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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Interhemispheric cyst (IHC)
- Asymmetric ventriculomegaly with IHC and dysgenesis of corpus callosum (AVID)
Synonyms
- Ependymal cyst
- Neuroepithelial cyst
- Glioependymal cyst
Definitions
- Intracranial cyst centered near midline/interhemispheric fissure
- Type 1 cyst: Communicates with ventricular system
- Type 1a (most common) associated with hydrocephalus
- Types 1b, 1c have additional anomalies
- Type 2 cyst: Intraparenchymal
IMAGING
General Features
Ultrasonographic Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Oh KY et al: Clinical outcomes following prenatal diagnosis of asymmetric ventriculomegaly, interhemispheric cyst, and callosal dysgenesis (AVID). Prenat Diagn. 39(1):26-32, 2019
- Uccella S et al: Dissecting the neurological phenotype in children with callosal agenesis, interhemispheric cysts and malformations of cortical development. J Neurol. 266(5):1167-81, 2019
- Revanna KG et al: Agenesis of the corpus callosum with interhemispheric cyst: clinical implications and outcome. BMJ Case Rep. 11(1), 2018
- Edwards TJ et al: Clinical, genetic and imaging findings identify new causes for corpus callosum development syndromes. Brain. 137(Pt 6):1579-613, 2014
- Cagneaux M et al: Agenesis of the corpus callosum with interhemispheric cyst, associated with aberrant cortical sulci and without underlying cortical dysplasia. Ultrasound Obstet Gynecol. 42(5):603-5, 2013
- Paladini D et al: Agenesis of the fetal corpus callosum: sonographic signs change with advancing gestational age. Ultrasound Obstet Gynecol. 42(6):687-90, 2013
- Oh KY et al: Asymmetric ventriculomegaly, interhemispheric cyst, and dysgenesis of the corpus callosum (AVID): an imaging triad. J Ultrasound Med. 31(11):1811-20, 2012
- Winter TC et al: The cavum septi pellucidi: why is it important? J Ultrasound Med. 29(3):427-44, 2010
- Wong SK et al: Supratentorial abnormalities in the Chiari II malformation, III: the interhemispheric cyst. J Ultrasound Med. 28(8):999-1006, 2009
- Moriyama E et al: Interhemispheric multiloculated ependymal cyst with dysgenesis of the corpus callosum: a case in a preterm fetus. Childs Nerv Syst. 23(7):807-13, 2007
- Mühler MR et al: Fetal MRI demonstrates glioependymal cyst in a case of sonographic unilateral ventriculomegaly. Pediatr Radiol. 37(4):391-5, 2007
- Utsunomiya H et al: Midline cystic malformations of the brain: imaging diagnosis and classification based on embryologic analysis. Radiat Med. 24(6):471-81, 2006
- Pavone P et al: Callosal anomalies with interhemispheric cyst: expanding the phenotype. Acta Paediatr. 94(8):1066-72, 2005
- Barkovich AJ et al: Callosal agenesis with cyst: a better understanding and new classification. Neurology. 56(2):220-7, 2001
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Interhemispheric cyst (IHC)
- Asymmetric ventriculomegaly with IHC and dysgenesis of corpus callosum (AVID)
Synonyms
- Ependymal cyst
- Neuroepithelial cyst
- Glioependymal cyst
Definitions
- Intracranial cyst centered near midline/interhemispheric fissure
- Type 1 cyst: Communicates with ventricular system
- Type 1a (most common) associated with hydrocephalus
- Types 1b, 1c have additional anomalies
- Type 2 cyst: Intraparenchymal
IMAGING
General Features
Ultrasonographic Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Oh KY et al: Clinical outcomes following prenatal diagnosis of asymmetric ventriculomegaly, interhemispheric cyst, and callosal dysgenesis (AVID). Prenat Diagn. 39(1):26-32, 2019
- Uccella S et al: Dissecting the neurological phenotype in children with callosal agenesis, interhemispheric cysts and malformations of cortical development. J Neurol. 266(5):1167-81, 2019
- Revanna KG et al: Agenesis of the corpus callosum with interhemispheric cyst: clinical implications and outcome. BMJ Case Rep. 11(1), 2018
- Edwards TJ et al: Clinical, genetic and imaging findings identify new causes for corpus callosum development syndromes. Brain. 137(Pt 6):1579-613, 2014
- Cagneaux M et al: Agenesis of the corpus callosum with interhemispheric cyst, associated with aberrant cortical sulci and without underlying cortical dysplasia. Ultrasound Obstet Gynecol. 42(5):603-5, 2013
- Paladini D et al: Agenesis of the fetal corpus callosum: sonographic signs change with advancing gestational age. Ultrasound Obstet Gynecol. 42(6):687-90, 2013
- Oh KY et al: Asymmetric ventriculomegaly, interhemispheric cyst, and dysgenesis of the corpus callosum (AVID): an imaging triad. J Ultrasound Med. 31(11):1811-20, 2012
- Winter TC et al: The cavum septi pellucidi: why is it important? J Ultrasound Med. 29(3):427-44, 2010
- Wong SK et al: Supratentorial abnormalities in the Chiari II malformation, III: the interhemispheric cyst. J Ultrasound Med. 28(8):999-1006, 2009
- Moriyama E et al: Interhemispheric multiloculated ependymal cyst with dysgenesis of the corpus callosum: a case in a preterm fetus. Childs Nerv Syst. 23(7):807-13, 2007
- Mühler MR et al: Fetal MRI demonstrates glioependymal cyst in a case of sonographic unilateral ventriculomegaly. Pediatr Radiol. 37(4):391-5, 2007
- Utsunomiya H et al: Midline cystic malformations of the brain: imaging diagnosis and classification based on embryologic analysis. Radiat Med. 24(6):471-81, 2006
- Pavone P et al: Callosal anomalies with interhemispheric cyst: expanding the phenotype. Acta Paediatr. 94(8):1066-72, 2005
- Barkovich AJ et al: Callosal agenesis with cyst: a better understanding and new classification. Neurology. 56(2):220-7, 2001
