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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Definitions
- Congenital aortic arch anomaly
- Persistent right and left 4th embryonic aortic arches
- Complete vascular ring encircles trachea and esophagus
- Most common symptomatic vascular ring (55%)
- May occur with or without other congenital abnormalities
- Often isolated anomaly in adults
- Congenital aortic arch anomaly
IMAGING
General Features
Radiographic Findings
Fluoroscopic Findings
CT Findings
MR Findings
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Young AA et al: Prenatal detection, comorbidities, and management of vascular rings. Am J Cardiol. 123(10):1703-8, 2019
- Priya S et al: Congenital anomalies of the aortic arch. Cardiovasc Diagn Ther. 8(Suppl 1):S26-44, 2018
- Hanneman K et al: Congenital variants and anomalies of the aortic arch. Radiographics. 37(1):32-51, 2017
- Backer CL et al: Vascular rings. Semin Pediatr Surg. 25(3):165-75, 2016
- Smith BM et al: Rings and slings revisited. Magn Reson Imaging Clin N Am. 23(1):127-35, 2015
- Etesami M et al: Computed tomography in the evaluation of vascular rings and slings. Insights Imaging. 5(4):507-21, 2014
- Murillo H et al: Imaging of the aorta: embryology and anatomy. Semin Ultrasound CT MR. 33(3):169-90, 2012
- Restrepo CS et al: Multidetector computed tomography of congenital anomalies of the thoracic aorta. Semin Ultrasound CT MR. 33(3):191-206, 2012
- Cerillo AG et al: Sixteen-row multislice computed tomography in infants with double aortic arch. Int J Cardiol. 99(2):191-4, 2005
- Chan MS et al: Angiography and dynamic airway evaluation with MDCT in the diagnosis of double aortic arch associated with tracheomalacia. AJR Am J Roentgenol. 185(5):1248-51, 2005
- Greil GF et al: Diagnosis of vascular rings and slings using an interleaved 3D double-slab FISP MR angiography technique. Pediatr Radiol. 2005
- Subramanyan R et al: Vascular rings: an important cause of persistent respiratory symptoms in infants and children. Indian Pediatr. 40(10):951-7, 2003
- Yilmaz M et al: Vascular anomalies causing tracheoesophageal compression: a 20-year experience in diagnosis and management. Heart Surg Forum. 6(3):149-52, 2003
- Fleck RJ et al: Imaging findings in pediatric patients with persistent airway symptoms after surgery for double aortic arch. AJR Am J Roentgenol. 178(5):1275-9, 2002
- Skinner LJ et al: Complete vascular ring detected by barium esophagography. Ear Nose Throat J. 81(8):554-5, 2002
- McElhinney DB et al: Association of chromosome 22q11 deletion with isolated anomalies of aortic arch laterality and branching. J Am Coll Cardiol. 37(8):2114-9, 2001
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Definitions
- Congenital aortic arch anomaly
- Persistent right and left 4th embryonic aortic arches
- Complete vascular ring encircles trachea and esophagus
- Most common symptomatic vascular ring (55%)
- May occur with or without other congenital abnormalities
- Often isolated anomaly in adults
- Congenital aortic arch anomaly
IMAGING
General Features
Radiographic Findings
Fluoroscopic Findings
CT Findings
MR Findings
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Young AA et al: Prenatal detection, comorbidities, and management of vascular rings. Am J Cardiol. 123(10):1703-8, 2019
- Priya S et al: Congenital anomalies of the aortic arch. Cardiovasc Diagn Ther. 8(Suppl 1):S26-44, 2018
- Hanneman K et al: Congenital variants and anomalies of the aortic arch. Radiographics. 37(1):32-51, 2017
- Backer CL et al: Vascular rings. Semin Pediatr Surg. 25(3):165-75, 2016
- Smith BM et al: Rings and slings revisited. Magn Reson Imaging Clin N Am. 23(1):127-35, 2015
- Etesami M et al: Computed tomography in the evaluation of vascular rings and slings. Insights Imaging. 5(4):507-21, 2014
- Murillo H et al: Imaging of the aorta: embryology and anatomy. Semin Ultrasound CT MR. 33(3):169-90, 2012
- Restrepo CS et al: Multidetector computed tomography of congenital anomalies of the thoracic aorta. Semin Ultrasound CT MR. 33(3):191-206, 2012
- Cerillo AG et al: Sixteen-row multislice computed tomography in infants with double aortic arch. Int J Cardiol. 99(2):191-4, 2005
- Chan MS et al: Angiography and dynamic airway evaluation with MDCT in the diagnosis of double aortic arch associated with tracheomalacia. AJR Am J Roentgenol. 185(5):1248-51, 2005
- Greil GF et al: Diagnosis of vascular rings and slings using an interleaved 3D double-slab FISP MR angiography technique. Pediatr Radiol. 2005
- Subramanyan R et al: Vascular rings: an important cause of persistent respiratory symptoms in infants and children. Indian Pediatr. 40(10):951-7, 2003
- Yilmaz M et al: Vascular anomalies causing tracheoesophageal compression: a 20-year experience in diagnosis and management. Heart Surg Forum. 6(3):149-52, 2003
- Fleck RJ et al: Imaging findings in pediatric patients with persistent airway symptoms after surgery for double aortic arch. AJR Am J Roentgenol. 178(5):1275-9, 2002
- Skinner LJ et al: Complete vascular ring detected by barium esophagography. Ear Nose Throat J. 81(8):554-5, 2002
- McElhinney DB et al: Association of chromosome 22q11 deletion with isolated anomalies of aortic arch laterality and branching. J Am Coll Cardiol. 37(8):2114-9, 2001
