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KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Müllerian duct anomalies (MDA)
Synonyms
- Uterine fusion anomalies
Definitions
- Abnormal development, improper fusion, or failure of resorption of müllerian (paramesonephric) duct structures
- Müllerian agenesis or hypoplasia (class I in American Fertility Society classification system)
- Complete or segmental agenesis or variable degrees of uterovaginal hypoplasia
- Unicornuate uterus (class II)
- Partial or complete unilateral hypoplasia
- Uterus didelphys (class III)
- Duplication of uterus
- Bicornuate uterus (class IV)
- Incomplete fusion of superior uterovaginal canal
- Septate uterus (class V)
- Incomplete resorption of uterine septum
- Arcuate uterus (class VI)
- Near complete resorption of uterine septum
- Müllerian agenesis or hypoplasia (class I in American Fertility Society classification system)
- Abnormal development, improper fusion, or failure of resorption of müllerian (paramesonephric) duct structures
IMAGING
General Features
MR Findings
Ultrasonographic Findings
Radiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Schlomer B et al: Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome should be redefined as ipsilateral renal anomalies: cases of symptomatic atrophic and dysplastic kidney with ectopic ureter to obstructed hemivagina. J Pediatr Urol. 11(2):77.e1-6, 2015
- Santos XM et al: The utility of ultrasound and magnetic resonance imaging versus surgery for the characterization of müllerian anomalies in the pediatric and adolescent population. J Pediatr Adolesc Gynecol. 25(3):181-4, 2012
- Marcal L et al: Mullerian duct anomalies: MR imaging. Abdom Imaging. 36(6):756-64, 2011
- Mane SB et al: Our 10-year experience of variable Müllerian anomalies and its management. Pediatr Surg Int. 26(8):795-800, 2010
- Vallerie AM et al: Update in Müllerian anomalies: diagnosis, management, and outcomes. Curr Opin Obstet Gynecol. 22(5):381-7, 2010
- Chandler TM et al: Mullerian duct anomalies: from diagnosis to intervention. Br J Radiol. 82(984):1034-42, 2009
- Junqueira BL et al: Müllerian duct anomalies and mimics in children and adolescents: correlative intraoperative assessment with clinical imaging. Radiographics. 29(4):1085-103, 2009
- Capito C et al: Pitfalls in the diagnosis and management of obstructive uterovaginal duplication: a series of 32 cases. Pediatrics. 122(4):e891-7, 2008
- Orazi C et al: Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. sonographic and MR findings in 11 cases. Pediatr Radiol. 37(7):657-65, 2007
- Troiano RN et al: Mullerian duct anomalies: imaging and clinical issues. Radiology. 233(1):19-34, 2004
- Elford KJ et al: The forgotten female: Pediatric and adolescent gynecological concerns and their reproductive consequences. J Pediatr Adolesc Gynecol. 15(2):65-77, 2002
- Lang IM et al: MR imaging of paediatric uterovaginal anomalies. Pediatr Radiol. 29(3):163-70, 1999
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Müllerian duct anomalies (MDA)
Synonyms
- Uterine fusion anomalies
Definitions
- Abnormal development, improper fusion, or failure of resorption of müllerian (paramesonephric) duct structures
- Müllerian agenesis or hypoplasia (class I in American Fertility Society classification system)
- Complete or segmental agenesis or variable degrees of uterovaginal hypoplasia
- Unicornuate uterus (class II)
- Partial or complete unilateral hypoplasia
- Uterus didelphys (class III)
- Duplication of uterus
- Bicornuate uterus (class IV)
- Incomplete fusion of superior uterovaginal canal
- Septate uterus (class V)
- Incomplete resorption of uterine septum
- Arcuate uterus (class VI)
- Near complete resorption of uterine septum
- Müllerian agenesis or hypoplasia (class I in American Fertility Society classification system)
- Abnormal development, improper fusion, or failure of resorption of müllerian (paramesonephric) duct structures
IMAGING
General Features
MR Findings
Ultrasonographic Findings
Radiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Schlomer B et al: Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome should be redefined as ipsilateral renal anomalies: cases of symptomatic atrophic and dysplastic kidney with ectopic ureter to obstructed hemivagina. J Pediatr Urol. 11(2):77.e1-6, 2015
- Santos XM et al: The utility of ultrasound and magnetic resonance imaging versus surgery for the characterization of müllerian anomalies in the pediatric and adolescent population. J Pediatr Adolesc Gynecol. 25(3):181-4, 2012
- Marcal L et al: Mullerian duct anomalies: MR imaging. Abdom Imaging. 36(6):756-64, 2011
- Mane SB et al: Our 10-year experience of variable Müllerian anomalies and its management. Pediatr Surg Int. 26(8):795-800, 2010
- Vallerie AM et al: Update in Müllerian anomalies: diagnosis, management, and outcomes. Curr Opin Obstet Gynecol. 22(5):381-7, 2010
- Chandler TM et al: Mullerian duct anomalies: from diagnosis to intervention. Br J Radiol. 82(984):1034-42, 2009
- Junqueira BL et al: Müllerian duct anomalies and mimics in children and adolescents: correlative intraoperative assessment with clinical imaging. Radiographics. 29(4):1085-103, 2009
- Capito C et al: Pitfalls in the diagnosis and management of obstructive uterovaginal duplication: a series of 32 cases. Pediatrics. 122(4):e891-7, 2008
- Orazi C et al: Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. sonographic and MR findings in 11 cases. Pediatr Radiol. 37(7):657-65, 2007
- Troiano RN et al: Mullerian duct anomalies: imaging and clinical issues. Radiology. 233(1):19-34, 2004
- Elford KJ et al: The forgotten female: Pediatric and adolescent gynecological concerns and their reproductive consequences. J Pediatr Adolesc Gynecol. 15(2):65-77, 2002
- Lang IM et al: MR imaging of paediatric uterovaginal anomalies. Pediatr Radiol. 29(3):163-70, 1999
