Patulous dural sac with posterior vertebral scalloping
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Nonvascular Interventions
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Polster SP et al: Dural ectasia in neurofibromatosis 1: case series, management, and review. Neurosurgery. 86(5):646-55, 2020
Böker T et al: Dural ectasia in Marfan syndrome and other hereditary connective tissue disorders: a 10-year follow-up study. Spine J. 19(8):1412-21, 2019
Kohns DJ: Interventional spine considerations for dural ectasia in a patient with Marfan syndrome. Am J Phys Med Rehabil. 97(1):e6-8, 2018
Razek AAKA: MR imaging of neoplastic and non-neoplastic lesions of the brain and spine in neurofibromatosis type I. Neurol Sci. 39(5):821-7, 2018
Sheridan GA et al: Dural ectasia associated with Mounier-Kuhn syndrome: a novel association in the context of spinal stenosis. BMJ Case Rep. 2017, 2017
Elgafy H et al: Sacral erosion and insufficiency fracture secondary to dural ectasia in patient with Marfan syndrome. Spine J. 16(5):e301-2, 2016
Kow CY et al: Incidental dural ectasia associated with scoliosis. Spine J. 16(1):e25-6, 2016
Jain VV et al: Dural ectasia in a child with larsen syndrome. J Pediatr Orthop. 34(7):e44-9, 2014
Kono AK et al: Prevalence of dural ectasia in Loeys-Dietz syndrome: comparison with Marfan syndrome and normal controls. PLoS One. 8(9):e75264, 2013
Mesfin A et al: Ten-year clinical and imaging follow-up of dural ectasia in adults with Marfan syndrome. Spine J. 13(1):62-7, 2013
Sznajder M et al: Spinal imaging contributes to the diagnosis of Marfan syndrome. Joint Bone Spine. 77(5):445-50, 2010
García-Estevez DA et al: [Dural ectasia in the cervical spine and neurofibromatosis type 1.] Rev Neurol. 48(1):51, 2009
Sanz-Ayan MP et al: [Dural ectasia and lumbar pain associated with Marfan syndrome.] Rev Neurol. 47(10):559-60, 2008
Kotil K et al: Lumbar radiculopathy in ankylosing spondylitis with dural ectasia. J Clin Neurosci. 14(10):981-3, 2007
Knirsch W et al: Dural ectasia in children with Marfan syndrome: a prospective, multicenter, patient-control study. Am J Med Genet A. 140(7):775-81, 2006
Reitman CA et al: Neurologic and morphologic features of dural ectasia in ankylosing spondylitis and rheumatoid arthritis: a case report. Am J Orthop (Belle Mead NJ). 35(11):530-1, 2006
Habermann CR et al: MR evaluation of dural ectasia in Marfan syndrome: reassessment of the established criteria in children, adolescents, and young adults. Radiology. 234(2):535-41, 2005
Knirsch W et al: Normal values of the sagittal diameter of the lumbar spine (vertebral body and dural sac) in children measured by MRI. Pediatr Radiol. 35(4):419-24, 2005
Tsirikos AI et al: Assessment of vertebral scalloping in neurofibromatosis type 1 with plain radiography and MRI. Clin Radiol. 59(11):1009-17, 2004
Nallamshetty L et al: Dural ectasia and back pain: review of the literature and case report. J Spinal Disord Tech. 15(4):326-9, 2002
Tubbs RS et al: Dural ectasia in neurofibromatosis. Pediatr Neurosurg. 37(6):331-2, 2002
Ahn NU et al: Dural ectasia and conventional radiography in the Marfan lumbosacral spine. Skeletal Radiol. 30(6):338-45, 2001
Oosterhof T et al: Quantitative assessment of dural ectasia as a marker for Marfan syndrome. Radiology. 220(2):514-8, 2001
Ahn NU et al: Dural ectasia in the Marfan syndrome: MR and CT findings and criteria. Genet Med. 2(3):173-9, 2000
