Most common neonatal upper intestinal obstruction (40-50%)
IMAGING
General Features
Radiographic Findings
Fluoroscopic Findings
Ultrasonographic Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Nguyen HN et al: Untwisting the complexity of midgut malrotation and volvulus ultrasound. Pediatr Radiol. 51(4):658-68, 2021
Tsitsiou Y et al: Diagnostic decision-making tool for imaging term neonatal bowel obstruction. Clin Radiol. 76(3):163-71, 2021
Bishop JC et al: The double bubble sign: duodenal atresia and associated genetic etiologies. Fetal Diagn Ther. 47(2):98-103, 2020
Hameed S et al: The role of sonography in differentiating congenital intrinsic duodenal anomalies from midgut malrotation: emphasizing the new signs of duodenal and gastric wall thickening and hyperechogenicity. Pediatr Radiol. 50(5):673-83, 2020
Chandrasekaran N et al: Prenatal sonographic diagnosis of meconium peritonitis from duodenal atresia. BMJ Case Rep. 2017, 2017
Angotti R et al: Association of duodenal atresia, malrotation, and atrial septal defect in a Down-syndrome patient. APSP J Case Rep. 7(2):16, 2016
Rattan KN et al: Neonatal duodenal obstruction: a 15-year experience. J Neonatal Surg. 5(2):13, 2016
Chandrasekharam V: Laparoscopic duodenoduodenostomy in neonates: report of two cases and review of the literature. J Indian Assoc Pediatr Surg. 20(3):150-2, 2015
Fragoso AC et al: Defective upper gastrointestinal function after repair of combined esophageal and duodenal atresia. J Pediatr Surg. 50(4):531-4, 2015
Virgone C et al: Accuracy of prenatal ultrasound in detecting jejunal and ileal atresia: systematic review and meta-analysis. Ultrasound Obstet Gynecol. 45(5):523-9, 2015
Adewole VA et al: Antenatally detected cystic biliary atresia: differential diagnoses of a double bubble. Springerplus. 3:368, 2014
Latzman JM et al: Duodenal atresia: not always a double bubble. Pediatr Radiol. 44(8):1031-4, 2014
Maxfield CM et al: A pattern-based approach to bowel obstruction in the newborn. Pediatr Radiol. 43(3):318-29, 2013
Mirza B et al: Multiple associated anomalies in patients of duodenal atresia: a case series. J Neonatal Surg. 1(2):23, 2012
Akcora B et al: A newborn with duodenal atresia and a gastric perforation. Afr J Paediatr Surg. 7(1):33-5, 2010
Choudhry MS et al: Duodenal atresia: associated anomalies, prenatal diagnosis and outcome. Pediatr Surg Int. 25(8):727-30, 2009
Gilbertson-Dahdal DL et al: Neonatal malrotation with midgut volvulus mimicking duodenal atresia. AJR Am J Roentgenol. 192(5):1269-71, 2009
Iwai A et al: Choledochal cyst associated with duodenal atresia: case report and review of the literature. Pediatr Surg Int. 25(11):995-8, 2009
Keckler SJ et al: The influence of trisomy 21 on the incidence and severity of congenital heart defects in patients with duodenal atresia. Pediatr Surg Int. 24(8):921-3, 2008
Mustafawi AR et al: Congenital duodenal obstruction in children: a decade's experience. Eur J Pediatr Surg. 18(2):93-7, 2008
Escobar MA et al: Duodenal atresia and stenosis: long-term follow-up over 30 years. J Pediatr Surg. 39(6):867-71; discussion 867-71, 2004
Forrester MB et al: Population-based study of small intestinal atresia and stenosis, Hawaii, 1986-2000. Public Health. 118(6):434-8, 2004
Sugimoto T et al: Choledochal cyst and duodenal atresia: a rare combination of malformations. Pediatr Surg Int. 20(9):724-6, 2004
Doray B et al: Esophageal and duodenal atresia in a girl with a 12q24.3-qter deletion. Clin Genet. 61(6):468-71, 2002
Haeusler MC et al: Prenatal ultrasonographic detection of gastrointestinal obstruction: results from 18 European congenital anomaly registries. Prenat Diagn. 22(7):616-23, 2002
Mordehai J et al: Preduodenal portal vein causing duodenal obstruction associated with situs inversus, intestinal malrotation, and polysplenia: a case report. J Pediatr Surg. 37(4):E5, 2002
Pumberger W et al: Duodeno-jejunal atresia with volvulus, absent dorsal mesentery, and absent superior mesenteric artery: a hereditary compound structure in duodenal atresia? Am J Med Genet. 109(1):52-5, 2002
Rothenberg SS: Laparoscopic duodenoduodenostomy for duodenal obstruction in infants and children. J Pediatr Surg. 37(7):1088-9, 2002
Sencan A et al: Symptomatic annular pancreas in newborns. Med Sci Monit. 8(6):CR434-7, 2002
Maruyama K et al: Partial monosomy 10q with partial trisomy 11q due to paternal balanced translocation. J Paediatr Child Health. 37(2):198-200, 2001
Dalla Vecchia LK et al: Intestinal atresia and stenosis: a 25-year experience with 277 cases. Arch Surg. 133(5):490-6; discussion 496-7, 1998
Courtens W et al: Feingold syndrome: report of a new family and review. Am J Med Genet. 73(1):55-60, 1997
Lemire EG et al: A familial disorder with duodenal atresia and tetralogy of Fallot. Am J Med Genet. 66(1):39-44, 1996
