Sagittal division of spinal cord into 2 hemicords, each with 1 central canal, dorsal horn, and ventral horn
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nonvascular Interventions
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Morioka T et al: Neurosurgical pathology of limited dorsal myeloschisis. Childs Nerv Syst. 34(2):293-303, 2018
Lee SM et al: Limited dorsal myeloschisis and congenital dermal sinus: comparison of clinical and MR imaging features. AJNR Am J Neuroradiol. 38(1):176-82, 2017
Schmidt C et al: Meningocele manqué: a comprehensive review of this enigmatic finding in occult spinal dysraphism. Childs Nerv Syst. 33(7):1065-71, 2017
McComb JG: A practical clinical classification of spinal neural tube defects. Childs Nerv Syst. 31(10):1641-57, 2015
Alzhrani GA et al: Multi-level split cord malformation: do we need a new classification? J Clin Imaging Sci. 4:32, 2014
Burnei G et al: L3-L5 Teratological spondylolysis with diastematomyelia and L4 radicular syndrome followed by spondyloschisis without myelomeningocele due to somato-arcuate shifting. Spine J. 5(1):202-4, 2014
Muroi A et al: Split medulla in association with multiple closed neural tube defects. Childs Nerv Syst. 26(7):967-71, 2010
Ayvaz M et al: Is it necessary to operate all split cord malformations before corrective surgery for patients with congenital spinal deformities? Spine (Phila Pa 1976). 34(22):2413-8, 2009
Liu W et al: Characteristics of osseous septum of split cord malformation in patients presenting with scoliosis: a retrospective study of 48 cases. Pediatr Neurosurg. 2009;45(5):350-3. Epub 2009 Nov 11. Erratum in: Pediatr Neurosurg. 45(5):406, 2009
Rowley VB et al: Lumbar split cord malformation with lateral hemimyelomeningocele and associated Chiari II malformation and other visceral and osseous anomalies: a case report. J Comput Assist Tomogr. 33(6):923-6, 2009
Ozturk E et al: Split-cord malformation and accompanying anomalies. J Neuroradiol. 35(3):150-6, 2008
Akiyama K et al: A case of split cord malformation associated with myeloschisis. Childs Nerv Syst. 23(5):577-80, 2007
Ansari S et al: Split cord malformation associated with myelomeningocele. J Neurosurg. 107(4 Suppl):281-5, 2007
Jankowitz BT et al: Cutaneous manifestations of split cord malformations. Report of three cases. J Neurosurg. 107(3 Suppl):240-3, 2007
Kumar R et al: Unusual split cord with neurenteric cyst and cerebellar heterotopia over spinal cord. Childs Nerv Syst. 23(2):243-7, 2007
Gupta DK et al: Proposal for a new clinicoradiological classification of type I split-cord malformations: a prospective study of 25 cases. Pediatr Neurosurg. 42(6):341-6, 2006
Moriya J et al: An unusual case of split cord malformation. AJNR Am J Neuroradiol. 27(7):1562-4, 2006
Balci S et al: Cervical diastematomyelia in cervico-oculo-acoustic (Wildervanck) syndrome: MRI findings. Clin Dysmorphol. 11(2):125-8, 2002
Proctor MR et al: Long-term outcome for patients with split cord malformation. Neurosurg Focus. 10(1):e5, 2001
Tortori-Donati P et al: Magnetic resonance imaging of spinal dysraphism. Top Magn Reson Imaging. 12(6):375-409, 2001
Balci S et al: Diastematomyelia in two sisters. Am J Med Genet. 86(2):180-2, 1999
Ersahin Y et al: Split spinal cord malformations in children. J Neurosurg. 88(1):57-65, 1998
Frymoyer et al: The Adult Spine. Vol 2. 2nd ed. Philadelphia: Lippincott-Raven. 1923-26, 1997
Miller A et al: Evaluation and treatment of diastematomyelia. J Bone Joint Surg Am. 75(9):1308-17, 1993
Kaffenberger DA et al: Meningocele manque: radiologic findings with clinical correlation. AJNR Am J Neuroradiol. 13(4):1083-8, 1992
Pang D et al: Split cord malformation: Part I: a unified theory of embryogenesis for double spinal cord malformations. Neurosurgery. 31(3):451-80, 1992
Pang D: Split cord malformation: part II: clinical syndrome. Neurosurgery. 31(3):481-500, 1992
Naidich TP et al: Diastematomyelia: hemicord and meningeal sheaths; single and double arachnoid and dural tubes. AJNR Am J Neuroradiol. 4(3):633-6, 1983
Harwood-Nash DC et al: Diastematomyelia in 172 children: the impact of modern neuroradiology. Pediatr Neurosurg. 16(4-5):247-51, 1990-91
Russell NA et al: Diastematomyelia in adults. A review. Pediatr Neurosurg. 16(4-5):252-7, 1990-91
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Split cord malformation (SCM), "diastem"
