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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
- Aggressive fibromatosis, extraabdominal desmoid, infantile fibromatosis
Definitions
- Rare, infiltrative mass lesion of benign monoclonal fibroblast proliferation
- In head & neck, these are deep fibromatoses
- Superficial fibromatoses most often in extremities
- Rare, infiltrative mass lesion of benign monoclonal fibroblast proliferation
IMAGING
General Features
CT Findings
MR Findings
Imaging Recommendations
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Reporting Tips
Selected References
- Cho YA et al: Case of medullary thyroid carcinoma with desmoid-type fibromatosis. Pathol Int. 70(6):364-9, 2020
- Daram SP et al: Desmoid fibromatosis of the maxilla. Ear Nose Throat J. 99(1):NP6-8, 2020
- Moro A et al: Orbital desmoid-type fibromatosis: a case report and literature review. Case Rep Oncol Med. 2018:1684763, 2018
- Rebecchini C et al: Papillary thyroid carcinoma with nodular fasciitis-like stroma and β-catenin mutations should be renamed papillary thyroid carcinoma with desmoid-type fibromatosis. Mod Pathol. 30(2):236-45, 2017
- Xia C et al: Sonography used in the infantile desmoid fibromatosis of postcricoid area: a case report. Medicine (Baltimore). 96(44):e8500, 2017
- Lacayo EA et al: Deep neck fibromatosis after diskectomy and cervical fusion: case series and review of the literature. AJR Am J Roentgenol. 1-5, 2016
- Otero S et al: Desmoid-type fibromatosis. Clin Radiol. 70(9):1038-45, 2015
- Wang W et al: Age-based treatment of aggressive fibromatosis in the head and neck region. J Oral Maxillofac Surg. 72(2):311-21, 2014
- Rhim JH et al: Desmoid-type fibromatosis in the head and neck: CT and MR imaging characteristics. Neuroradiology. 55(3):351-9, 2013
- Soto-Miranda MA et al: Surgical treatment of pediatric desmoid tumors. A 12-year, single-center experience. Ann Surg Oncol. 20(11):3384-90, 2013
- Meazza C et al: Aggressive fibromatosis in children and adolescents: the Italian experience. Cancer. 116(1):233-40, 2010
- Guglielmi G et al: Imaging of superficial and deep fibromatosis. Radiol Med. 114(8):1292-307, 2009
- Lazar AJ et al: Desmoid tumor: from surgical extirpation to molecular dissection. Curr Opin Oncol. 21(4):352-9, 2009
- McKenzie G et al: Pictorial review: Non-neoplastic soft-tissue masses. Br J Radiol. 82(981):775-85, 2009
- Schneider M et al: Desmoplastic fibroma of the mandible--review of the literature and presentation of a rare case. Head Face Med. 5:25, 2009
- Sinno H et al: Desmoid tumors of the pediatric mandible: case report and review. Ann Plast Surg. 62(2):213-9, 2009
- Chung EM et al: From the Archives of the AFIP. Pediatric orbit tumors and tumorlike lesions: osseous lesions of the orbit. Radiographics. 28(4):1193-214, 2008
- Douglas-Akinwande AC et al: AJR teaching file: facial mass in a child. AJR Am J Roentgenol. 191(3 Suppl):S37-9, 2008
- Hsu YB et al: Pathology quiz case. Fibromatosis (desmoid tumor) of the neck. Arch Otolaryngol Head Neck Surg. 134(5):559, 560-1, 2008
- Melis M et al: Multimodality management of desmoid tumors: how important is a negative surgical margin? J Surg Oncol. 98(8):594-602, 2008
- Sharma A et al: Pediatric aggressive fibromatosis of the head and neck: a 20-year retrospective review. J Pediatr Surg. 43(9):1596-604, 2008
- Wong SL: Diagnosis and management of desmoid tumors and fibrosarcoma. J Surg Oncol. 97(6):554-8, 2008
- Basu S et al: Uptake characteristics of fluorodeoxyglucose (FDG) in deep fibromatosis and abdominal desmoids: potential clinical role of FDG-PET in the management. Br J Radiol. 80(957):750-6, 2007
- Dinauer PA et al: Pathologic and MR imaging features of benign fibrous soft-tissue tumors in adults. Radiographics. 27(1):173-87, 2007
- Goodwin RW et al: MRI appearances of common benign soft-tissue tumours. Clin Radiol. 62(9):843-53, 2007
- Tolan S et al: Fibromatosis: benign by name but not necessarily by nature. Clin Oncol (R Coll Radiol). 19(5):319-26, 2007
- Okuno S: The enigma of desmoid tumors. Curr Treat Options Oncol. 7(6):438-43, 2006
