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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Fibrotic bronchiolitis
Obliterative bronchiolitis
Bronchiolitis obliterans
Definitions
Idiopathic constrictive bronchiolitis
Nonspecific, irreversible process
Concentric fibrosis anatomically located between bronchiolar epithelium and muscularis mucosa
Affects terminal and respiratory bronchioles with resultant bronchiolar luminal narrowing &/or obliteration
Little bronchiolar/peribronchiolar chronic inflammation, absence of granulation tissue polyps
Diagnosis of exclusion: Exclusion of known causes of constrictive bronchiolitis
Constrictive bronchiolitis is not to be confused with bronchiolitis obliterans organizing pneumonia, preferably referred to as organizing pneumonia or as cryptogenic organizing pneumonia if idiopathic
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Reporting Tips
Selected References
Berniker AV et al: Imaging of small airways diseases. Radiol Clin North Am. 54(6):1165-1181, 2016
Edwards RM et al: Imaging of small airways and emphysema. Clin Chest Med. 36(2):335-47, x, 2015
Kligerman SJ et al: Mosaic attenuation: etiology, methods of differentiation, and pitfalls. Radiographics. 35(5):1360-80, 2015
Allen TC: Small Airways disease. Surg Pathol Clin. 3(1):171-86, 2010
Lynch DA: Imaging of small airways disease and chronic obstructive pulmonary disease. Clin Chest Med. 29(1):165-79, vii, 2008
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Fibrotic bronchiolitis
Obliterative bronchiolitis
Bronchiolitis obliterans
Definitions
Idiopathic constrictive bronchiolitis
Nonspecific, irreversible process
Concentric fibrosis anatomically located between bronchiolar epithelium and muscularis mucosa
Affects terminal and respiratory bronchioles with resultant bronchiolar luminal narrowing &/or obliteration
Little bronchiolar/peribronchiolar chronic inflammation, absence of granulation tissue polyps
Diagnosis of exclusion: Exclusion of known causes of constrictive bronchiolitis
Constrictive bronchiolitis is not to be confused with bronchiolitis obliterans organizing pneumonia, preferably referred to as organizing pneumonia or as cryptogenic organizing pneumonia if idiopathic
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Reporting Tips
Selected References
Berniker AV et al: Imaging of small airways diseases. Radiol Clin North Am. 54(6):1165-1181, 2016
Edwards RM et al: Imaging of small airways and emphysema. Clin Chest Med. 36(2):335-47, x, 2015
Kligerman SJ et al: Mosaic attenuation: etiology, methods of differentiation, and pitfalls. Radiographics. 35(5):1360-80, 2015
Allen TC: Small Airways disease. Surg Pathol Clin. 3(1):171-86, 2010
Lynch DA: Imaging of small airways disease and chronic obstructive pulmonary disease. Clin Chest Med. 29(1):165-79, vii, 2008
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