Ahn NU et al: Dural ectasia is associated with back pain in Marfan syndrome. Spine. 25(12):1562-8, 2000
Rose PS et al: A comparison of the Berlin and Ghent nosologies and the influence of dural ectasia in the diagnosis of Marfan syndrome. Genet Med. 2(5):278-82, 2000
Schonauer C et al: Lumbosacral dural ectasia in type 1 neurofibromatosis. Report of two cases. J Neurosurg Sci. 44(3):165-8; discussion 169, 2000
Sponseller PD et al: Osseous anatomy of the lumbosacral spine in Marfan syndrome. Spine. 25(21):2797-802, 2000
De Paepe A: Dural ectasia and the diagnosis of Marfan's syndrome. Lancet. 354(9182):878-9, 1999
Fattori R et al: Importance of dural ectasia in phenotypic assessment of Marfan's syndrome. Lancet. 354(9182):910-3, 1999
Villeirs GM et al: Widening of the spinal canal and dural ectasia in Marfan's syndrome: assessment by CT. Neuroradiology. 41(11):850-4, 1999
Raff ML et al: Joint hypermobility syndromes. Curr Opin Rheumatol. 8(5):459-66, 1996
Helfen M et al: Intrathoracic dural ectasia mimicking neurofibroma and scoliosis. A case report. Int Orthop. 19(3):181-4, 1995
Bensaid AH et al: Neurofibromatosis with dural ectasia and bilateral symmetrical pedicular clefts: report of two cases. Neuroradiology. 34(2):107-9, 1992
Pyeritz RE et al: Dural ectasia is a common feature of the Marfan syndrome. Am J Hum Genet. 43(5):726-32, 1988
Stern WE: Dural ectasia and the Marfan syndrome. J Neurosurg. 69(2):221-7, 1988
Katz SG et al: Thoracic and lumbar dural ectasia in a two-year-old boy. Pediatr Radiol. 6(4):238-40, 1978
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
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Diagnostic Checklist
TERMINOLOGY
Synonyms
Dural ectasia
Definitions
Patulous dural sac with posterior vertebral scalloping
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Nonvascular Interventions
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Polster SP et al: Dural ectasia in neurofibromatosis 1: case series, management, and review. Neurosurgery. 86(5):646-55, 2020
Böker T et al: Dural ectasia in Marfan syndrome and other hereditary connective tissue disorders: a 10-year follow-up study. Spine J. 19(8):1412-21, 2019
Kohns DJ: Interventional spine considerations for dural ectasia in a patient with Marfan syndrome. Am J Phys Med Rehabil. 97(1):e6-8, 2018
Razek AAKA: MR imaging of neoplastic and non-neoplastic lesions of the brain and spine in neurofibromatosis type I. Neurol Sci. 39(5):821-7, 2018
Sheridan GA et al: Dural ectasia associated with Mounier-Kuhn syndrome: a novel association in the context of spinal stenosis. BMJ Case Rep. 2017, 2017
Elgafy H et al: Sacral erosion and insufficiency fracture secondary to dural ectasia in patient with Marfan syndrome. Spine J. 16(5):e301-2, 2016
Kow CY et al: Incidental dural ectasia associated with scoliosis. Spine J. 16(1):e25-6, 2016
Jain VV et al: Dural ectasia in a child with larsen syndrome. J Pediatr Orthop. 34(7):e44-9, 2014
Kono AK et al: Prevalence of dural ectasia in Loeys-Dietz syndrome: comparison with Marfan syndrome and normal controls. PLoS One. 8(9):e75264, 2013
Mesfin A et al: Ten-year clinical and imaging follow-up of dural ectasia in adults with Marfan syndrome. Spine J. 13(1):62-7, 2013
Sznajder M et al: Spinal imaging contributes to the diagnosis of Marfan syndrome. Joint Bone Spine. 77(5):445-50, 2010
