Rare syndrome of unknown etiology characterized by cellular bronchiolitis and chronic sinusitis
Diffuse: Bilateral lung involvement
Panbronchiolitis: Involves all layers of respiratory bronchiole wall
Characterized by accumulation of foamy macrophages in respiratory bronchiolar walls and alveolar ducts
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Sugimoto S et al: Lung transplantation for diffuse panbronchiolitis: 5 cases from a single centre. Interact Cardiovasc Thorac Surg. 22(5):679-81, 2016
Tsuji T et al: Nontuberculous mycobacteria in diffuse panbronchiolitis. Respirology. 20(1):80-6, 2015
Kudoh S et al: Diffuse panbronchiolitis. Clin Chest Med. 33(2):297-305, 2012
Anthony M et al: Diffuse panbronchiolitis: not just an Asian disease: Australian case series and review of the literature. Biomed Imaging Interv J. 5(4):e19, 2009
Poletti V et al: Diffuse panbronchiolitis. Eur Respir J. 28(4):862-71, 2006
Park MH et al: Association of HLA class I antigens with diffuse panbronchiolitis in Korean patients. Am J Respir Crit Care Med. 159(2):526-9, 1999
Fitzgerald JE et al: Diffuse panbronchiolitis in the United States. Am J Respir Crit Care Med. 154(2 Pt 1):497-503, 1996
Akira M et al: Diffuse panbronchiolitis: follow-up CT examination. Radiology. 189(2):559-62, 1993
Nishimura K et al: Diffuse panbronchiolitis: correlation of high-resolution CT and pathologic findings. Radiology. 184(3):779-85, 1992
Sugiyama Y et al: Analysis of HLA antigens in patients with diffuse panbronchiolitis. Am Rev Respir Dis. 141(6):1459-62, 1990
Akira M et al: Diffuse panbronchiolitis: evaluation with high-resolution CT. Radiology. 168(2):433-8, 1988
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Diffuse panbronchiolitis (DPB)
Definitions
Rare syndrome of unknown etiology characterized by cellular bronchiolitis and chronic sinusitis
Diffuse: Bilateral lung involvement
Panbronchiolitis: Involves all layers of respiratory bronchiole wall
Characterized by accumulation of foamy macrophages in respiratory bronchiolar walls and alveolar ducts
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Sugimoto S et al: Lung transplantation for diffuse panbronchiolitis: 5 cases from a single centre. Interact Cardiovasc Thorac Surg. 22(5):679-81, 2016
Tsuji T et al: Nontuberculous mycobacteria in diffuse panbronchiolitis. Respirology. 20(1):80-6, 2015
Kudoh S et al: Diffuse panbronchiolitis. Clin Chest Med. 33(2):297-305, 2012
Anthony M et al: Diffuse panbronchiolitis: not just an Asian disease: Australian case series and review of the literature. Biomed Imaging Interv J. 5(4):e19, 2009
Poletti V et al: Diffuse panbronchiolitis. Eur Respir J. 28(4):862-71, 2006
Park MH et al: Association of HLA class I antigens with diffuse panbronchiolitis in Korean patients. Am J Respir Crit Care Med. 159(2):526-9, 1999
Fitzgerald JE et al: Diffuse panbronchiolitis in the United States. Am J Respir Crit Care Med. 154(2 Pt 1):497-503, 1996
Akira M et al: Diffuse panbronchiolitis: follow-up CT examination. Radiology. 189(2):559-62, 1993
Nishimura K et al: Diffuse panbronchiolitis: correlation of high-resolution CT and pathologic findings. Radiology. 184(3):779-85, 1992
Sugiyama Y et al: Analysis of HLA antigens in patients with diffuse panbronchiolitis. Am Rev Respir Dis. 141(6):1459-62, 1990
Akira M et al: Diffuse panbronchiolitis: evaluation with high-resolution CT. Radiology. 168(2):433-8, 1988
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