Inflammatory vasculopathy (more general term indicating any vascular pathology with inflammation)
Arteritis (specifies arterial inflammation)
Angiitis (inflammation of either arteries or veins)
Definitions
Heterogeneous group of CNS disorders characterized by nonatheromatous inflammation and necrosis of blood vessel walls
Involves either arteries or veins
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Destrebecq V et al: Intracranial vessel wall MRI in cryptogenic stroke and intracranial vasculitis. J Stroke Cerebrovasc Dis. 29(5):104684, 2020
Leao DJ et al: Intracranial vessel wall imaging: applications, interpretation, and pitfalls. Clin Radiol. ePub, 2020
Salvador F: ANCA associated vasculitis. Eur J Intern Med. 74:18-28, 2020
Arun K et al: Magnetic resonance vessel wall imaging in intracranial atherosclerotic disease simulating vasculitis. Neurol India. 67(2):588-9, 2019
Castro PNP et al: Sarcoid vasculitis presenting with stroke: 3D T1 dark blood vessel wall imaging. Arq Neuropsiquiatr. 77(6):447, 2019
Corrêa DG et al: Use of high-resolution vessel wall magnetic resonance imaging in the diagnosis of temporal arteritis. Rheumatol Int. 39(8):1479-81, 2019
Corrêa DG et al: High-resolution vessel wall MR imaging as an alternative to brain biopsy. AJNR Am J Neuroradiol. 40(3):E17-8, 2019
Eiden S et al: High-resolution contrast-enhanced vessel wall imaging in patients with suspected cerebral vasculitis: prospective comparison of whole-brain 3D T1 SPACE versus 2D T1 black blood MRI at 3 Tesla. PLoS One. 14(3):e0213514, 2019
Guggenberger K et al: High-resolution compressed-sensing T1 black-blood MRI : a new multipurpose sequence in vascular neuroimaging? Clin Neuroradiol. ePub, 2019
Shulman JG et al: Infectious etiologies of stroke. Semin Neurol. 39(4):482-494, 2019
Chen CY et al: Vascular wall imaging in reversible cerebral vasoconstriction syndrome - a 3-T contrast-enhanced MRI study. J Headache Pain. 19(1):74, 2018
Van Rooij JL et al: Vessel wall enhancement on MRI in the diagnosis of primary central nervous system vasculitis. Int J Stroke. 13(9):NP24-7, 2018
Abdel Razek AA et al: Imaging spectrum of CNS vasculitis. Radiographics. 34(4):873-94, 2014
Obusez EC et al: High-resolution MRI vessel wall imaging: spatial and temporal patterns of reversible cerebral vasoconstriction syndrome and central nervous system vasculitis. AJNR Am J Neuroradiol. 35(8):1527-32, 2014
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
Inflammatory vasculopathy (more general term indicating any vascular pathology with inflammation)
Arteritis (specifies arterial inflammation)
Angiitis (inflammation of either arteries or veins)
Definitions
Heterogeneous group of CNS disorders characterized by nonatheromatous inflammation and necrosis of blood vessel walls
Involves either arteries or veins
IMAGING
General Features
CT Findings
MR Findings
Ultrasonographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Destrebecq V et al: Intracranial vessel wall MRI in cryptogenic stroke and intracranial vasculitis. J Stroke Cerebrovasc Dis. 29(5):104684, 2020
Leao DJ et al: Intracranial vessel wall imaging: applications, interpretation, and pitfalls. Clin Radiol. ePub, 2020
Salvador F: ANCA associated vasculitis. Eur J Intern Med. 74:18-28, 2020
Arun K et al: Magnetic resonance vessel wall imaging in intracranial atherosclerotic disease simulating vasculitis. Neurol India. 67(2):588-9, 2019
Castro PNP et al: Sarcoid vasculitis presenting with stroke: 3D T1 dark blood vessel wall imaging. Arq Neuropsiquiatr. 77(6):447, 2019
Corrêa DG et al: Use of high-resolution vessel wall magnetic resonance imaging in the diagnosis of temporal arteritis. Rheumatol Int. 39(8):1479-81, 2019
Corrêa DG et al: High-resolution vessel wall MR imaging as an alternative to brain biopsy. AJNR Am J Neuroradiol. 40(3):E17-8, 2019
Eiden S et al: High-resolution contrast-enhanced vessel wall imaging in patients with suspected cerebral vasculitis: prospective comparison of whole-brain 3D T1 SPACE versus 2D T1 black blood MRI at 3 Tesla. PLoS One. 14(3):e0213514, 2019
Guggenberger K et al: High-resolution compressed-sensing T1 black-blood MRI : a new multipurpose sequence in vascular neuroimaging? Clin Neuroradiol. ePub, 2019
Shulman JG et al: Infectious etiologies of stroke. Semin Neurol. 39(4):482-494, 2019
Chen CY et al: Vascular wall imaging in reversible cerebral vasoconstriction syndrome - a 3-T contrast-enhanced MRI study. J Headache Pain. 19(1):74, 2018
Van Rooij JL et al: Vessel wall enhancement on MRI in the diagnosis of primary central nervous system vasculitis. Int J Stroke. 13(9):NP24-7, 2018
Abdel Razek AA et al: Imaging spectrum of CNS vasculitis. Radiographics. 34(4):873-94, 2014
Obusez EC et al: High-resolution MRI vessel wall imaging: spatial and temporal patterns of reversible cerebral vasoconstriction syndrome and central nervous system vasculitis. AJNR Am J Neuroradiol. 35(8):1527-32, 2014
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