García-Estevez DA et al: [Dural ectasia in the cervical spine and neurofibromatosis type 1.] Rev Neurol. 48(1):51, 2009
Sanz-Ayan MP et al: [Dural ectasia and lumbar pain associated with Marfan syndrome.] Rev Neurol. 47(10):559-60, 2008
Kotil K et al: Lumbar radiculopathy in ankylosing spondylitis with dural ectasia. J Clin Neurosci. 14(10):981-3, 2007
Knirsch W et al: Dural ectasia in children with Marfan syndrome: a prospective, multicenter, patient-control study. Am J Med Genet A. 140(7):775-81, 2006
Reitman CA et al: Neurologic and morphologic features of dural ectasia in ankylosing spondylitis and rheumatoid arthritis: a case report. Am J Orthop (Belle Mead NJ). 35(11):530-1, 2006
Habermann CR et al: MR evaluation of dural ectasia in Marfan syndrome: reassessment of the established criteria in children, adolescents, and young adults. Radiology. 234(2):535-41, 2005
Knirsch W et al: Normal values of the sagittal diameter of the lumbar spine (vertebral body and dural sac) in children measured by MRI. Pediatr Radiol. 35(4):419-24, 2005
Tsirikos AI et al: Assessment of vertebral scalloping in neurofibromatosis type 1 with plain radiography and MRI. Clin Radiol. 59(11):1009-17, 2004
Nallamshetty L et al: Dural ectasia and back pain: review of the literature and case report. J Spinal Disord Tech. 15(4):326-9, 2002
Tubbs RS et al: Dural ectasia in neurofibromatosis. Pediatr Neurosurg. 37(6):331-2, 2002
Ahn NU et al: Dural ectasia and conventional radiography in the Marfan lumbosacral spine. Skeletal Radiol. 30(6):338-45, 2001
Oosterhof T et al: Quantitative assessment of dural ectasia as a marker for Marfan syndrome. Radiology. 220(2):514-8, 2001
Ahn NU et al: Dural ectasia in the Marfan syndrome: MR and CT findings and criteria. Genet Med. 2(3):173-9, 2000
Ahn NU et al: Dural ectasia is associated with back pain in Marfan syndrome. Spine. 25(12):1562-8, 2000
Rose PS et al: A comparison of the Berlin and Ghent nosologies and the influence of dural ectasia in the diagnosis of Marfan syndrome. Genet Med. 2(5):278-82, 2000
Schonauer C et al: Lumbosacral dural ectasia in type 1 neurofibromatosis. Report of two cases. J Neurosurg Sci. 44(3):165-8; discussion 169, 2000
Sponseller PD et al: Osseous anatomy of the lumbosacral spine in Marfan syndrome. Spine. 25(21):2797-802, 2000
De Paepe A: Dural ectasia and the diagnosis of Marfan's syndrome. Lancet. 354(9182):878-9, 1999
Fattori R et al: Importance of dural ectasia in phenotypic assessment of Marfan's syndrome. Lancet. 354(9182):910-3, 1999
Villeirs GM et al: Widening of the spinal canal and dural ectasia in Marfan's syndrome: assessment by CT. Neuroradiology. 41(11):850-4, 1999
Raff ML et al: Joint hypermobility syndromes. Curr Opin Rheumatol. 8(5):459-66, 1996
Helfen M et al: Intrathoracic dural ectasia mimicking neurofibroma and scoliosis. A case report. Int Orthop. 19(3):181-4, 1995
Bensaid AH et al: Neurofibromatosis with dural ectasia and bilateral symmetrical pedicular clefts: report of two cases. Neuroradiology. 34(2):107-9, 1992
Pyeritz RE et al: Dural ectasia is a common feature of the Marfan syndrome. Am J Hum Genet. 43(5):726-32, 1988
Stern WE: Dural ectasia and the Marfan syndrome. J Neurosurg. 69(2):221-7, 1988
Katz SG et al: Thoracic and lumbar dural ectasia in a two-year-old boy. Pediatr Radiol. 6(4):238-40, 1978
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