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Infantile Fibrosarcoma
Catherine C. Roberts, MD
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KEY FACTS

  • Terminology

    • Imaging

      • Pathology

        • Clinical Issues

          TERMINOLOGY

          • Synonyms

            • Congenital fibrosarcoma, desmoplastic fibrosarcoma of infancy, congenital infantile fibrosarcoma, juvenile fibrosarcoma, medullary fibromatosis of infancy, aggressive infantile fibromatosis, congenital fibrosarcoma-like fibromatosis, medullary fibromatosis of infancy
          • Definitions

            • Rare, malignant neoplasm of infancy histologically similar to adult fibrosarcoma but with different molecular alterations and more favorable clinical course

          IMAGING

          • General Features

            • Imaging Recommendations

              • Radiographic Findings

                • CT Findings

                  • MR Findings

                    • Ultrasonographic Findings

                      • Angiographic Findings

                        DIFFERENTIAL DIAGNOSIS

                          PATHOLOGY

                          • General Features

                            • Gross Pathologic & Surgical Features

                              • Microscopic Features

                                CLINICAL ISSUES

                                • Presentation

                                  • Demographics

                                    • Natural History & Prognosis

                                      • Treatment

                                        Selected References

                                        1. Suzuki T et al: Sonographic features of congenital infantile fibrosarcoma that appeared as a sacrococcygeal teratoma during pregnancy. J Obstet Gynaecol Res. 41(8):1282-6, 2015
                                        2. Ainsworth KE et al: Congenital infantile fibrosarcoma: review of imaging features. Pediatr Radiol. 44(9):1124-9, 2014
                                        3. Farmakis SG et al: Congenital infantile fibrosarcoma. J Perinatol. 34(4):329-30, 2014
                                        4. Hu Z et al: Infantile fibrosarcoma-a clinical and histologic mimicker of vascular malformations: case report and review of the literature. Pediatr Dev Pathol. 16(5):357-63, 2013
                                        5. Kerl K et al: Infantile fibrosarcoma - an important differential diagnosis of congenital vascular tumors. Pediatr Hematol Oncol. 29(6):545-8, 2012
                                        6. Weiss SW et al: Fibrous tumors of infancy and childhood. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Philadelphia: Elsevier. 279-84, 2008
                                        7. Kransdorf MJ et al: Malignant fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 2nd ed. Philadelphia: Lippincott Williams & Wilkins. 268-71, 2006
                                        8. Coffin CM et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon: IARC Press. 98-100, 2002
                                        Related Anatomy
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                                        Related Differential Diagnoses
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                                        References
                                        Tables

                                        Tables

                                        KEY FACTS

                                        • Terminology

                                          • Imaging

                                            • Pathology

                                              • Clinical Issues

                                                TERMINOLOGY

                                                • Synonyms

                                                  • Congenital fibrosarcoma, desmoplastic fibrosarcoma of infancy, congenital infantile fibrosarcoma, juvenile fibrosarcoma, medullary fibromatosis of infancy, aggressive infantile fibromatosis, congenital fibrosarcoma-like fibromatosis, medullary fibromatosis of infancy
                                                • Definitions

                                                  • Rare, malignant neoplasm of infancy histologically similar to adult fibrosarcoma but with different molecular alterations and more favorable clinical course

                                                IMAGING

                                                • General Features

                                                  • Imaging Recommendations

                                                    • Radiographic Findings

                                                      • CT Findings

                                                        • MR Findings

                                                          • Ultrasonographic Findings

                                                            • Angiographic Findings

                                                              DIFFERENTIAL DIAGNOSIS

                                                                PATHOLOGY

                                                                • General Features

                                                                  • Gross Pathologic & Surgical Features

                                                                    • Microscopic Features

                                                                      CLINICAL ISSUES

                                                                      • Presentation

                                                                        • Demographics

                                                                          • Natural History & Prognosis

                                                                            • Treatment

                                                                              Selected References

                                                                              1. Suzuki T et al: Sonographic features of congenital infantile fibrosarcoma that appeared as a sacrococcygeal teratoma during pregnancy. J Obstet Gynaecol Res. 41(8):1282-6, 2015
                                                                              2. Ainsworth KE et al: Congenital infantile fibrosarcoma: review of imaging features. Pediatr Radiol. 44(9):1124-9, 2014
                                                                              3. Farmakis SG et al: Congenital infantile fibrosarcoma. J Perinatol. 34(4):329-30, 2014
                                                                              4. Hu Z et al: Infantile fibrosarcoma-a clinical and histologic mimicker of vascular malformations: case report and review of the literature. Pediatr Dev Pathol. 16(5):357-63, 2013
                                                                              5. Kerl K et al: Infantile fibrosarcoma - an important differential diagnosis of congenital vascular tumors. Pediatr Hematol Oncol. 29(6):545-8, 2012
                                                                              6. Weiss SW et al: Fibrous tumors of infancy and childhood. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Philadelphia: Elsevier. 279-84, 2008
                                                                              7. Kransdorf MJ et al: Malignant fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 2nd ed. Philadelphia: Lippincott Williams & Wilkins. 268-71, 2006
                                                                              8. Coffin CM et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon: IARC Press. 98-100, 2002