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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Diffuse pulmonary lymphangiomatosis (DPL)
Synonyms
- Diffuse pulmonary angiomatosis; uncertain nature of vascular abnormalities
Definitions
- Congenital disorder: Increased number and complexity of anastomosing lymphatic channels
- Lymphatics in interlobular septa, pleura, peribronchovascular regions
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Biscotto I et al: Diffuse pulmonary lymphangiomatosis. J Bras Pneumol. 45(5):e20180412, 2019
- Ernotte C et al: Diffuse pulmonary lymphangiomatosis. J Belg Soc Radiol. 102(1):64, 2018
- Sun X et al: Diffuse Pulmonary lymphangiomatosis: MDCT findings after direct lymphangiography. AJR Am J Roentgenol. 208(2):300-5, 2017
- Ozeki M et al: Propranolol for intractable diffuse lymphangiomatosis. N Engl J Med. 364(14):1380-2, 2011
- Shah V et al: Mediastinal involvement in lymphangiomatosis: a previously unreported MRI sign. Pediatr Radiol. 41(8):985-92, 2011
- Raman SP et al: Imaging of thoracic lymphatic diseases. AJR Am J Roentgenol. 193(6):1504-13, 2009
- El Hajj L et al: Diagnostic value of bronchoscopy, CT and transbronchial biopsies in diffuse pulmonary lymphangiomatosis: case report and review of the literature. Clin Radiol. 60(8):921-5, 2005
- Yekeler E et al: Diffuse pulmonary lymphangiomatosis: imaging findings. Diagn Interv Radiol. 11(1):31-4, 2005
- Swensen SJ et al: Diffuse pulmonary lymphangiomatosis: CT findings. J Comput Assist Tomogr. 19(3):348-52, 1995
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Diffuse pulmonary lymphangiomatosis (DPL)
Synonyms
- Diffuse pulmonary angiomatosis; uncertain nature of vascular abnormalities
Definitions
- Congenital disorder: Increased number and complexity of anastomosing lymphatic channels
- Lymphatics in interlobular septa, pleura, peribronchovascular regions
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Biscotto I et al: Diffuse pulmonary lymphangiomatosis. J Bras Pneumol. 45(5):e20180412, 2019
- Ernotte C et al: Diffuse pulmonary lymphangiomatosis. J Belg Soc Radiol. 102(1):64, 2018
- Sun X et al: Diffuse Pulmonary lymphangiomatosis: MDCT findings after direct lymphangiography. AJR Am J Roentgenol. 208(2):300-5, 2017
- Ozeki M et al: Propranolol for intractable diffuse lymphangiomatosis. N Engl J Med. 364(14):1380-2, 2011
- Shah V et al: Mediastinal involvement in lymphangiomatosis: a previously unreported MRI sign. Pediatr Radiol. 41(8):985-92, 2011
- Raman SP et al: Imaging of thoracic lymphatic diseases. AJR Am J Roentgenol. 193(6):1504-13, 2009
- El Hajj L et al: Diagnostic value of bronchoscopy, CT and transbronchial biopsies in diffuse pulmonary lymphangiomatosis: case report and review of the literature. Clin Radiol. 60(8):921-5, 2005
- Yekeler E et al: Diffuse pulmonary lymphangiomatosis: imaging findings. Diagn Interv Radiol. 11(1):31-4, 2005
- Swensen SJ et al: Diffuse pulmonary lymphangiomatosis: CT findings. J Comput Assist Tomogr. 19(3):348-52, 1995
