link
Bookmarks
Kaposiform Lymphangiomatosis
A. Carlson Merrow, Jr., MD, FAAP
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Log inSubscribe
0
0
3
0

KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Pathology

          • Clinical Issues

            TERMINOLOGY

            • Abbreviations

              • Kaposiform lymphangiomatosis (KLA)
            • Definitions

              • Uncommon but distinct subtype of generalized lymphatic anomaly (GLA) with poor prognosis
                • Features of both neoplasia and malformation
              • Predominantly affects thorax with progressive respiratory symptoms and hemorrhages

            IMAGING

            • General Features

              DIFFERENTIAL DIAGNOSIS

                PATHOLOGY

                • Microscopic Features

                  CLINICAL ISSUES

                  • Presentation

                    • Demographics

                      • Natural History & Prognosis

                        • Treatment

                          Selected References

                          1. Fernandes VM et al: Kaposiform lymphangiomatosis: unifying features of a heterogeneous disorder. Pediatr Blood Cancer. 62(5):901-4, 2015
                          2. Wang Z et al: Successful treatment of kaposiform lymphangiomatosis with sirolimus. Pediatr Blood Cancer. 62(7):1291-3, 2015
                          3. Croteau SE et al: Kaposiform lymphangiomatosis: a distinct aggressive lymphatic anomaly. J Pediatr. 164(2):383-8, 2014
                          4. Safi F et al: Kaposiform lymphangiomatosis, a newly characterized vascular anomaly presenting with hemoptysis in an adult woman. Ann Am Thorac Soc. 11(1):92-5, 2014
                          5. Trenor CC 3rd et al: Complex lymphatic anomalies. Semin Pediatr Surg. 23(4):186-90, 2014
                          Related Anatomy
                          Loading...
                          Related Differential Diagnoses
                          Loading...
                          References
                          Tables

                          Tables

                          KEY FACTS

                          • Terminology

                            • Imaging

                              • Top Differential Diagnoses

                                • Pathology

                                  • Clinical Issues

                                    TERMINOLOGY

                                    • Abbreviations

                                      • Kaposiform lymphangiomatosis (KLA)
                                    • Definitions

                                      • Uncommon but distinct subtype of generalized lymphatic anomaly (GLA) with poor prognosis
                                        • Features of both neoplasia and malformation
                                      • Predominantly affects thorax with progressive respiratory symptoms and hemorrhages

                                    IMAGING

                                    • General Features

                                      DIFFERENTIAL DIAGNOSIS

                                        PATHOLOGY

                                        • Microscopic Features

                                          CLINICAL ISSUES

                                          • Presentation

                                            • Demographics

                                              • Natural History & Prognosis

                                                • Treatment

                                                  Selected References

                                                  1. Fernandes VM et al: Kaposiform lymphangiomatosis: unifying features of a heterogeneous disorder. Pediatr Blood Cancer. 62(5):901-4, 2015
                                                  2. Wang Z et al: Successful treatment of kaposiform lymphangiomatosis with sirolimus. Pediatr Blood Cancer. 62(7):1291-3, 2015
                                                  3. Croteau SE et al: Kaposiform lymphangiomatosis: a distinct aggressive lymphatic anomaly. J Pediatr. 164(2):383-8, 2014
                                                  4. Safi F et al: Kaposiform lymphangiomatosis, a newly characterized vascular anomaly presenting with hemoptysis in an adult woman. Ann Am Thorac Soc. 11(1):92-5, 2014
                                                  5. Trenor CC 3rd et al: Complex lymphatic anomalies. Semin Pediatr Surg. 23(4):186-90, 2014