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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Dural ectasia
Definitions
- Patulous dural sac with posterior vertebral scalloping
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Nonvascular Interventions
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Polster SP et al: Dural ectasia in neurofibromatosis 1: case series, management, and review. Neurosurgery. 86(5):646-55, 2020
- Böker T et al: Dural ectasia in Marfan syndrome and other hereditary connective tissue disorders: a 10-year follow-up study. Spine J. 19(8):1412-21, 2019
- Kohns DJ: Interventional spine considerations for dural ectasia in a patient with Marfan syndrome. Am J Phys Med Rehabil. 97(1):e6-8, 2018
- Razek AAKA: MR imaging of neoplastic and non-neoplastic lesions of the brain and spine in neurofibromatosis type I. Neurol Sci. 39(5):821-7, 2018
- Sheridan GA et al: Dural ectasia associated with Mounier-Kuhn syndrome: a novel association in the context of spinal stenosis. BMJ Case Rep. 2017, 2017
- Elgafy H et al: Sacral erosion and insufficiency fracture secondary to dural ectasia in patient with Marfan syndrome. Spine J. 16(5):e301-2, 2016
- Kow CY et al: Incidental dural ectasia associated with scoliosis. Spine J. 16(1):e25-6, 2016
- Jain VV et al: Dural ectasia in a child with larsen syndrome. J Pediatr Orthop. 34(7):e44-9, 2014
- Kono AK et al: Prevalence of dural ectasia in Loeys-Dietz syndrome: comparison with Marfan syndrome and normal controls. PLoS One. 8(9):e75264, 2013
- Mesfin A et al: Ten-year clinical and imaging follow-up of dural ectasia in adults with Marfan syndrome. Spine J. 13(1):62-7, 2013
- Sznajder M et al: Spinal imaging contributes to the diagnosis of Marfan syndrome. Joint Bone Spine. 77(5):445-50, 2010
- García-Estevez DA et al: [Dural ectasia in the cervical spine and neurofibromatosis type 1.] Rev Neurol. 48(1):51, 2009
- Sanz-Ayan MP et al: [Dural ectasia and lumbar pain associated with Marfan syndrome.] Rev Neurol. 47(10):559-60, 2008
- Kotil K et al: Lumbar radiculopathy in ankylosing spondylitis with dural ectasia. J Clin Neurosci. 14(10):981-3, 2007
- Knirsch W et al: Dural ectasia in children with Marfan syndrome: a prospective, multicenter, patient-control study. Am J Med Genet A. 140(7):775-81, 2006
- Reitman CA et al: Neurologic and morphologic features of dural ectasia in ankylosing spondylitis and rheumatoid arthritis: a case report. Am J Orthop (Belle Mead NJ). 35(11):530-1, 2006
- Habermann CR et al: MR evaluation of dural ectasia in Marfan syndrome: reassessment of the established criteria in children, adolescents, and young adults. Radiology. 234(2):535-41, 2005
- Knirsch W et al: Normal values of the sagittal diameter of the lumbar spine (vertebral body and dural sac) in children measured by MRI. Pediatr Radiol. 35(4):419-24, 2005
- Tsirikos AI et al: Assessment of vertebral scalloping in neurofibromatosis type 1 with plain radiography and MRI. Clin Radiol. 59(11):1009-17, 2004
- Nallamshetty L et al: Dural ectasia and back pain: review of the literature and case report. J Spinal Disord Tech. 15(4):326-9, 2002
- Tubbs RS et al: Dural ectasia in neurofibromatosis. Pediatr Neurosurg. 37(6):331-2, 2002
- Ahn NU et al: Dural ectasia and conventional radiography in the Marfan lumbosacral spine. Skeletal Radiol. 30(6):338-45, 2001
- Oosterhof T et al: Quantitative assessment of dural ectasia as a marker for Marfan syndrome. Radiology. 220(2):514-8, 2001
