Complete luminal and anatomical wall discontinuity between ascending aorta and descending aorta
Not true interruption, as there is fibrotic continuity between blind ends
HAA
Tubular narrowing of aortic arch without luminal discontinuity
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
LaPar DJ et al: Surgical considerations in interrupted aortic arch. Semin Cardiothorac Vasc Anesth. 22(3):278-84, 2018
Hanneman K et al: Congenital variants and anomalies of the aortic arch. Radiographics. 37(1):32-51, 2017
Goudar SP et al: Echocardiography of coarctation of the aorta, aortic arch hypoplasia, and arch interruption: strategies for evaluation of the aortic arch. Cardiol Young. 26(8):1553-1562, 2016
Frank L et al: Cardiovascular MR imaging of conotruncal anomalies. Radiographics. 30(4):1069-94, 2010
Kimura-Hayama ET et al: Uncommon congenital and acquired aortic diseases: role of multidetector CT angiography. Radiographics. 30(1):79-98, 2010
Dillman JR et al: Interrupted aortic arch: spectrum of MRI findings. AJR Am J Roentgenol. 190(6):1467-74, 2008
Yang DH et al: Multislice CT angiography of interrupted aortic arch. Pediatr Radiol. 38(1):89-100, 2008
Loffredo CA et al: Interrupted aortic arch: an epidemiologic study. Teratology. 61(5):368-75, 2000
Kaulitz R et al: Echocardiographic assessment of interrupted aortic arch. Cardiol Young. 9(6):562-71, 1999
Reardon MJ et al: Interrupted aortic arch: brief review and summary of an eighteen-year experience. Tex Heart Inst J. 11(3):250-9, 1984
CELORIA GC et al: Congenital absence of the aortic arch. Am Heart J. 58:407-13, 1959
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Interrupted aortic arch (IAA)
Hypoplastic aortic arch (HAA)
Synonyms
Atresia of aortic arch
Definitions
IAA
Complete luminal and anatomical wall discontinuity between ascending aorta and descending aorta
Not true interruption, as there is fibrotic continuity between blind ends
HAA
Tubular narrowing of aortic arch without luminal discontinuity
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
LaPar DJ et al: Surgical considerations in interrupted aortic arch. Semin Cardiothorac Vasc Anesth. 22(3):278-84, 2018
Hanneman K et al: Congenital variants and anomalies of the aortic arch. Radiographics. 37(1):32-51, 2017
Goudar SP et al: Echocardiography of coarctation of the aorta, aortic arch hypoplasia, and arch interruption: strategies for evaluation of the aortic arch. Cardiol Young. 26(8):1553-1562, 2016
Frank L et al: Cardiovascular MR imaging of conotruncal anomalies. Radiographics. 30(4):1069-94, 2010
Kimura-Hayama ET et al: Uncommon congenital and acquired aortic diseases: role of multidetector CT angiography. Radiographics. 30(1):79-98, 2010
Dillman JR et al: Interrupted aortic arch: spectrum of MRI findings. AJR Am J Roentgenol. 190(6):1467-74, 2008
Yang DH et al: Multislice CT angiography of interrupted aortic arch. Pediatr Radiol. 38(1):89-100, 2008
Loffredo CA et al: Interrupted aortic arch: an epidemiologic study. Teratology. 61(5):368-75, 2000
Kaulitz R et al: Echocardiographic assessment of interrupted aortic arch. Cardiol Young. 9(6):562-71, 1999
Reardon MJ et al: Interrupted aortic arch: brief review and summary of an eighteen-year experience. Tex Heart Inst J. 11(3):250-9, 1984
CELORIA GC et al: Congenital absence of the aortic arch. Am Heart J. 58:407-13, 1959
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