link
Bookmarks
Epidermolysis and Pemphigoid
Atif Zaheer, MD; Michael P. Federle, MD, FACR
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Subscribe
0
3
2
2

KEY FACTS

  • Terminology

    • Imaging

      • Clinical Issues

        TERMINOLOGY

        • Definitions

          • Epidermolysis bullosa (EB): Heterogeneous group of rare inherited skin blistering diseases that develop in response to minor trauma
          • Benign mucous membrane pemphigoid (BMMP): Acquired autoimmune skin blistering disease

        IMAGING

        • General Features

          • Imaging Recommendations

            • Radiographic Findings

              DIFFERENTIAL DIAGNOSIS

                PATHOLOGY

                • General Features

                  • Microscopic Features

                    CLINICAL ISSUES

                    • Presentation

                      • Demographics

                        • Natural History & Prognosis

                          • Treatment

                            Selected References

                            1. Lee MH et al: Clinical, imaging, and pathologic features of conditions with combined esophageal and cutaneous manifestations. Radiographics. 39(5):1411-34, 2019
                            2. Amber KT et al: Autoimmune subepidermal bullous diseases of the skin and mucosae: clinical features, diagnosis, and management. Clin Rev Allergy Immunol. 54(1):26-51, 2018
                            3. Ksia A et al: [Esophageal strictures in children with epidermolysis bullosa.] Arch Pediatr. 19(12):1325-9, 2012
                            4. Fine JD et al: Epidermolysis bullosa and the risk of life-threatening cancers: the National EB Registry experience, 1986-2006. J Am Acad Dermatol. 60(2):203-11, 2009
                            5. Oliveira TM et al: Clinical management for epidermolysis bullosa dystrophica. J Appl Oral Sci. 16(1):81-5, 2008
                            6. Image interpretation session 1999: Dunnick NR. Radiographics. 20(1):268-9, 2000
                            Related Anatomy
                            Loading...
                            Related Differential Diagnoses
                            Loading...
                            References
                            Tables

                            Tables

                            KEY FACTS

                            • Terminology

                              • Imaging

                                • Clinical Issues

                                  TERMINOLOGY

                                  • Definitions

                                    • Epidermolysis bullosa (EB): Heterogeneous group of rare inherited skin blistering diseases that develop in response to minor trauma
                                    • Benign mucous membrane pemphigoid (BMMP): Acquired autoimmune skin blistering disease

                                  IMAGING

                                  • General Features

                                    • Imaging Recommendations

                                      • Radiographic Findings

                                        DIFFERENTIAL DIAGNOSIS

                                          PATHOLOGY

                                          • General Features

                                            • Microscopic Features

                                              CLINICAL ISSUES

                                              • Presentation

                                                • Demographics

                                                  • Natural History & Prognosis

                                                    • Treatment

                                                      Selected References

                                                      1. Lee MH et al: Clinical, imaging, and pathologic features of conditions with combined esophageal and cutaneous manifestations. Radiographics. 39(5):1411-34, 2019
                                                      2. Amber KT et al: Autoimmune subepidermal bullous diseases of the skin and mucosae: clinical features, diagnosis, and management. Clin Rev Allergy Immunol. 54(1):26-51, 2018
                                                      3. Ksia A et al: [Esophageal strictures in children with epidermolysis bullosa.] Arch Pediatr. 19(12):1325-9, 2012
                                                      4. Fine JD et al: Epidermolysis bullosa and the risk of life-threatening cancers: the National EB Registry experience, 1986-2006. J Am Acad Dermatol. 60(2):203-11, 2009
                                                      5. Oliveira TM et al: Clinical management for epidermolysis bullosa dystrophica. J Appl Oral Sci. 16(1):81-5, 2008
                                                      6. Image interpretation session 1999: Dunnick NR. Radiographics. 20(1):268-9, 2000