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KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
- Congenital fibrosarcoma, desmoplastic fibrosarcoma of infancy, congenital infantile fibrosarcoma, juvenile fibrosarcoma, medullary fibromatosis of infancy, aggressive infantile fibromatosis, congenital fibrosarcoma-like fibromatosis, medullary fibromatosis of infancy
Definitions
- Rare, malignant neoplasm of infancy histologically similar to adult fibrosarcoma but with different molecular alterations and more favorable clinical course
IMAGING
General Features
Imaging Recommendations
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Suzuki T et al: Sonographic features of congenital infantile fibrosarcoma that appeared as a sacrococcygeal teratoma during pregnancy. J Obstet Gynaecol Res. 41(8):1282-6, 2015
- Ainsworth KE et al: Congenital infantile fibrosarcoma: review of imaging features. Pediatr Radiol. 44(9):1124-9, 2014
- Farmakis SG et al: Congenital infantile fibrosarcoma. J Perinatol. 34(4):329-30, 2014
- Hu Z et al: Infantile fibrosarcoma-a clinical and histologic mimicker of vascular malformations: case report and review of the literature. Pediatr Dev Pathol. 16(5):357-63, 2013
- Kerl K et al: Infantile fibrosarcoma - an important differential diagnosis of congenital vascular tumors. Pediatr Hematol Oncol. 29(6):545-8, 2012
- Weiss SW et al: Fibrous tumors of infancy and childhood. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Philadelphia: Elsevier. 279-84, 2008
- Kransdorf MJ et al: Malignant fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 2nd ed. Philadelphia: Lippincott Williams & Wilkins. 268-71, 2006
- Coffin CM et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon: IARC Press. 98-100, 2002
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
- Congenital fibrosarcoma, desmoplastic fibrosarcoma of infancy, congenital infantile fibrosarcoma, juvenile fibrosarcoma, medullary fibromatosis of infancy, aggressive infantile fibromatosis, congenital fibrosarcoma-like fibromatosis, medullary fibromatosis of infancy
Definitions
- Rare, malignant neoplasm of infancy histologically similar to adult fibrosarcoma but with different molecular alterations and more favorable clinical course
IMAGING
General Features
Imaging Recommendations
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Suzuki T et al: Sonographic features of congenital infantile fibrosarcoma that appeared as a sacrococcygeal teratoma during pregnancy. J Obstet Gynaecol Res. 41(8):1282-6, 2015
- Ainsworth KE et al: Congenital infantile fibrosarcoma: review of imaging features. Pediatr Radiol. 44(9):1124-9, 2014
- Farmakis SG et al: Congenital infantile fibrosarcoma. J Perinatol. 34(4):329-30, 2014
- Hu Z et al: Infantile fibrosarcoma-a clinical and histologic mimicker of vascular malformations: case report and review of the literature. Pediatr Dev Pathol. 16(5):357-63, 2013
- Kerl K et al: Infantile fibrosarcoma - an important differential diagnosis of congenital vascular tumors. Pediatr Hematol Oncol. 29(6):545-8, 2012
- Weiss SW et al: Fibrous tumors of infancy and childhood. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Philadelphia: Elsevier. 279-84, 2008
- Kransdorf MJ et al: Malignant fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 2nd ed. Philadelphia: Lippincott Williams & Wilkins. 268-71, 2006
- Coffin CM et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon: IARC Press. 98-100, 2002
