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KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Double outlet right ventricle (DORV)
Definitions
Form of abnormal ventriculoarterial connection in which both great arteries arise completely or predominately from morphologic right ventricle
16 variants based on relationship of great arteries & position/location of ventricular septal defect (VSD)
Fibrinous discontinuity between mitral & semilunar valves or bilateral conus
May be part of complex lesions coexisting with ventricular anomalies, valve stenosis or atresia, abnormal atrioventricular valve, aortic valve anomalies, coarctation, coronary anomalies, & anomalies of systemic & pulmonary venous return
Taussig-Bing anomaly with DORV is subpulmonary VSD where left ventricular outflow is directed toward pulmonary artery with preferential flow
IMAGING
General Features
Radiographic Findings
CTA or MRA
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Treatment
Selected References
Farooqi KM et al: Use of 3-dimensional printing to demonstrate complex intracardiac relationships in double-outlet right ventricle for surgical planning. Circ Cardiovasc Imaging. 8(5), 2015
Singla M et al: Double-outlet right ventricle without interventricular communication: an unusual and challenging problem. Pediatr Cardiol. 34(8):1941-4, 2013
Kha LC et al: Multimodality cardiac imaging of a double chambered right ventricle with intrapulmonary shunting: a case report. BMC Res Notes. 5:516, 2012
Mershina EA et al: [Radial diagnosis MRT and MSCT in assessing the outcomes of surgical correction for complicated congenital heart defects: discordant atrioventricular connections with double outlet right ventricle.] Angiol Sosud Khir. 18(1):39-44, 2012
Frank L et al: Cardiovascular MR imaging of conotruncal anomalies. Radiographics. 30(4):1069-94, 2010
Saleeb SF et al: Anatomic, imaging, and clinical characteristics of double-inlet, double-outlet right ventricle. Am J Cardiol. 105(4):542-9, 2010
Uehara M et al: Double outlet right ventricle demonstrated by multislice computed tomography. Int J Cardiol. 121(2):218-20, 2007
Brown JW et al: Surgical results in patients with double outlet right ventricle: a 20-year experience. Ann Thorac Surg. 72(5):1630-5, 2001
Hagler DJ. Double-outlet right ventricle. In Allen HD et al: Heart Disease in Infants, Children, and Adolescents. Philadelphia: Lippincott Williams & Wilkins. 1102-28, 2001
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Double outlet right ventricle (DORV)
Definitions
Form of abnormal ventriculoarterial connection in which both great arteries arise completely or predominately from morphologic right ventricle
16 variants based on relationship of great arteries & position/location of ventricular septal defect (VSD)
Fibrinous discontinuity between mitral & semilunar valves or bilateral conus
May be part of complex lesions coexisting with ventricular anomalies, valve stenosis or atresia, abnormal atrioventricular valve, aortic valve anomalies, coarctation, coronary anomalies, & anomalies of systemic & pulmonary venous return
Taussig-Bing anomaly with DORV is subpulmonary VSD where left ventricular outflow is directed toward pulmonary artery with preferential flow
IMAGING
General Features
Radiographic Findings
CTA or MRA
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Treatment
Selected References
Farooqi KM et al: Use of 3-dimensional printing to demonstrate complex intracardiac relationships in double-outlet right ventricle for surgical planning. Circ Cardiovasc Imaging. 8(5), 2015
Singla M et al: Double-outlet right ventricle without interventricular communication: an unusual and challenging problem. Pediatr Cardiol. 34(8):1941-4, 2013
Kha LC et al: Multimodality cardiac imaging of a double chambered right ventricle with intrapulmonary shunting: a case report. BMC Res Notes. 5:516, 2012
Mershina EA et al: [Radial diagnosis MRT and MSCT in assessing the outcomes of surgical correction for complicated congenital heart defects: discordant atrioventricular connections with double outlet right ventricle.] Angiol Sosud Khir. 18(1):39-44, 2012
Frank L et al: Cardiovascular MR imaging of conotruncal anomalies. Radiographics. 30(4):1069-94, 2010
Saleeb SF et al: Anatomic, imaging, and clinical characteristics of double-inlet, double-outlet right ventricle. Am J Cardiol. 105(4):542-9, 2010
Uehara M et al: Double outlet right ventricle demonstrated by multislice computed tomography. Int J Cardiol. 121(2):218-20, 2007
Brown JW et al: Surgical results in patients with double outlet right ventricle: a 20-year experience. Ann Thorac Surg. 72(5):1630-5, 2001
Hagler DJ. Double-outlet right ventricle. In Allen HD et al: Heart Disease in Infants, Children, and Adolescents. Philadelphia: Lippincott Williams & Wilkins. 1102-28, 2001
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