- Ahn NU et al: Dural ectasia in the Marfan syndrome: MR and CT findings and criteria. Genet Med. 2(3):173-9, 2000
- Ahn NU et al: Dural ectasia is associated with back pain in Marfan syndrome. Spine. 25(12):1562-8, 2000
- Rose PS et al: A comparison of the Berlin and Ghent nosologies and the influence of dural ectasia in the diagnosis of Marfan syndrome. Genet Med. 2(5):278-82, 2000
- Schonauer C et al: Lumbosacral dural ectasia in type 1 neurofibromatosis. Report of two cases. J Neurosurg Sci. 44(3):165-8; discussion 169, 2000
- Sponseller PD et al: Osseous anatomy of the lumbosacral spine in Marfan syndrome. Spine. 25(21):2797-802, 2000
- De Paepe A: Dural ectasia and the diagnosis of Marfan's syndrome. Lancet. 354(9182):878-9, 1999
- Fattori R et al: Importance of dural ectasia in phenotypic assessment of Marfan's syndrome. Lancet. 354(9182):910-3, 1999
- Villeirs GM et al: Widening of the spinal canal and dural ectasia in Marfan's syndrome: assessment by CT. Neuroradiology. 41(11):850-4, 1999
- Raff ML et al: Joint hypermobility syndromes. Curr Opin Rheumatol. 8(5):459-66, 1996
- Helfen M et al: Intrathoracic dural ectasia mimicking neurofibroma and scoliosis. A case report. Int Orthop. 19(3):181-4, 1995
- Bensaid AH et al: Neurofibromatosis with dural ectasia and bilateral symmetrical pedicular clefts: report of two cases. Neuroradiology. 34(2):107-9, 1992
- Pyeritz RE et al: Dural ectasia is a common feature of the Marfan syndrome. Am J Hum Genet. 43(5):726-32, 1988
- Stern WE: Dural ectasia and the Marfan syndrome. J Neurosurg. 69(2):221-7, 1988
- Katz SG et al: Thoracic and lumbar dural ectasia in a two-year-old boy. Pediatr Radiol. 6(4):238-40, 1978
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Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Dural ectasia
Definitions
- Patulous dural sac with posterior vertebral scalloping
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Nonvascular Interventions
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Polster SP et al: Dural ectasia in neurofibromatosis 1: case series, management, and review. Neurosurgery. 86(5):646-55, 2020
- Böker T et al: Dural ectasia in Marfan syndrome and other hereditary connective tissue disorders: a 10-year follow-up study. Spine J. 19(8):1412-21, 2019
- Kohns DJ: Interventional spine considerations for dural ectasia in a patient with Marfan syndrome. Am J Phys Med Rehabil. 97(1):e6-8, 2018
- Razek AAKA: MR imaging of neoplastic and non-neoplastic lesions of the brain and spine in neurofibromatosis type I. Neurol Sci. 39(5):821-7, 2018
- Sheridan GA et al: Dural ectasia associated with Mounier-Kuhn syndrome: a novel association in the context of spinal stenosis. BMJ Case Rep. 2017, 2017
- Elgafy H et al: Sacral erosion and insufficiency fracture secondary to dural ectasia in patient with Marfan syndrome. Spine J. 16(5):e301-2, 2016
- Kow CY et al: Incidental dural ectasia associated with scoliosis. Spine J. 16(1):e25-6, 2016
- Jain VV et al: Dural ectasia in a child with larsen syndrome. J Pediatr Orthop. 34(7):e44-9, 2014
- Kono AK et al: Prevalence of dural ectasia in Loeys-Dietz syndrome: comparison with Marfan syndrome and normal controls. PLoS One. 8(9):e75264, 2013
- Mesfin A et al: Ten-year clinical and imaging follow-up of dural ectasia in adults with Marfan syndrome. Spine J. 13(1):62-7, 2013