Long FR et al: Intestinal malrotation in children: tutorial on radiographic diagnosis in difficult cases. Radiology. 198(3):775-80, 1996
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Duodenal atresia (DA), duodenal stenosis (DS)
Definitions
Atresia: Congenital occlusion of intestinal lumen
Stenosis: Fixed narrowing of intestinal lumen
Most common neonatal upper intestinal obstruction (40-50%)
IMAGING
General Features
Radiographic Findings
Fluoroscopic Findings
Ultrasonographic Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Nguyen HN et al: Untwisting the complexity of midgut malrotation and volvulus ultrasound. Pediatr Radiol. 51(4):658-68, 2021
Tsitsiou Y et al: Diagnostic decision-making tool for imaging term neonatal bowel obstruction. Clin Radiol. 76(3):163-71, 2021
Bishop JC et al: The double bubble sign: duodenal atresia and associated genetic etiologies. Fetal Diagn Ther. 47(2):98-103, 2020
Hameed S et al: The role of sonography in differentiating congenital intrinsic duodenal anomalies from midgut malrotation: emphasizing the new signs of duodenal and gastric wall thickening and hyperechogenicity. Pediatr Radiol. 50(5):673-83, 2020
Chandrasekaran N et al: Prenatal sonographic diagnosis of meconium peritonitis from duodenal atresia. BMJ Case Rep. 2017, 2017
Angotti R et al: Association of duodenal atresia, malrotation, and atrial septal defect in a Down-syndrome patient. APSP J Case Rep. 7(2):16, 2016
Rattan KN et al: Neonatal duodenal obstruction: a 15-year experience. J Neonatal Surg. 5(2):13, 2016
Chandrasekharam V: Laparoscopic duodenoduodenostomy in neonates: report of two cases and review of the literature. J Indian Assoc Pediatr Surg. 20(3):150-2, 2015
Fragoso AC et al: Defective upper gastrointestinal function after repair of combined esophageal and duodenal atresia. J Pediatr Surg. 50(4):531-4, 2015
Virgone C et al: Accuracy of prenatal ultrasound in detecting jejunal and ileal atresia: systematic review and meta-analysis. Ultrasound Obstet Gynecol. 45(5):523-9, 2015
Adewole VA et al: Antenatally detected cystic biliary atresia: differential diagnoses of a double bubble. Springerplus. 3:368, 2014
Latzman JM et al: Duodenal atresia: not always a double bubble. Pediatr Radiol. 44(8):1031-4, 2014
Maxfield CM et al: A pattern-based approach to bowel obstruction in the newborn. Pediatr Radiol. 43(3):318-29, 2013
Mirza B et al: Multiple associated anomalies in patients of duodenal atresia: a case series. J Neonatal Surg. 1(2):23, 2012
Akcora B et al: A newborn with duodenal atresia and a gastric perforation. Afr J Paediatr Surg. 7(1):33-5, 2010
Choudhry MS et al: Duodenal atresia: associated anomalies, prenatal diagnosis and outcome. Pediatr Surg Int. 25(8):727-30, 2009
Gilbertson-Dahdal DL et al: Neonatal malrotation with midgut volvulus mimicking duodenal atresia. AJR Am J Roentgenol. 192(5):1269-71, 2009
Iwai A et al: Choledochal cyst associated with duodenal atresia: case report and review of the literature. Pediatr Surg Int. 25(11):995-8, 2009
Keckler SJ et al: The influence of trisomy 21 on the incidence and severity of congenital heart defects in patients with duodenal atresia. Pediatr Surg Int. 24(8):921-3, 2008
Mustafawi AR et al: Congenital duodenal obstruction in children: a decade's experience. Eur J Pediatr Surg. 18(2):93-7, 2008
Escobar MA et al: Duodenal atresia and stenosis: long-term follow-up over 30 years. J Pediatr Surg. 39(6):867-71; discussion 867-71, 2004
Forrester MB et al: Population-based study of small intestinal atresia and stenosis, Hawaii, 1986-2000. Public Health. 118(6):434-8, 2004
Sugimoto T et al: Choledochal cyst and duodenal atresia: a rare combination of malformations. Pediatr Surg Int. 20(9):724-6, 2004
Doray B et al: Esophageal and duodenal atresia in a girl with a 12q24.3-qter deletion. Clin Genet. 61(6):468-71, 2002
Haeusler MC et al: Prenatal ultrasonographic detection of gastrointestinal obstruction: results from 18 European congenital anomaly registries. Prenat Diagn. 22(7):616-23, 2002
Mordehai J et al: Preduodenal portal vein causing duodenal obstruction associated with situs inversus, intestinal malrotation, and polysplenia: a case report. J Pediatr Surg. 37(4):E5, 2002
Pumberger W et al: Duodeno-jejunal atresia with volvulus, absent dorsal mesentery, and absent superior mesenteric artery: a hereditary compound structure in duodenal atresia? Am J Med Genet. 109(1):52-5, 2002
Rothenberg SS: Laparoscopic duodenoduodenostomy for duodenal obstruction in infants and children. J Pediatr Surg. 37(7):1088-9, 2002
Sencan A et al: Symptomatic annular pancreas in newborns. Med Sci Monit. 8(6):CR434-7, 2002
Maruyama K et al: Partial monosomy 10q with partial trisomy 11q due to paternal balanced translocation. J Paediatr Child Health. 37(2):198-200, 2001
Dalla Vecchia LK et al: Intestinal atresia and stenosis: a 25-year experience with 277 cases. Arch Surg. 133(5):490-6; discussion 496-7, 1998