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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Idiopathic pulmonary fibrosis (IPF)
Synonyms
Idiopathic usual interstitial pneumonia (UIP)
Cryptogenic fibrosing alveolitis
Definitions
Fibrosing idiopathic interstitial pneumonia associated with histologic pattern of UIP on surgical biopsy
Represents 40% of all idiopathic interstitial pneumonias
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Travis WD et al: An official American Thoracic Society/European Respiratory Society statement: update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med. 188(6):733-48, 2013
Raghu G et al: An official ATS/ERS/JRS/ALAT statement: idiopathic pulmonary fibrosis: evidence-based guidelines for diagnosis and management. Am J Respir Crit Care Med. 183(6):788-824, 2011
Mueller-Mang C et al: What every radiologist should know about idiopathic interstitial pneumonias. Radiographics. 27(3):595-615, 2007
Lynch DA et al: High-resolution computed tomography in idiopathic pulmonary fibrosis: diagnosis and prognosis. Am J Respir Crit Care Med. 172(4):488-93, 2005
Lynch DA: Idiopathic interstitial pneumonias: CT features. Radiology. 236(1):10-21, 2005
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Idiopathic pulmonary fibrosis (IPF)
Synonyms
Idiopathic usual interstitial pneumonia (UIP)
Cryptogenic fibrosing alveolitis
Definitions
Fibrosing idiopathic interstitial pneumonia associated with histologic pattern of UIP on surgical biopsy
Represents 40% of all idiopathic interstitial pneumonias
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Travis WD et al: An official American Thoracic Society/European Respiratory Society statement: update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med. 188(6):733-48, 2013
Raghu G et al: An official ATS/ERS/JRS/ALAT statement: idiopathic pulmonary fibrosis: evidence-based guidelines for diagnosis and management. Am J Respir Crit Care Med. 183(6):788-824, 2011
Mueller-Mang C et al: What every radiologist should know about idiopathic interstitial pneumonias. Radiographics. 27(3):595-615, 2007
Lynch DA et al: High-resolution computed tomography in idiopathic pulmonary fibrosis: diagnosis and prognosis. Am J Respir Crit Care Med. 172(4):488-93, 2005
Lynch DA: Idiopathic interstitial pneumonias: CT features. Radiology. 236(1):10-21, 2005
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