- Sznajder M et al: Spinal imaging contributes to the diagnosis of Marfan syndrome. Joint Bone Spine. 77(5):445-50, 2010
- García-Estevez DA et al: [Dural ectasia in the cervical spine and neurofibromatosis type 1.] Rev Neurol. 48(1):51, 2009
- Sanz-Ayan MP et al: [Dural ectasia and lumbar pain associated with Marfan syndrome.] Rev Neurol. 47(10):559-60, 2008
- Kotil K et al: Lumbar radiculopathy in ankylosing spondylitis with dural ectasia. J Clin Neurosci. 14(10):981-3, 2007
- Knirsch W et al: Dural ectasia in children with Marfan syndrome: a prospective, multicenter, patient-control study. Am J Med Genet A. 140(7):775-81, 2006
- Reitman CA et al: Neurologic and morphologic features of dural ectasia in ankylosing spondylitis and rheumatoid arthritis: a case report. Am J Orthop (Belle Mead NJ). 35(11):530-1, 2006
- Habermann CR et al: MR evaluation of dural ectasia in Marfan syndrome: reassessment of the established criteria in children, adolescents, and young adults. Radiology. 234(2):535-41, 2005
- Knirsch W et al: Normal values of the sagittal diameter of the lumbar spine (vertebral body and dural sac) in children measured by MRI. Pediatr Radiol. 35(4):419-24, 2005
- Tsirikos AI et al: Assessment of vertebral scalloping in neurofibromatosis type 1 with plain radiography and MRI. Clin Radiol. 59(11):1009-17, 2004
- Nallamshetty L et al: Dural ectasia and back pain: review of the literature and case report. J Spinal Disord Tech. 15(4):326-9, 2002
- Tubbs RS et al: Dural ectasia in neurofibromatosis. Pediatr Neurosurg. 37(6):331-2, 2002
- Ahn NU et al: Dural ectasia and conventional radiography in the Marfan lumbosacral spine. Skeletal Radiol. 30(6):338-45, 2001
- Oosterhof T et al: Quantitative assessment of dural ectasia as a marker for Marfan syndrome. Radiology. 220(2):514-8, 2001
- Ahn NU et al: Dural ectasia in the Marfan syndrome: MR and CT findings and criteria. Genet Med. 2(3):173-9, 2000
- Ahn NU et al: Dural ectasia is associated with back pain in Marfan syndrome. Spine. 25(12):1562-8, 2000
- Rose PS et al: A comparison of the Berlin and Ghent nosologies and the influence of dural ectasia in the diagnosis of Marfan syndrome. Genet Med. 2(5):278-82, 2000
- Schonauer C et al: Lumbosacral dural ectasia in type 1 neurofibromatosis. Report of two cases. J Neurosurg Sci. 44(3):165-8; discussion 169, 2000
- Sponseller PD et al: Osseous anatomy of the lumbosacral spine in Marfan syndrome. Spine. 25(21):2797-802, 2000
- De Paepe A: Dural ectasia and the diagnosis of Marfan's syndrome. Lancet. 354(9182):878-9, 1999
- Fattori R et al: Importance of dural ectasia in phenotypic assessment of Marfan's syndrome. Lancet. 354(9182):910-3, 1999
- Villeirs GM et al: Widening of the spinal canal and dural ectasia in Marfan's syndrome: assessment by CT. Neuroradiology. 41(11):850-4, 1999
- Raff ML et al: Joint hypermobility syndromes. Curr Opin Rheumatol. 8(5):459-66, 1996
- Helfen M et al: Intrathoracic dural ectasia mimicking neurofibroma and scoliosis. A case report. Int Orthop. 19(3):181-4, 1995
- Bensaid AH et al: Neurofibromatosis with dural ectasia and bilateral symmetrical pedicular clefts: report of two cases. Neuroradiology. 34(2):107-9, 1992
- Pyeritz RE et al: Dural ectasia is a common feature of the Marfan syndrome. Am J Hum Genet. 43(5):726-32, 1988
- Stern WE: Dural ectasia and the Marfan syndrome. J Neurosurg. 69(2):221-7, 1988
- Katz SG et al: Thoracic and lumbar dural ectasia in a two-year-old boy. Pediatr Radiol. 6(4):238-40, 1978
