Cephalocele: Outward herniation of CNS contents through defect in cranium
Term includes meningocele and meningoencephalocele
Congenital herniation of meninges and CSF (meningocele) + brain tissue (meningoencephalocele)
Through mesodermal defect in anterior skull/skull base presenting as extranasal, intranasal, or medial orbital mass
Do not confuse for basal encephaloceles,which occur through cribriform plate or sphenoid defects
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Arifin M et al: Frontoethmoidal encephalocele: clinical presentation, diagnosis, treatment, and complications in 400 cases. Childs Nerv Syst. 34(6):1161-8, 2018
Keshri AK et al: Transnasal endoscopic repair of pediatric meningoencephalocele. J Pediatr Neurosci. 11(1):42-5, 2016
Castelnuovo P et al: Endoscopic endonasal management of encephaloceles in children: an eight-year experience. Int J Pediatr Otorhinolaryngol. 73(8):1132-6, 2009
Kumar A et al: Correction of frontonasoethmoidal encephalocele: the HULA procedure. Plast Reconstr Surg. 123(2):661-9, 2009
Arshad AR et al: Frontoethmoidal encephalocele: treatment and outcome. J Craniofac Surg. 19(1):175-83, 2008
Holm C et al: Extracranial correction of frontoethmoidal meningoencephaloceles: feasibility and outcome in 52 consecutive cases. Plast Reconstr Surg. 121(6):386e-95e, 2008
Lo BW et al: Clinical predictors of developmental outcome in patients with cephaloceles. J Neurosurg Pediatr. 2(4):254-7, 2008
Rahbar R et al: Nasal glioma and encephalocele: diagnosis and management. Laryngoscope. 113(12):2069-77, 2003
Rojvachiranonda N et al: Frontoethmoidal encephalomeningocele: new morphological findings and a new classification. J Craniofac Surg. 14(6):847-58, 2003
Mahapatra AK et al: Anterior encephaloceles: a study of 92 cases. Pediatr Neurosurg. 36(3):113-8, 2002
Holmes AD et al: Frontoethmoidal encephaloceles: reconstruction and refinements. J Craniofac Surg. 12(1):6-18, 2001
De Ponte FS et al: Surgical treatment of frontoethmoidal encephalocele: a case report. J Craniofac Surg. 11(4):342-5, 2000
Songur E et al: Management of frontoethmoidal (sincipital) encephalocele. J Craniofac Surg. 10(2):135-9, 1999
Boonvisut S et al: Morphologic study of 120 skull base defects in frontoethmoidal encephalomeningoceles. Plast Reconstr Surg. 101(7):1784-95, 1998
Turgut M et al: Congenital nasal encephalocele: a review of 35 cases. J Craniomaxillofac Surg. 23(1):1-5, 1995
Koch BL et al: Congenital malformations causing skull base changes. Neuroimaging Clin N Am. 4(3):479-98, 1994
Naidich TP et al: Cephaloceles and related malformations. AJNR Am J Neuroradiol. 13(2):655-90, 1992
Barkovich AJ et al: Congenital nasal masses: CT and MR imaging features in 16 cases. AJNR Am J Neuroradiol. 12(1):105-16, 1991
David DJ et al: Cephaloceles: classification, pathology, and management. World J Surg. 13(4):349-57, 1989
Vattoth S, Chapman PR. Anterior skull base. In: Watanabe K, et al., eds. Anatomy for Plastic Surgery of the Face, Head, and Neck.1st ed. New York: Thieme Publishers; 2016:13-9
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Frontoethmoidal cephalocele (FECeph)
Frontonasal cephalocele (FNCeph)
Nasoethmoidal cephalocele (NECeph)
Nasoorbital cephalocele (NOCeph)
Synonyms
Sincipital cephalocele
Definitions
Cephalocele: Outward herniation of CNS contents through defect in cranium
Term includes meningocele and meningoencephalocele
Congenital herniation of meninges and CSF (meningocele) + brain tissue (meningoencephalocele)
Through mesodermal defect in anterior skull/skull base presenting as extranasal, intranasal, or medial orbital mass
Do not confuse for basal encephaloceles,which occur through cribriform plate or sphenoid defects
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Arifin M et al: Frontoethmoidal encephalocele: clinical presentation, diagnosis, treatment, and complications in 400 cases. Childs Nerv Syst. 34(6):1161-8, 2018
Keshri AK et al: Transnasal endoscopic repair of pediatric meningoencephalocele. J Pediatr Neurosci. 11(1):42-5, 2016
Castelnuovo P et al: Endoscopic endonasal management of encephaloceles in children: an eight-year experience. Int J Pediatr Otorhinolaryngol. 73(8):1132-6, 2009
Kumar A et al: Correction of frontonasoethmoidal encephalocele: the HULA procedure. Plast Reconstr Surg. 123(2):661-9, 2009
Arshad AR et al: Frontoethmoidal encephalocele: treatment and outcome. J Craniofac Surg. 19(1):175-83, 2008
Holm C et al: Extracranial correction of frontoethmoidal meningoencephaloceles: feasibility and outcome in 52 consecutive cases. Plast Reconstr Surg. 121(6):386e-95e, 2008
Lo BW et al: Clinical predictors of developmental outcome in patients with cephaloceles. J Neurosurg Pediatr. 2(4):254-7, 2008
Rahbar R et al: Nasal glioma and encephalocele: diagnosis and management. Laryngoscope. 113(12):2069-77, 2003
Rojvachiranonda N et al: Frontoethmoidal encephalomeningocele: new morphological findings and a new classification. J Craniofac Surg. 14(6):847-58, 2003
Mahapatra AK et al: Anterior encephaloceles: a study of 92 cases. Pediatr Neurosurg. 36(3):113-8, 2002
Holmes AD et al: Frontoethmoidal encephaloceles: reconstruction and refinements. J Craniofac Surg. 12(1):6-18, 2001
De Ponte FS et al: Surgical treatment of frontoethmoidal encephalocele: a case report. J Craniofac Surg. 11(4):342-5, 2000
Songur E et al: Management of frontoethmoidal (sincipital) encephalocele. J Craniofac Surg. 10(2):135-9, 1999
Boonvisut S et al: Morphologic study of 120 skull base defects in frontoethmoidal encephalomeningoceles. Plast Reconstr Surg. 101(7):1784-95, 1998
Turgut M et al: Congenital nasal encephalocele: a review of 35 cases. J Craniomaxillofac Surg. 23(1):1-5, 1995
Koch BL et al: Congenital malformations causing skull base changes. Neuroimaging Clin N Am. 4(3):479-98, 1994
Naidich TP et al: Cephaloceles and related malformations. AJNR Am J Neuroradiol. 13(2):655-90, 1992
Barkovich AJ et al: Congenital nasal masses: CT and MR imaging features in 16 cases. AJNR Am J Neuroradiol. 12(1):105-16, 1991
David DJ et al: Cephaloceles: classification, pathology, and management. World J Surg. 13(4):349-57, 1989
Vattoth S, Chapman PR. Anterior skull base. In: Watanabe K, et al., eds. Anatomy for Plastic Surgery of the Face, Head, and Neck.1st ed. New York: Thieme Publishers; 2016:13-9
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