- Abikhzer G et al: Aggressive fibromatosis of the head and neck: case report and review of the literature. J Otolaryngol. 34(4):289-94, 2005
- Collins BJ et al: Desmoid tumors of the head and neck: a review. Ann Plast Surg. 54(1):103-8, 2005
- Koeda S et al: Extra-abdominal fibromatosis of the cheek: report of a case. J Oral Maxillofac Surg. 63(8):1222-6, 2005
- Mendenhall WM et al: Aggressive fibromatosis. Am J Clin Oncol. 28(2):211-5, 2005
- Schlemmer M: Desmoid tumors and deep fibromatoses. Hematol Oncol Clin North Am. 19(3):565-71, vii-viii, 2005
- Gronchi A et al: Quality of surgery and outcome in extra-abdominal aggressive fibromatosis: a series of patients surgically treated at a single institution. J Clin Oncol. 21(7):1390-7, 2003
- Janinis J et al: The pharmacological treatment of aggressive fibromatosis: a systematic review. Ann Oncol. 14(2):181-90, 2003
- Zlotecki RA et al: External beam radiotherapy for primary and adjuvant management of aggressive fibromatosis. Int J Radiat Oncol Biol Phys. 54(1):177-81, 2002
- Abdelkader M et al: Aggressive fibromatosis of the head and neck (desmoid tumours). J Laryngol Otol. 115(10):772-6, 2001
- Robbin MR et al: Imaging of musculoskeletal fibromatosis. RadioGraphics. 21(10):585-600, 2001
- Hoos A et al: Desmoid tumors of the head and neck--a clinical study of a rare entity. Head Neck. 22(8):814-21, 2000
- Pignatti G et al: Extraabdominal desmoid tumor. A study of 83 cases. Clin Orthop. (375):207-13, 2000
- Flacke S et al: Infantile fibromatosis of the neck with intracranial involvement: MR and CT findings. AJNR Am J Neuroradiol. 20(5):923-5, 1999
- Garant M et al: Aggressive fibromatosis of the neck: MR findings. AJNR Am J Neuroradiol. 18(8):1429-31, 1997
- Vandevenne JE et al: New concepts in understanding evolution of desmoid tumors: MR imaging of 30 lesions. Eur Radiol. 7(7):1013-9, 1997
- Faulkner LB et al: Pediatric desmoid tumor: retrospective analysis of 63 cases. J Clin Oncol. 13(11):2813-8, 1995
- Lewin JS et al: Aggressive fibromatosis of the prevertebral and retropharyngeal spaces: MR and CT characteristics. AJNR Am J Neuroradiol. 16(4 Suppl):897-900, 1995
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
- Aggressive fibromatosis, extraabdominal desmoid, infantile fibromatosis
Definitions
- Rare, infiltrative mass lesion of benign monoclonal fibroblast proliferation
- In head & neck, these are deep fibromatoses
- Superficial fibromatoses most often in extremities
- Rare, infiltrative mass lesion of benign monoclonal fibroblast proliferation
IMAGING
General Features
CT Findings
MR Findings
Imaging Recommendations
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Reporting Tips
Selected References
- Cho YA et al: Case of medullary thyroid carcinoma with desmoid-type fibromatosis. Pathol Int. 70(6):364-9, 2020
- Daram SP et al: Desmoid fibromatosis of the maxilla. Ear Nose Throat J. 99(1):NP6-8, 2020
- Moro A et al: Orbital desmoid-type fibromatosis: a case report and literature review. Case Rep Oncol Med. 2018:1684763, 2018
- Rebecchini C et al: Papillary thyroid carcinoma with nodular fasciitis-like stroma and β-catenin mutations should be renamed papillary thyroid carcinoma with desmoid-type fibromatosis. Mod Pathol. 30(2):236-45, 2017
- Xia C et al: Sonography used in the infantile desmoid fibromatosis of postcricoid area: a case report. Medicine (Baltimore). 96(44):e8500, 2017
- Lacayo EA et al: Deep neck fibromatosis after diskectomy and cervical fusion: case series and review of the literature. AJR Am J Roentgenol. 1-5, 2016
- Otero S et al: Desmoid-type fibromatosis. Clin Radiol. 70(9):1038-45, 2015
- Wang W et al: Age-based treatment of aggressive fibromatosis in the head and neck region. J Oral Maxillofac Surg. 72(2):311-21, 2014
- Rhim JH et al: Desmoid-type fibromatosis in the head and neck: CT and MR imaging characteristics. Neuroradiology. 55(3):351-9, 2013
- Soto-Miranda MA et al: Surgical treatment of pediatric desmoid tumors. A 12-year, single-center experience. Ann Surg Oncol. 20(11):3384-90, 2013
- Meazza C et al: Aggressive fibromatosis in children and adolescents: the Italian experience. Cancer. 116(1):233-40, 2010
