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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- IgG4-related disease (IgG4-RD)
Synonyms
- Organ-specific conditions now related to IgG4
- Mikulicz disease (lacrimal, parotid, submandibular glands)
- Autoimmune pancreatitis (AIP)
- Ormond disease (retroperitoneal fibrosis)
- IgG4-related ophthalmic disease
- "Idiopathic" pseudotumor (generic)
- Organ-specific conditions now related to IgG4
Definitions
- Chronic fibroinflammatory disease characterized by IgG4(+) plasma cell infiltrates
IMAGING
General Features
CT Findings
MR Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross, Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Peng L et al: Clinical features of immunoglobulin G4-related disease with central nervous system involvement: an analysis of 15 cases. Clin Exp Rheumatol. ePub, 2020
- Satou A et al: Clinicopathological differential diagnosis of IgG4-related disease: a historical overview and a proposal of the criteria for excluding mimickers of IgG4-related disease. Pathol Int. ePub, 2020
- Vakrakou AG et al: Recurrent myelitis and asymptomatic hypophysitis in IgG4-related disease: case-based review. Rheumatol Int. 40(2):337-43, 2020
- Goulam-Houssein S et al: IgG4-related intracranial disease. Neuroradiol J. 32(1):29-35, 2019
- Kuroda N et al: Intracranial multiple pseudotumor due to immunoglobulin G4-related disease without other lesions: case report and literature review. World Neurosurg. 132:69-74, 2019
- Ryu G et al: Clinical significance of IgG4 in sinonasal and skull base inflammatory pseudotumor. Eur Arch Otorhinolaryngol. ePub, 2019
- AbdelRazek MA et al: IgG4-related disease of the central and peripheral nervous systems. Lancet Neurol. 17(2):183-92, 2018
- Tanji H et al: Inflammatory Pseudotumor of the Brain Parenchyma with IgG4 Hypergammaglobulinemia. Intern Med. 55(14):1911-6, 2016
- Deshpande V: IgG4 related disease of the head and neck. Head Neck Pathol. 9(1):24-31, 2015
- Okano A et al: Intracranial Inflammatory Pseudotumors Associated with Immunoglobulin G4-Related Disease Mimicking Multiple Meningiomas: A Case Report and Review of the Literature. World Neurosurg. 83(6):1181.e1-4, 2015
- Fujita A et al: IgG4-related disease of the head and neck: CT and MR imaging manifestations. Radiographics. 32(7):1945-58, 2012
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- IgG4-related disease (IgG4-RD)
Synonyms
- Organ-specific conditions now related to IgG4
- Mikulicz disease (lacrimal, parotid, submandibular glands)
- Autoimmune pancreatitis (AIP)
- Ormond disease (retroperitoneal fibrosis)
- IgG4-related ophthalmic disease
- "Idiopathic" pseudotumor (generic)
- Organ-specific conditions now related to IgG4
Definitions
- Chronic fibroinflammatory disease characterized by IgG4(+) plasma cell infiltrates
IMAGING
General Features
CT Findings
MR Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross, Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
- Peng L et al: Clinical features of immunoglobulin G4-related disease with central nervous system involvement: an analysis of 15 cases. Clin Exp Rheumatol. ePub, 2020
- Satou A et al: Clinicopathological differential diagnosis of IgG4-related disease: a historical overview and a proposal of the criteria for excluding mimickers of IgG4-related disease. Pathol Int. ePub, 2020
- Vakrakou AG et al: Recurrent myelitis and asymptomatic hypophysitis in IgG4-related disease: case-based review. Rheumatol Int. 40(2):337-43, 2020
- Goulam-Houssein S et al: IgG4-related intracranial disease. Neuroradiol J. 32(1):29-35, 2019
- Kuroda N et al: Intracranial multiple pseudotumor due to immunoglobulin G4-related disease without other lesions: case report and literature review. World Neurosurg. 132:69-74, 2019
- Ryu G et al: Clinical significance of IgG4 in sinonasal and skull base inflammatory pseudotumor. Eur Arch Otorhinolaryngol. ePub, 2019
- AbdelRazek MA et al: IgG4-related disease of the central and peripheral nervous systems. Lancet Neurol. 17(2):183-92, 2018
- Tanji H et al: Inflammatory Pseudotumor of the Brain Parenchyma with IgG4 Hypergammaglobulinemia. Intern Med. 55(14):1911-6, 2016
- Deshpande V: IgG4 related disease of the head and neck. Head Neck Pathol. 9(1):24-31, 2015
- Okano A et al: Intracranial Inflammatory Pseudotumors Associated with Immunoglobulin G4-Related Disease Mimicking Multiple Meningiomas: A Case Report and Review of the Literature. World Neurosurg. 83(6):1181.e1-4, 2015
- Fujita A et al: IgG4-related disease of the head and neck: CT and MR imaging manifestations. Radiographics. 32(7):1945-58, 2012
