Multisystem necrotizing granulomatous vasculitis of autoimmune origin, which affects small to medium-sized vessels
IMAGING
General Features
Radiographic Findings
CT Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Feragalli B et al: The lung in systemic vasculitis: radiological patterns and differential diagnosis. Br J Radiol. 89(1061):20150992, 2016
Serra G et al: Thoracic involvement in systemic primary vasculitis: radiological patterns and follow-up. JBR-BTR. 97(2):57-68, 2014
CastaƱer E et al: Imaging findings in pulmonary vasculitis. Semin Ultrasound CT MR. 33(6):567-79, 2012
Martinez F et al: Common and uncommon manifestations of Wegener granulomatosis at chest CT: radiologic-pathologic correlation. Radiographics. 32(1):51-69, 2012
Chung MP et al: Imaging of pulmonary vasculitis. Radiology. 255(2):322-41, 2010
Ananthakrishnan L et al: Wegener's granulomatosis in the chest: high-resolution CT findings. AJR Am J Roentgenol. 192(3):676-82, 2009
Allen SD et al: Imaging of Wegener's granulomatosis. Br J Radiol. 80(957):757-65, 2007
Lee KS et al: Thoracic manifestation of Wegener's granulomatosis: CT findings in 30 patients. Eur Radiol. 13(1):43-51, 2003
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
TERMINOLOGY
Abbreviations
Granulomatosis with polyangiitis (GPA)
Synonyms
Wegener granulomatosis (term no longer used)
Definitions
Multisystem necrotizing granulomatous vasculitis of autoimmune origin, which affects small to medium-sized vessels
IMAGING
General Features
Radiographic Findings
CT Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Feragalli B et al: The lung in systemic vasculitis: radiological patterns and differential diagnosis. Br J Radiol. 89(1061):20150992, 2016
Serra G et al: Thoracic involvement in systemic primary vasculitis: radiological patterns and follow-up. JBR-BTR. 97(2):57-68, 2014
CastaƱer E et al: Imaging findings in pulmonary vasculitis. Semin Ultrasound CT MR. 33(6):567-79, 2012
Martinez F et al: Common and uncommon manifestations of Wegener granulomatosis at chest CT: radiologic-pathologic correlation. Radiographics. 32(1):51-69, 2012
Chung MP et al: Imaging of pulmonary vasculitis. Radiology. 255(2):322-41, 2010
Ananthakrishnan L et al: Wegener's granulomatosis in the chest: high-resolution CT findings. AJR Am J Roentgenol. 192(3):676-82, 2009
Allen SD et al: Imaging of Wegener's granulomatosis. Br J Radiol. 80(957):757-65, 2007
Lee KS et al: Thoracic manifestation of Wegener's granulomatosis: CT findings in 30 patients. Eur Radiol. 13(1):43-51, 2003
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