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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
TERMINOLOGY
Abbreviations
- Pulmonary Langerhans cell histiocytosis (PLCH)
- Langerhans cell histiocytosis (LCH)
- Erdheim-Chester disease (ECD)
- Rosai-Dorfman disease (RDD)
- Pulmonary Langerhans cell histiocytosis (PLCH)
Synonyms
- RDD: Sinus histiocytosis with massive lymphadenopathy
Definitions
- Rare disorders characterized by accumulation of macrophages, dendritic cells, or monocyte-derived cells in various tissues and organs
- PLCH: Isolated form of LCH occurring in smokers characterized by granulomatous infiltration of distal bronchial walls with cells derived from myeloid dendritic cells (i.e., Langerhans cells)
- ECD: Non-LCH dendritic cell disorder characterized by xanthomatous infiltration of involved tissues by foamy histiocytes
- RDD: Nonmalignant proliferation of histiocytic &/or phagocytic cells
IMAGING
Radiographic Findings
CT Findings
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Vargas D et al: Cardiothoracic manifestations of primary histiocytoses. Br J Radiol. 89(1068):20160347, 2016
- Ahuja J et al: Histiocytic disorders of the chest: imaging findings. Radiographics. 35(2):357-70, 2015
- Antunes C et al: Thoracic, abdominal and musculoskeletal involvement in Erdheim-Chester disease: CT, MR and PET imaging findings. Insights Imaging. 5(4):473-82, 2014
- Zaveri J et al: More than just Langerhans cell histiocytosis: a radiologic review of histiocytic disorders. Radiographics. 34(7):2008-24, 2014
- Mazor RD et al: Erdheim-Chester Disease: a comprehensive review of the literature. Orphanet J Rare Dis. 8:137, 2013
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
TERMINOLOGY
Abbreviations
- Pulmonary Langerhans cell histiocytosis (PLCH)
- Langerhans cell histiocytosis (LCH)
- Erdheim-Chester disease (ECD)
- Rosai-Dorfman disease (RDD)
- Pulmonary Langerhans cell histiocytosis (PLCH)
Synonyms
- RDD: Sinus histiocytosis with massive lymphadenopathy
Definitions
- Rare disorders characterized by accumulation of macrophages, dendritic cells, or monocyte-derived cells in various tissues and organs
- PLCH: Isolated form of LCH occurring in smokers characterized by granulomatous infiltration of distal bronchial walls with cells derived from myeloid dendritic cells (i.e., Langerhans cells)
- ECD: Non-LCH dendritic cell disorder characterized by xanthomatous infiltration of involved tissues by foamy histiocytes
- RDD: Nonmalignant proliferation of histiocytic &/or phagocytic cells
IMAGING
Radiographic Findings
CT Findings
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Vargas D et al: Cardiothoracic manifestations of primary histiocytoses. Br J Radiol. 89(1068):20160347, 2016
- Ahuja J et al: Histiocytic disorders of the chest: imaging findings. Radiographics. 35(2):357-70, 2015
- Antunes C et al: Thoracic, abdominal and musculoskeletal involvement in Erdheim-Chester disease: CT, MR and PET imaging findings. Insights Imaging. 5(4):473-82, 2014
- Zaveri J et al: More than just Langerhans cell histiocytosis: a radiologic review of histiocytic disorders. Radiographics. 34(7):2008-24, 2014
- Mazor RD et al: Erdheim-Chester Disease: a comprehensive review of the literature. Orphanet J Rare Dis. 8:137, 2013
