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Low-Grade Fibromyxoid Sarcoma
Catherine C. Roberts, MD
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KEY FACTS

  • Terminology

    • Imaging

      • Pathology

        • Clinical Issues

          TERMINOLOGY

          • Synonyms

            • Fibrosarcoma, fibromyxoid type; hyalinizing spindle cell tumor with giant rosettes
          • Definitions

            • Rare malignant fibrosarcoma variant found in young to middle-aged adults with deceivingly bland histologic appearance

          IMAGING

          • General Features

            • Imaging Recommendations

              • CT Findings

                • MR Findings

                  DIFFERENTIAL DIAGNOSIS

                    PATHOLOGY

                    • General Features

                      • Staging, Grading, & Classification

                        • Gross Pathologic & Surgical Features

                          • Microscopic Features

                            CLINICAL ISSUES

                            • Presentation

                              • Demographics

                                • Natural History & Prognosis

                                  • Treatment

                                    Selected References

                                    1. Yamashita H et al: Intramuscular myxoma of the buttock mimicking low-grade fibromyxoid sarcoma: diagnostic usefulness of MUC4 expression. Skeletal Radiol. 42(10):1475-9, 2013
                                    2. Hwang S et al: Imaging features of low-grade fibromyxoid sarcoma (Evans tumor). Skeletal Radiol. 41(10):1263-72, 2012
                                    3. Weiss SW et al: Fibrosarcoma. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Philadelphia: Elsevier. 316-25, 2008
                                    4. Kransdorf MJ et al: Malignant fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 2nd ed. Philadelphia: Lippincott Williams & Wilkins. 276, 2006
                                    5. Folpe A et al: Low grade fibromyxoid sarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon: IARC Press. 104-5, 2002
                                    Related Anatomy
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                                    Related Differential Diagnoses
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                                    References
                                    Tables

                                    Tables

                                    KEY FACTS

                                    • Terminology

                                      • Imaging

                                        • Pathology

                                          • Clinical Issues

                                            TERMINOLOGY

                                            • Synonyms

                                              • Fibrosarcoma, fibromyxoid type; hyalinizing spindle cell tumor with giant rosettes
                                            • Definitions

                                              • Rare malignant fibrosarcoma variant found in young to middle-aged adults with deceivingly bland histologic appearance

                                            IMAGING

                                            • General Features

                                              • Imaging Recommendations

                                                • CT Findings

                                                  • MR Findings

                                                    DIFFERENTIAL DIAGNOSIS

                                                      PATHOLOGY

                                                      • General Features

                                                        • Staging, Grading, & Classification

                                                          • Gross Pathologic & Surgical Features

                                                            • Microscopic Features

                                                              CLINICAL ISSUES

                                                              • Presentation

                                                                • Demographics

                                                                  • Natural History & Prognosis

                                                                    • Treatment

                                                                      Selected References

                                                                      1. Yamashita H et al: Intramuscular myxoma of the buttock mimicking low-grade fibromyxoid sarcoma: diagnostic usefulness of MUC4 expression. Skeletal Radiol. 42(10):1475-9, 2013
                                                                      2. Hwang S et al: Imaging features of low-grade fibromyxoid sarcoma (Evans tumor). Skeletal Radiol. 41(10):1263-72, 2012
                                                                      3. Weiss SW et al: Fibrosarcoma. In Weiss SW et al: Enzinger and Weiss' Soft Tissue Tumors. 5th ed. Philadelphia: Elsevier. 316-25, 2008
                                                                      4. Kransdorf MJ et al: Malignant fibrous and fibrohistiocytic tumors. In Kransdorf MJ et al: Imaging of Soft Tissue Tumors. 2nd ed. Philadelphia: Lippincott Williams & Wilkins. 276, 2006
                                                                      5. Folpe A et al: Low grade fibromyxoid sarcoma. In Fletcher CDM et al: World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone. Lyon: IARC Press. 104-5, 2002