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Microscopic Polyangiitis
Jorge Alberto Carrillo-Bayona, MD
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Clinical Issues

          • Diagnostic Checklist

            TERMINOLOGY

            • Abbreviations

              • Microscopic polyangiitis (MPA)
            • Definitions

              • MPA: Idiopathic autoimmune disease characterized by systemic vasculitis of small caliber vessels
                • Frequent renal (glomerulonephritis) and pulmonary (diffuse alveolar hemorrhage with capillaritis) manifestations
                • Presence of antineutrophil cytoplasmic autoantibodies specifically directed against myeloperoxidase

            IMAGING

            • Radiographic Findings

              • CT Findings

                • Imaging Recommendations

                  DIFFERENTIAL DIAGNOSIS

                    PATHOLOGY

                    • General Features

                      • Microscopic Features

                        CLINICAL ISSUES

                        • Presentation

                          • Demographics

                            • Natural History & Prognosis

                              • Treatment

                                DIAGNOSTIC CHECKLIST

                                • Consider

                                  Selected References

                                  1. Chung SA et al: Microscopic polyangiitis. Rheum Dis Clin North Am. 36(3):545-58, 2010
                                  2. Tzelepis GE et al: Prevalence and outcome of pulmonary fibrosis in microscopic polyangiitis. Eur Respir J. 36(1):116-21, 2010
                                  Related Anatomy
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                                  Related Differential Diagnoses
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                                  References
                                  Tables

                                  Tables

                                  KEY FACTS

                                  • Terminology

                                    • Imaging

                                      • Top Differential Diagnoses

                                        • Clinical Issues

                                          • Diagnostic Checklist

                                            TERMINOLOGY

                                            • Abbreviations

                                              • Microscopic polyangiitis (MPA)
                                            • Definitions

                                              • MPA: Idiopathic autoimmune disease characterized by systemic vasculitis of small caliber vessels
                                                • Frequent renal (glomerulonephritis) and pulmonary (diffuse alveolar hemorrhage with capillaritis) manifestations
                                                • Presence of antineutrophil cytoplasmic autoantibodies specifically directed against myeloperoxidase

                                            IMAGING

                                            • Radiographic Findings

                                              • CT Findings

                                                • Imaging Recommendations

                                                  DIFFERENTIAL DIAGNOSIS

                                                    PATHOLOGY

                                                    • General Features

                                                      • Microscopic Features

                                                        CLINICAL ISSUES

                                                        • Presentation

                                                          • Demographics

                                                            • Natural History & Prognosis

                                                              • Treatment

                                                                DIAGNOSTIC CHECKLIST

                                                                • Consider

                                                                  Selected References

                                                                  1. Chung SA et al: Microscopic polyangiitis. Rheum Dis Clin North Am. 36(3):545-58, 2010
                                                                  2. Tzelepis GE et al: Prevalence and outcome of pulmonary fibrosis in microscopic polyangiitis. Eur Respir J. 36(1):116-21, 2010