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KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
- "Congenitally corrected transposition" (misnomer)
- Discordant transposition
Definitions
- Inversion of ventricles & great arteries: Atrioventricular (AV) discordance & ventriculoarterial discordance
- Category: Dependent on associated anomalies
- Ventricular septal defect (VSD) (60-80%): Acyanotic, ↑ pulmonary vascularity
- Left ventricular outflow tract (subpulmonary) obstruction (30-50%): Cyanotic
- Dysplasia (Ebstein anomaly) with regurgitation of left-sided AV valve: Pulmonary venous congestion/hypertension
- Conduction abnormalities, heart block
- Only 1% have no associated anomalies: True congenitally corrected transposition
- Hemodynamics
- Right atrium connects via mitral valve to right-sided morphologic left ventricle (LV), which connects to pulmonary circulation
- Left atrium connects via tricuspid valve to left-sided morphologic right ventricle (RV), which connects to systemic circulation
- Hemodynamic sequelae dependent on associated anomalies
- Segmental analysis & description of anatomic relationships required for complete evaluation of this complex disorder
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Bilal MS et al: Double switch procedure and surgical alternatives for the treatment of congenitally corrected transposition of the great arteries. J Card Surg. 31(4):231-6, 2016
- Han BK et al: Multi-institutional evaluation of the indications and radiation dose of functional cardiovascular computed tomography (CCT) imaging in congenital heart disease. Int J Cardiovasc Imaging. 32(2):339-46, 2016
- Rickers C et al: Is the Lecompte technique the last word on transposition of the great arteries repair for all patients? A magnetic resonance imaging study including a spiral technique two decades postoperatively. Interact Cardiovasc Thorac Surg. 2016 Jun;22(6):817-25, 2016
- Sinning C et al: Long-term course of a patient with congenital corrected transposition of the great arteries and dextrocardia - the Fisher King. Int J Cardiol. 203:436-7, 2016
- Gutberlet M et al: [Preoperative and postoperative imaging in patients with transposition of the great arteries.] Radiologe. 51(1):15-22, 2011
- Huang SC et al: Coronary artery anatomy in anatomically corrected malposition of the great arteries and their surgical implications. Eur J Cardiothorac Surg. 39(5):705-10., 2010
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
- "Congenitally corrected transposition" (misnomer)
- Discordant transposition
Definitions
- Inversion of ventricles & great arteries: Atrioventricular (AV) discordance & ventriculoarterial discordance
- Category: Dependent on associated anomalies
- Ventricular septal defect (VSD) (60-80%): Acyanotic, ↑ pulmonary vascularity
- Left ventricular outflow tract (subpulmonary) obstruction (30-50%): Cyanotic
- Dysplasia (Ebstein anomaly) with regurgitation of left-sided AV valve: Pulmonary venous congestion/hypertension
- Conduction abnormalities, heart block
- Only 1% have no associated anomalies: True congenitally corrected transposition
- Hemodynamics
- Right atrium connects via mitral valve to right-sided morphologic left ventricle (LV), which connects to pulmonary circulation
- Left atrium connects via tricuspid valve to left-sided morphologic right ventricle (RV), which connects to systemic circulation
- Hemodynamic sequelae dependent on associated anomalies
- Segmental analysis & description of anatomic relationships required for complete evaluation of this complex disorder
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Bilal MS et al: Double switch procedure and surgical alternatives for the treatment of congenitally corrected transposition of the great arteries. J Card Surg. 31(4):231-6, 2016
- Han BK et al: Multi-institutional evaluation of the indications and radiation dose of functional cardiovascular computed tomography (CCT) imaging in congenital heart disease. Int J Cardiovasc Imaging. 32(2):339-46, 2016
- Rickers C et al: Is the Lecompte technique the last word on transposition of the great arteries repair for all patients? A magnetic resonance imaging study including a spiral technique two decades postoperatively. Interact Cardiovasc Thorac Surg. 2016 Jun;22(6):817-25, 2016
- Sinning C et al: Long-term course of a patient with congenital corrected transposition of the great arteries and dextrocardia - the Fisher King. Int J Cardiol. 203:436-7, 2016
- Gutberlet M et al: [Preoperative and postoperative imaging in patients with transposition of the great arteries.] Radiologe. 51(1):15-22, 2011
- Huang SC et al: Coronary artery anatomy in anatomically corrected malposition of the great arteries and their surgical implications. Eur J Cardiothorac Surg. 39(5):705-10., 2010
