Diffuse pulmonary angiomatosis; uncertain nature of vascular abnormalities
Definitions
Congenital disorder: Increased number and complexity of anastomosing lymphatic channels
Lymphatics in interlobular septa, pleura, peribronchovascular regions
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Biscotto I et al: Diffuse pulmonary lymphangiomatosis. J Bras Pneumol. 45(5):e20180412, 2019
Ernotte C et al: Diffuse pulmonary lymphangiomatosis. J Belg Soc Radiol. 102(1):64, 2018
Sun X et al: Diffuse Pulmonary lymphangiomatosis: MDCT findings after direct lymphangiography. AJR Am J Roentgenol. 208(2):300-5, 2017
Ozeki M et al: Propranolol for intractable diffuse lymphangiomatosis. N Engl J Med. 364(14):1380-2, 2011
Shah V et al: Mediastinal involvement in lymphangiomatosis: a previously unreported MRI sign. Pediatr Radiol. 41(8):985-92, 2011
Raman SP et al: Imaging of thoracic lymphatic diseases. AJR Am J Roentgenol. 193(6):1504-13, 2009
El Hajj L et al: Diagnostic value of bronchoscopy, CT and transbronchial biopsies in diffuse pulmonary lymphangiomatosis: case report and review of the literature. Clin Radiol. 60(8):921-5, 2005
Yekeler E et al: Diffuse pulmonary lymphangiomatosis: imaging findings. Diagn Interv Radiol. 11(1):31-4, 2005
Diffuse pulmonary angiomatosis; uncertain nature of vascular abnormalities
Definitions
Congenital disorder: Increased number and complexity of anastomosing lymphatic channels
Lymphatics in interlobular septa, pleura, peribronchovascular regions
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Biscotto I et al: Diffuse pulmonary lymphangiomatosis. J Bras Pneumol. 45(5):e20180412, 2019
Ernotte C et al: Diffuse pulmonary lymphangiomatosis. J Belg Soc Radiol. 102(1):64, 2018
Sun X et al: Diffuse Pulmonary lymphangiomatosis: MDCT findings after direct lymphangiography. AJR Am J Roentgenol. 208(2):300-5, 2017
Ozeki M et al: Propranolol for intractable diffuse lymphangiomatosis. N Engl J Med. 364(14):1380-2, 2011
Shah V et al: Mediastinal involvement in lymphangiomatosis: a previously unreported MRI sign. Pediatr Radiol. 41(8):985-92, 2011
Raman SP et al: Imaging of thoracic lymphatic diseases. AJR Am J Roentgenol. 193(6):1504-13, 2009
El Hajj L et al: Diagnostic value of bronchoscopy, CT and transbronchial biopsies in diffuse pulmonary lymphangiomatosis: case report and review of the literature. Clin Radiol. 60(8):921-5, 2005
Yekeler E et al: Diffuse pulmonary lymphangiomatosis: imaging findings. Diagn Interv Radiol. 11(1):31-4, 2005