General Features

                                            • Imaging Recommendations

                                              • Radiographic Findings

                                                • CT Findings

                                                  • MR Findings

                                                    DIFFERENTIAL DIAGNOSIS

                                                      PATHOLOGY

                                                      • General Features

                                                        • Gross Pathologic & Surgical Features

                                                          • Microscopic Features

                                                            CLINICAL ISSUES

                                                            • Presentation

                                                              • Demographics

                                                                • Natural History & Prognosis

                                                                  • Treatment

                                                                    DIAGNOSTIC CHECKLIST

                                                                    • Consider

                                                                      Selected References

                                                                      1. Kahraman D et al: Desmoplastic fibroma of the jaw bones: a series of twenty-two cases. J Bone Oncol. 26:100333, 2021
                                                                      2. Suurmeijer AJH et al: Tumours of soft tissue and bone. In Fletcher CDM et al: WHO Classification of Tumours: Soft Tissue and Bone Tumours. IARC Press. 422-3, 2020
                                                                      3. Fahmy MD et al: Desmoplastic fibroma associated with tuberous sclerosis: case report and literature review. Oral Surg Oral Med Oral Pathol Oral Radiol. 128(2):e92-9, 2019
                                                                      4. Xu Y et al: Desmoplastic fibroma of the femur with atypical image findings: a case report. Medicine (Baltimore). 97(52):e13787, 2018
                                                                      5. Okubo T et al: Desmoplastic fibroma of the rib with cystic change: a case report and literature review. Skeletal Radiol. 43(5):703-8, 2014
                                                                      6. Yin H et al: Desmoplastic fibroma of the spine: a series of 12 cases and outcomes. Spine J. 14(8):1622-8, 2014
                                                                      7. Wadhwa V et al: Incidental lesion in the femoral metaphysis. Desmoplastic fibroma of the bone. Skeletal Radiol. 42(12):1739-40, 1775-6, 2013
                                                                      8. Apaydin M et al: Desmoplastic fibroma in humerus. J Med Imaging Radiat Oncol. 52(5):489-90, 2008
                                                                      9. Rastogi S et al: Desmoplastic fibroma: a report of three cases at unusual locations. Joint Bone Spine. 75(2):222-5, 2008
                                                                      10. Callahan KS et al: Desmoplastic fibroma of bone with extensive cartilaginous metaplasia. Ann Diagn Pathol. 10(6):343-6, 2006
                                                                      11. Frick MA et al: Imaging findings in desmoplastic fibroma of bone: distinctive T2 characteristics. AJR Am J Roentgenol. 184(6):1762-7, 2005
                                                                      12. Hauben EI et al: Desmoplastic fibroma of bone: an immunohistochemical study including beta-catenin expression and mutational analysis for beta-catenin. Hum Pathol. 36(9):1025-30, 2005
                                                                      13. Bahk WJ et al: Desmoid tumor of bone with enchondromatous nodules, mistaken for chondrosarcoma. Skeletal Radiol. 32(4):223-6, 2003
                                                                      14. Takazawa K et al: Osteosarcoma arising from desmoplastic fibroma treated 16 years earlier: a case report. J Orthop Sci. 8(6):864-8, 2003
                                                                      15. Crim JR et al: Desmoplastic fibroma of bone: radiographic analysis. Radiology. 172(3):827-32, 1989