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Infantile Fibrosarcoma
Eric Walker, MD, MHA, FACR, FACHE; Catherine C. Roberts, MD
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KEY FACTS

  • Terminology

    • Imaging

      • Pathology

        • Clinical Issues

          TERMINOLOGY

          • Synonyms

            • Congenital fibrosarcoma, infantile fibrosarcoma-like tumor, cellular congenital mesoblastic nephroma, desmoplastic fibrosarcoma of infancy, congenital infantile fibrosarcoma, juvenile fibrosarcoma, medullary fibromatosis of infancy, aggressive infantile fibromatosis, congenital fibrosarcoma-like fibromatosis, medullary fibromatosis of infancy
          • Definitions

            • Malignant fibroblastic tumor most commonly occurring in infancy

          IMAGING

          • General Features

            • Radiographic Findings

              • CT Findings

                • MR Findings

                  • Ultrasonographic Findings

                    • Angiographic Findings

                      • Nuclear Medicine Findings

                        • Imaging Recommendations

                          DIFFERENTIAL DIAGNOSIS

                            PATHOLOGY

                            • General Features

                              • Gross Pathologic & Surgical Features

                                • Microscopic Features

                                  CLINICAL ISSUES

                                  • Presentation

                                    • Demographics

                                      • Natural History & Prognosis

                                        • Treatment

                                          Selected References

                                          1. Rashid T et al: Advances in the diagnosis and management of neonatal sarcomas. Clin Perinatol. 48(1):117-45, 2021
                                          2. Siozopoulou V et al: NTRK fusions in sarcomas: diagnostic challenges and clinical aspects. Diagnostics (Basel). 11(3):478, 2021
                                          3. Davis JL et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours: Soft Tissue and Bone Tumours. 5th ed. IARC Press. 119-21, 2020
                                          4. Suzuki T et al: Sonographic features of congenital infantile fibrosarcoma that appeared as a sacrococcygeal teratoma during pregnancy. J Obstet Gynaecol Res. 41(8):1282-6, 2015
                                          5. Ainsworth KE et al: Congenital infantile fibrosarcoma: review of imaging features. Pediatr Radiol. 44(9):1124-9, 2014
                                          6. Farmakis SG et al: Congenital infantile fibrosarcoma. J Perinatol. 34(4):329-30, 2014
                                          7. Kransdorf MJ et al: Fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 3rd ed. Lippincott Williams & Wilkins. 316-22, 2014
                                          8. Hu Z et al: Infantile fibrosarcoma-a clinical and histologic mimicker of vascular malformations: case report and review of the literature. Pediatr Dev Pathol. 16(5):357-63, 2013
                                          9. Kerl K et al: Infantile fibrosarcoma - an important differential diagnosis of congenital vascular tumors. Pediatr Hematol Oncol. 29(6):545-8, 2012
                                          10. Weiss SW et al: Fibrous tumors of infancy and childhood. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Elsevier. 279-84, 2008
                                          11. Coffin CM et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. IARC Press. 98-100, 2002
                                          Related Anatomy
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                                          Related Differential Diagnoses
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                                          References
                                          Tables

                                          Tables

                                          KEY FACTS

                                          • Terminology

                                            • Imaging

                                              • Pathology

                                                • Clinical Issues

                                                  TERMINOLOGY

                                                  • Synonyms

                                                    • Congenital fibrosarcoma, infantile fibrosarcoma-like tumor, cellular congenital mesoblastic nephroma, desmoplastic fibrosarcoma of infancy, congenital infantile fibrosarcoma, juvenile fibrosarcoma, medullary fibromatosis of infancy, aggressive infantile fibromatosis, congenital fibrosarcoma-like fibromatosis, medullary fibromatosis of infancy
                                                  • Definitions

                                                    • Malignant fibroblastic tumor most commonly occurring in infancy

                                                  IMAGING

                                                  • General Features

                                                    • Radiographic Findings

                                                      • CT Findings

                                                        • MR Findings

                                                          • Ultrasonographic Findings

                                                            • Angiographic Findings

                                                              • Nuclear Medicine Findings

                                                                • Imaging Recommendations

                                                                  DIFFERENTIAL DIAGNOSIS

                                                                    PATHOLOGY

                                                                    • General Features

                                                                      • Gross Pathologic & Surgical Features

                                                                        • Microscopic Features

                                                                          CLINICAL ISSUES

                                                                          • Presentation

                                                                            • Demographics

                                                                              • Natural History & Prognosis

                                                                                • Treatment

                                                                                  Selected References

                                                                                  1. Rashid T et al: Advances in the diagnosis and management of neonatal sarcomas. Clin Perinatol. 48(1):117-45, 2021
                                                                                  2. Siozopoulou V et al: NTRK fusions in sarcomas: diagnostic challenges and clinical aspects. Diagnostics (Basel). 11(3):478, 2021
                                                                                  3. Davis JL et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours: Soft Tissue and Bone Tumours. 5th ed. IARC Press. 119-21, 2020
                                                                                  4. Suzuki T et al: Sonographic features of congenital infantile fibrosarcoma that appeared as a sacrococcygeal teratoma during pregnancy. J Obstet Gynaecol Res. 41(8):1282-6, 2015
                                                                                  5. Ainsworth KE et al: Congenital infantile fibrosarcoma: review of imaging features. Pediatr Radiol. 44(9):1124-9, 2014
                                                                                  6. Farmakis SG et al: Congenital infantile fibrosarcoma. J Perinatol. 34(4):329-30, 2014
                                                                                  7. Kransdorf MJ et al: Fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 3rd ed. Lippincott Williams & Wilkins. 316-22, 2014
                                                                                  8. Hu Z et al: Infantile fibrosarcoma-a clinical and histologic mimicker of vascular malformations: case report and review of the literature. Pediatr Dev Pathol. 16(5):357-63, 2013
                                                                                  9. Kerl K et al: Infantile fibrosarcoma - an important differential diagnosis of congenital vascular tumors. Pediatr Hematol Oncol. 29(6):545-8, 2012
                                                                                  10. Weiss SW et al: Fibrous tumors of infancy and childhood. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Elsevier. 279-84, 2008
                                                                                  11. Coffin CM et al: Infantile fibrosarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. IARC Press. 98-100, 2002