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Connective Tissue Disorders, Immunological Diseases, and Vasculitis
Immunological and Connective Tissue Disorders
Microscopic Polyangiitis
Microscopic Polyangiitis
Jorge Alberto Carrillo-Bayona, MD
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Microscopic polyangiitis (MPA)
Definitions
MPA: Idiopathic autoimmune disease characterized by systemic vasculitis of small caliber vessels
Frequent renal (glomerulonephritis) and pulmonary (diffuse alveolar hemorrhage with capillaritis) manifestations
Presence of antineutrophil cytoplasmic autoantibodies specifically directed against myeloperoxidase
IMAGING
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Chung SA et al: Microscopic polyangiitis. Rheum Dis Clin North Am. 36(3):545-58, 2010
Tzelepis GE et al: Prevalence and outcome of pulmonary fibrosis in microscopic polyangiitis. Eur Respir J. 36(1):116-21, 2010
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Microscopic polyangiitis (MPA)
Definitions
MPA: Idiopathic autoimmune disease characterized by systemic vasculitis of small caliber vessels
Frequent renal (glomerulonephritis) and pulmonary (diffuse alveolar hemorrhage with capillaritis) manifestations
Presence of antineutrophil cytoplasmic autoantibodies specifically directed against myeloperoxidase
IMAGING
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Chung SA et al: Microscopic polyangiitis. Rheum Dis Clin North Am. 36(3):545-58, 2010
Tzelepis GE et al: Prevalence and outcome of pulmonary fibrosis in microscopic polyangiitis. Eur Respir J. 36(1):116-21, 2010
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