Cervical myelopathy related to anterior displacement of posterior cervical dura with flexion
IMAGING
General Features
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Lay SE et al: Hirayama disease (non-progressive juvenile spinal muscular atrophy), 2020
Kieser DC et al: Hirayama disease. Eur Spine J. 27(6):1201-6, 2018
Paredes I et al: A severe case of Hirayama disease successfully treated by anterior cervical fusion. J Neurosurg Spine. 20(2):191-5, 2014
Lehman VT et al: Cervical spine MR imaging findings of patients with Hirayama disease in North America: a multisite study. AJNR Am J Neuroradiol. 34(2):451-6, 2013
Zhou B et al: Clinical features of Hirayama disease in mainland China. Amyotroph Lateral Scler. 11(1-2):133-9, 2010
Patel TR et al: Lack of epidural pressure change with neck flexion in a patient with Hirayama disease: case report. Neurosurgery. 64(6):E1196-7; discussion E1197, 2009
Cerami C et al: A cervical myelopathy with a Hirayama disease-like phenotype. Neurol Sci. 29(6):451-4, 2008
Hirayama K: [Juvenile muscular atrophy of unilateral upper extremity (Hirayama disease)--half-century progress and establishment since its discovery.] Brain Nerve. 60(1):17-29, 2008
Huang YC et al: A clinical study of Hirayama disease in Taiwan. Muscle Nerve. 37(5):576-82, 2008
Misra UK et al: A clinical, magnetic resonance imaging, and survival motor neuron gene deletion study of Hirayama disease. Arch Neurol. 62(1):120-3, 2005
Chen CJ et al: Hirayama flexion myelopathy: neutral-position MR imaging findings--importance of loss of attachment. Radiology. 231(1):39-44, 2004
Cervical myelopathy related to anterior displacement of posterior cervical dura with flexion
IMAGING
General Features
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
Lay SE et al: Hirayama disease (non-progressive juvenile spinal muscular atrophy), 2020
Kieser DC et al: Hirayama disease. Eur Spine J. 27(6):1201-6, 2018
Paredes I et al: A severe case of Hirayama disease successfully treated by anterior cervical fusion. J Neurosurg Spine. 20(2):191-5, 2014
Lehman VT et al: Cervical spine MR imaging findings of patients with Hirayama disease in North America: a multisite study. AJNR Am J Neuroradiol. 34(2):451-6, 2013
Zhou B et al: Clinical features of Hirayama disease in mainland China. Amyotroph Lateral Scler. 11(1-2):133-9, 2010
Patel TR et al: Lack of epidural pressure change with neck flexion in a patient with Hirayama disease: case report. Neurosurgery. 64(6):E1196-7; discussion E1197, 2009
Cerami C et al: A cervical myelopathy with a Hirayama disease-like phenotype. Neurol Sci. 29(6):451-4, 2008
Hirayama K: [Juvenile muscular atrophy of unilateral upper extremity (Hirayama disease)--half-century progress and establishment since its discovery.] Brain Nerve. 60(1):17-29, 2008
Huang YC et al: A clinical study of Hirayama disease in Taiwan. Muscle Nerve. 37(5):576-82, 2008
Misra UK et al: A clinical, magnetic resonance imaging, and survival motor neuron gene deletion study of Hirayama disease. Arch Neurol. 62(1):120-3, 2005
Chen CJ et al: Hirayama flexion myelopathy: neutral-position MR imaging findings--importance of loss of attachment. Radiology. 231(1):39-44, 2004