- Guglielmi G et al: Imaging of superficial and deep fibromatosis. Radiol Med. 114(8):1292-307, 2009
- Lazar AJ et al: Desmoid tumor: from surgical extirpation to molecular dissection. Curr Opin Oncol. 21(4):352-9, 2009
- McKenzie G et al: Pictorial review: Non-neoplastic soft-tissue masses. Br J Radiol. 82(981):775-85, 2009
- Schneider M et al: Desmoplastic fibroma of the mandible--review of the literature and presentation of a rare case. Head Face Med. 5:25, 2009
- Sinno H et al: Desmoid tumors of the pediatric mandible: case report and review. Ann Plast Surg. 62(2):213-9, 2009
- Chung EM et al: From the Archives of the AFIP. Pediatric orbit tumors and tumorlike lesions: osseous lesions of the orbit. Radiographics. 28(4):1193-214, 2008
- Douglas-Akinwande AC et al: AJR teaching file: facial mass in a child. AJR Am J Roentgenol. 191(3 Suppl):S37-9, 2008
- Hsu YB et al: Pathology quiz case. Fibromatosis (desmoid tumor) of the neck. Arch Otolaryngol Head Neck Surg. 134(5):559, 560-1, 2008
- Melis M et al: Multimodality management of desmoid tumors: how important is a negative surgical margin? J Surg Oncol. 98(8):594-602, 2008
- Sharma A et al: Pediatric aggressive fibromatosis of the head and neck: a 20-year retrospective review. J Pediatr Surg. 43(9):1596-604, 2008
- Wong SL: Diagnosis and management of desmoid tumors and fibrosarcoma. J Surg Oncol. 97(6):554-8, 2008
- Basu S et al: Uptake characteristics of fluorodeoxyglucose (FDG) in deep fibromatosis and abdominal desmoids: potential clinical role of FDG-PET in the management. Br J Radiol. 80(957):750-6, 2007
- Dinauer PA et al: Pathologic and MR imaging features of benign fibrous soft-tissue tumors in adults. Radiographics. 27(1):173-87, 2007
- Goodwin RW et al: MRI appearances of common benign soft-tissue tumours. Clin Radiol. 62(9):843-53, 2007
- Tolan S et al: Fibromatosis: benign by name but not necessarily by nature. Clin Oncol (R Coll Radiol). 19(5):319-26, 2007
- Okuno S: The enigma of desmoid tumors. Curr Treat Options Oncol. 7(6):438-43, 2006
- Abikhzer G et al: Aggressive fibromatosis of the head and neck: case report and review of the literature. J Otolaryngol. 34(4):289-94, 2005
- Collins BJ et al: Desmoid tumors of the head and neck: a review. Ann Plast Surg. 54(1):103-8, 2005
- Koeda S et al: Extra-abdominal fibromatosis of the cheek: report of a case. J Oral Maxillofac Surg. 63(8):1222-6, 2005
- Mendenhall WM et al: Aggressive fibromatosis. Am J Clin Oncol. 28(2):211-5, 2005
- Schlemmer M: Desmoid tumors and deep fibromatoses. Hematol Oncol Clin North Am. 19(3):565-71, vii-viii, 2005
- Gronchi A et al: Quality of surgery and outcome in extra-abdominal aggressive fibromatosis: a series of patients surgically treated at a single institution. J Clin Oncol. 21(7):1390-7, 2003
- Janinis J et al: The pharmacological treatment of aggressive fibromatosis: a systematic review. Ann Oncol. 14(2):181-90, 2003
- Zlotecki RA et al: External beam radiotherapy for primary and adjuvant management of aggressive fibromatosis. Int J Radiat Oncol Biol Phys. 54(1):177-81, 2002
- Abdelkader M et al: Aggressive fibromatosis of the head and neck (desmoid tumours). J Laryngol Otol. 115(10):772-6, 2001
- Robbin MR et al: Imaging of musculoskeletal fibromatosis. RadioGraphics. 21(10):585-600, 2001
- Hoos A et al: Desmoid tumors of the head and neck--a clinical study of a rare entity. Head Neck. 22(8):814-21, 2000
- Pignatti G et al: Extraabdominal desmoid tumor. A study of 83 cases. Clin Orthop. (375):207-13, 2000
- Flacke S et al: Infantile fibromatosis of the neck with intracranial involvement: MR and CT findings. AJNR Am J Neuroradiol. 20(5):923-5, 1999
- Garant M et al: Aggressive fibromatosis of the neck: MR findings. AJNR Am J Neuroradiol. 18(8):1429-31, 1997
- Vandevenne JE et al: New concepts in understanding evolution of desmoid tumors: MR imaging of 30 lesions. Eur Radiol. 7(7):1013-9, 1997
- Faulkner LB et al: Pediatric desmoid tumor: retrospective analysis of 63 cases. J Clin Oncol. 13(11):2813-8, 1995
- Lewin JS et al: Aggressive fibromatosis of the prevertebral and retropharyngeal spaces: MR and CT characteristics. AJNR Am J Neuroradiol. 16(4 Suppl):897-900, 1995
