Apical displacement of septal and posterior tricuspid valve (TV) leaflets
Coaptation point of TV is lowered into right ventricle (RV), not at atrioventricular junction
Results in "atrialization" of RV
IMAGING
General Features
Echocardiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Freud LR et al: Risk factors for mortality and circulatory outcome among neonates prenatally diagnosed with Ebstein anomaly or tricuspid valve dysplasia: a multicenter study. J Am Heart Assoc. 9(21):e016684, 2020
Masoller N et al: Prediction of perinatal mortality in Ebstein's anomaly diagnosed in the second trimester of pregnancy. Fetal Diagn Ther. 47(8):604-14, 2020
Rydzewska K et al: Ebstein's anomaly: epidemiological analysis and presentation of different prenatal management. J Matern Fetal Neonatal Med. 1-8, 2020
Wang S et al: Extracardiac Doppler indices predict perinatal mortality in fetuses with Ebstein anomaly and tricuspid valve dysplasia. Prenat Diagn. ePub, 2020
Selamet Tierney ES et al: Assessment of progressive pathophysiology after early prenatal diagnosis of the Ebstein anomaly or tricuspid valve dysplasia. Am J Cardiol. 119(1):106-11, 2017
Freud LR et al: Outcomes and predictors of perinatal mortality in fetuses with Ebstein anomaly or tricuspid valve dysplasia in the current era: a multicenter study. Circulation. 132(6):481-9, 2015
Ibrahim M et al: Cone reconstruction for Ebstein's anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg. 149(4):1144-50, 2015
Luu Q et al: Ebstein's anomaly in those surviving to adult life - a single centre experience. Heart Lung Circ. 24(10):996-1001, 2015
Freire G et al: Impact of prenatal haemodynamic and functional abnormalities in Ebstein's anomaly on survival. Cardiol Young. 24(6):1049-56, 2014
Shinkawa T et al: Management and long-term outcome of neonatal Ebstein anomaly. J Thorac Cardiovasc Surg. 139(2):354-8, 2010
Related Anatomy
Loading...
Related Differential Diagnoses
Loading...
References
Tables
Tables
KEY FACTS
Terminology
Imaging
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Definitions
Apical displacement of septal and posterior tricuspid valve (TV) leaflets
Coaptation point of TV is lowered into right ventricle (RV), not at atrioventricular junction
Results in "atrialization" of RV
IMAGING
General Features
Echocardiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Freud LR et al: Risk factors for mortality and circulatory outcome among neonates prenatally diagnosed with Ebstein anomaly or tricuspid valve dysplasia: a multicenter study. J Am Heart Assoc. 9(21):e016684, 2020
Masoller N et al: Prediction of perinatal mortality in Ebstein's anomaly diagnosed in the second trimester of pregnancy. Fetal Diagn Ther. 47(8):604-14, 2020
Rydzewska K et al: Ebstein's anomaly: epidemiological analysis and presentation of different prenatal management. J Matern Fetal Neonatal Med. 1-8, 2020
Wang S et al: Extracardiac Doppler indices predict perinatal mortality in fetuses with Ebstein anomaly and tricuspid valve dysplasia. Prenat Diagn. ePub, 2020
Selamet Tierney ES et al: Assessment of progressive pathophysiology after early prenatal diagnosis of the Ebstein anomaly or tricuspid valve dysplasia. Am J Cardiol. 119(1):106-11, 2017
Freud LR et al: Outcomes and predictors of perinatal mortality in fetuses with Ebstein anomaly or tricuspid valve dysplasia in the current era: a multicenter study. Circulation. 132(6):481-9, 2015
Ibrahim M et al: Cone reconstruction for Ebstein's anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg. 149(4):1144-50, 2015
Luu Q et al: Ebstein's anomaly in those surviving to adult life - a single centre experience. Heart Lung Circ. 24(10):996-1001, 2015
Freire G et al: Impact of prenatal haemodynamic and functional abnormalities in Ebstein's anomaly on survival. Cardiol Young. 24(6):1049-56, 2014
Shinkawa T et al: Management and long-term outcome of neonatal Ebstein anomaly. J Thorac Cardiovasc Surg. 139(2):354-8, 2010
STATdx includes over 200,000 searchable images, including x-ray, CT, MR, and ultrasound images. To access all images, please log in or subscribe.