Definitions
Sagittal division of spinal cord into 2 hemicords, each with 1 central canal, dorsal horn, and ventral horn
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nonvascular Interventions
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Morioka T et al: Neurosurgical pathology of limited dorsal myeloschisis. Childs Nerv Syst. 34(2):293-303, 2018
Lee SM et al: Limited dorsal myeloschisis and congenital dermal sinus: comparison of clinical and MR imaging features. AJNR Am J Neuroradiol. 38(1):176-82, 2017
Schmidt C et al: Meningocele manqué: a comprehensive review of this enigmatic finding in occult spinal dysraphism. Childs Nerv Syst. 33(7):1065-71, 2017
McComb JG: A practical clinical classification of spinal neural tube defects. Childs Nerv Syst. 31(10):1641-57, 2015
Alzhrani GA et al: Multi-level split cord malformation: do we need a new classification? J Clin Imaging Sci. 4:32, 2014
Burnei G et al: L3-L5 Teratological spondylolysis with diastematomyelia and L4 radicular syndrome followed by spondyloschisis without myelomeningocele due to somato-arcuate shifting. Spine J. 5(1):202-4, 2014
Muroi A et al: Split medulla in association with multiple closed neural tube defects. Childs Nerv Syst. 26(7):967-71, 2010
Ayvaz M et al: Is it necessary to operate all split cord malformations before corrective surgery for patients with congenital spinal deformities? Spine (Phila Pa 1976). 34(22):2413-8, 2009
Liu W et al: Characteristics of osseous septum of split cord malformation in patients presenting with scoliosis: a retrospective study of 48 cases. Pediatr Neurosurg. 2009;45(5):350-3. Epub 2009 Nov 11. Erratum in: Pediatr Neurosurg. 45(5):406, 2009
Rowley VB et al: Lumbar split cord malformation with lateral hemimyelomeningocele and associated Chiari II malformation and other visceral and osseous anomalies: a case report. J Comput Assist Tomogr. 33(6):923-6, 2009
Ozturk E et al: Split-cord malformation and accompanying anomalies. J Neuroradiol. 35(3):150-6, 2008
Akiyama K et al: A case of split cord malformation associated with myeloschisis. Childs Nerv Syst. 23(5):577-80, 2007
Ansari S et al: Split cord malformation associated with myelomeningocele. J Neurosurg. 107(4 Suppl):281-5, 2007
Jankowitz BT et al: Cutaneous manifestations of split cord malformations. Report of three cases. J Neurosurg. 107(3 Suppl):240-3, 2007
Kumar R et al: Unusual split cord with neurenteric cyst and cerebellar heterotopia over spinal cord. Childs Nerv Syst. 23(2):243-7, 2007
Gupta DK et al: Proposal for a new clinicoradiological classification of type I split-cord malformations: a prospective study of 25 cases. Pediatr Neurosurg. 42(6):341-6, 2006
Moriya J et al: An unusual case of split cord malformation. AJNR Am J Neuroradiol. 27(7):1562-4, 2006
Balci S et al: Cervical diastematomyelia in cervico-oculo-acoustic (Wildervanck) syndrome: MRI findings. Clin Dysmorphol. 11(2):125-8, 2002
Proctor MR et al: Long-term outcome for patients with split cord malformation. Neurosurg Focus. 10(1):e5, 2001
Tortori-Donati P et al: Magnetic resonance imaging of spinal dysraphism. Top Magn Reson Imaging. 12(6):375-409, 2001
Balci S et al: Diastematomyelia in two sisters. Am J Med Genet. 86(2):180-2, 1999
Ersahin Y et al: Split spinal cord malformations in children. J Neurosurg. 88(1):57-65, 1998
Frymoyer et al: The Adult Spine. Vol 2. 2nd ed. Philadelphia: Lippincott-Raven. 1923-26, 1997
Miller A et al: Evaluation and treatment of diastematomyelia. J Bone Joint Surg Am. 75(9):1308-17, 1993
Kaffenberger DA et al: Meningocele manque: radiologic findings with clinical correlation. AJNR Am J Neuroradiol. 13(4):1083-8, 1992
Pang D et al: Split cord malformation: Part I: a unified theory of embryogenesis for double spinal cord malformations. Neurosurgery. 31(3):451-80, 1992
Pang D: Split cord malformation: part II: clinical syndrome. Neurosurgery. 31(3):481-500, 1992
Naidich TP et al: Diastematomyelia: hemicord and meningeal sheaths; single and double arachnoid and dural tubes. AJNR Am J Neuroradiol. 4(3):633-6, 1983
Harwood-Nash DC et al: Diastematomyelia in 172 children: the impact of modern neuroradiology. Pediatr Neurosurg. 16(4-5):247-51, 1990-91
Russell NA et al: Diastematomyelia in adults. A review. Pediatr Neurosurg. 16(4-5):252-7, 1990-91
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