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KEY FACTS
Terminology
Imaging
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Definitions
- Apical displacement of septal and posterior tricuspid valve (TV) leaflets
- Coaptation point of TV is lowered into right ventricle (RV), not at atrioventricular junction
- Results in "atrialization" of RV
- Coaptation point of TV is lowered into right ventricle (RV), not at atrioventricular junction
- Apical displacement of septal and posterior tricuspid valve (TV) leaflets
IMAGING
General Features
Echocardiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Freud LR et al: Risk factors for mortality and circulatory outcome among neonates prenatally diagnosed with Ebstein anomaly or tricuspid valve dysplasia: a multicenter study. J Am Heart Assoc. 9(21):e016684, 2020
- Masoller N et al: Prediction of perinatal mortality in Ebstein's anomaly diagnosed in the second trimester of pregnancy. Fetal Diagn Ther. 47(8):604-14, 2020
- Rydzewska K et al: Ebstein's anomaly: epidemiological analysis and presentation of different prenatal management. J Matern Fetal Neonatal Med. 1-8, 2020
- Wang S et al: Extracardiac Doppler indices predict perinatal mortality in fetuses with Ebstein anomaly and tricuspid valve dysplasia. Prenat Diagn. ePub, 2020
- Selamet Tierney ES et al: Assessment of progressive pathophysiology after early prenatal diagnosis of the Ebstein anomaly or tricuspid valve dysplasia. Am J Cardiol. 119(1):106-11, 2017
- Freud LR et al: Outcomes and predictors of perinatal mortality in fetuses with Ebstein anomaly or tricuspid valve dysplasia in the current era: a multicenter study. Circulation. 132(6):481-9, 2015
- Ibrahim M et al: Cone reconstruction for Ebstein's anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg. 149(4):1144-50, 2015
- Luu Q et al: Ebstein's anomaly in those surviving to adult life - a single centre experience. Heart Lung Circ. 24(10):996-1001, 2015
- Freire G et al: Impact of prenatal haemodynamic and functional abnormalities in Ebstein's anomaly on survival. Cardiol Young. 24(6):1049-56, 2014
- Shinkawa T et al: Management and long-term outcome of neonatal Ebstein anomaly. J Thorac Cardiovasc Surg. 139(2):354-8, 2010
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Definitions
- Apical displacement of septal and posterior tricuspid valve (TV) leaflets
- Coaptation point of TV is lowered into right ventricle (RV), not at atrioventricular junction
- Results in "atrialization" of RV
- Coaptation point of TV is lowered into right ventricle (RV), not at atrioventricular junction
- Apical displacement of septal and posterior tricuspid valve (TV) leaflets
IMAGING
General Features
Echocardiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Freud LR et al: Risk factors for mortality and circulatory outcome among neonates prenatally diagnosed with Ebstein anomaly or tricuspid valve dysplasia: a multicenter study. J Am Heart Assoc. 9(21):e016684, 2020
- Masoller N et al: Prediction of perinatal mortality in Ebstein's anomaly diagnosed in the second trimester of pregnancy. Fetal Diagn Ther. 47(8):604-14, 2020
- Rydzewska K et al: Ebstein's anomaly: epidemiological analysis and presentation of different prenatal management. J Matern Fetal Neonatal Med. 1-8, 2020
- Wang S et al: Extracardiac Doppler indices predict perinatal mortality in fetuses with Ebstein anomaly and tricuspid valve dysplasia. Prenat Diagn. ePub, 2020
- Selamet Tierney ES et al: Assessment of progressive pathophysiology after early prenatal diagnosis of the Ebstein anomaly or tricuspid valve dysplasia. Am J Cardiol. 119(1):106-11, 2017
- Freud LR et al: Outcomes and predictors of perinatal mortality in fetuses with Ebstein anomaly or tricuspid valve dysplasia in the current era: a multicenter study. Circulation. 132(6):481-9, 2015
- Ibrahim M et al: Cone reconstruction for Ebstein's anomaly: patient outcomes, biventricular function, and cardiopulmonary exercise capacity. J Thorac Cardiovasc Surg. 149(4):1144-50, 2015
- Luu Q et al: Ebstein's anomaly in those surviving to adult life - a single centre experience. Heart Lung Circ. 24(10):996-1001, 2015
- Freire G et al: Impact of prenatal haemodynamic and functional abnormalities in Ebstein's anomaly on survival. Cardiol Young. 24(6):1049-56, 2014
- Shinkawa T et al: Management and long-term outcome of neonatal Ebstein anomaly. J Thorac Cardiovasc Surg. 139(2):354-8, 2010
