link
Bookmarks
Müllerian Duct Anomalies
Sara M. O'Hara, MD, FAAP
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Log inSubscribe
0
0
2
0

KEY FACTS

  • Terminology

    • Imaging

      • Pathology

        • Clinical Issues

          • Diagnostic Checklist

            TERMINOLOGY

            • Abbreviations

              • Müllerian duct anomalies (MDA)
            • Synonyms

              • Uterine fusion anomalies
            • Definitions

              • Abnormal development, improper fusion, or failure of resorption of müllerian (paramesonephric) duct structures
                • Müllerian agenesis or hypoplasia (class I in American Fertility Society classification system)
                  • Complete or segmental agenesis or variable degrees of uterovaginal hypoplasia
                • Unicornuate uterus (class II)
                  • Partial or complete unilateral hypoplasia
                • Uterus didelphys (class III)
                  • Duplication of uterus
                • Bicornuate uterus (class IV)
                  • Incomplete fusion of superior uterovaginal canal
                • Septate uterus (class V)
                  • Incomplete resorption of uterine septum
                • Arcuate uterus (class VI)
                  • Near complete resorption of uterine septum

            IMAGING

            • General Features

              • MR Findings

                • Ultrasonographic Findings

                  • Radiographic Findings

                    • Imaging Recommendations

                      DIFFERENTIAL DIAGNOSIS

                        PATHOLOGY

                        • General Features

                          CLINICAL ISSUES

                          • Presentation

                            • Demographics

                              • Natural History & Prognosis

                                • Treatment

                                  DIAGNOSTIC CHECKLIST

                                  • Image Interpretation Pearls

                                    Selected References

                                    1. Schlomer B et al: Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome should be redefined as ipsilateral renal anomalies: cases of symptomatic atrophic and dysplastic kidney with ectopic ureter to obstructed hemivagina. J Pediatr Urol. 11(2):77.e1-6, 2015
                                    2. Santos XM et al: The utility of ultrasound and magnetic resonance imaging versus surgery for the characterization of müllerian anomalies in the pediatric and adolescent population. J Pediatr Adolesc Gynecol. 25(3):181-4, 2012
                                    3. Marcal L et al: Mullerian duct anomalies: MR imaging. Abdom Imaging. 36(6):756-64, 2011
                                    4. Mane SB et al: Our 10-year experience of variable Müllerian anomalies and its management. Pediatr Surg Int. 26(8):795-800, 2010
                                    5. Vallerie AM et al: Update in Müllerian anomalies: diagnosis, management, and outcomes. Curr Opin Obstet Gynecol. 22(5):381-7, 2010
                                    6. Chandler TM et al: Mullerian duct anomalies: from diagnosis to intervention. Br J Radiol. 82(984):1034-42, 2009
                                    7. Junqueira BL et al: Müllerian duct anomalies and mimics in children and adolescents: correlative intraoperative assessment with clinical imaging. Radiographics. 29(4):1085-103, 2009
                                    8. Capito C et al: Pitfalls in the diagnosis and management of obstructive uterovaginal duplication: a series of 32 cases. Pediatrics. 122(4):e891-7, 2008
                                    9. Orazi C et al: Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. sonographic and MR findings in 11 cases. Pediatr Radiol. 37(7):657-65, 2007
                                    10. Troiano RN et al: Mullerian duct anomalies: imaging and clinical issues. Radiology. 233(1):19-34, 2004
                                    11. Elford KJ et al: The forgotten female: Pediatric and adolescent gynecological concerns and their reproductive consequences. J Pediatr Adolesc Gynecol. 15(2):65-77, 2002
                                    12. Lang IM et al: MR imaging of paediatric uterovaginal anomalies. Pediatr Radiol. 29(3):163-70, 1999
                                    Related Anatomy
                                    Loading...
                                    Related Differential Diagnoses
                                    Loading...
                                    References
                                    Tables

                                    Tables

                                    KEY FACTS

                                    • Terminology

                                      • Imaging

                                        • Pathology

                                          • Clinical Issues

                                            • Diagnostic Checklist

                                              TERMINOLOGY

                                              • Abbreviations

                                                • Müllerian duct anomalies (MDA)
                                              • Synonyms

                                                • Uterine fusion anomalies
                                              • Definitions

                                                • Abnormal development, improper fusion, or failure of resorption of müllerian (paramesonephric) duct structures
                                                  • Müllerian agenesis or hypoplasia (class I in American Fertility Society classification system)
                                                    • Complete or segmental agenesis or variable degrees of uterovaginal hypoplasia
                                                  • Unicornuate uterus (class II)
                                                    • Partial or complete unilateral hypoplasia
                                                  • Uterus didelphys (class III)
                                                    • Duplication of uterus
                                                  • Bicornuate uterus (class IV)
                                                    • Incomplete fusion of superior uterovaginal canal
                                                  • Septate uterus (class V)
                                                    • Incomplete resorption of uterine septum
                                                  • Arcuate uterus (class VI)
                                                    • Near complete resorption of uterine septum

                                              IMAGING

                                              • General Features

                                                • MR Findings

                                                  • Ultrasonographic Findings

                                                    • Radiographic Findings

                                                      • Imaging Recommendations

                                                        DIFFERENTIAL DIAGNOSIS

                                                          PATHOLOGY

                                                          • General Features

                                                            CLINICAL ISSUES

                                                            • Presentation

                                                              • Demographics

                                                                • Natural History & Prognosis

                                                                  • Treatment

                                                                    DIAGNOSTIC CHECKLIST

                                                                    • Image Interpretation Pearls

                                                                      Selected References

                                                                      1. Schlomer B et al: Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) syndrome should be redefined as ipsilateral renal anomalies: cases of symptomatic atrophic and dysplastic kidney with ectopic ureter to obstructed hemivagina. J Pediatr Urol. 11(2):77.e1-6, 2015
                                                                      2. Santos XM et al: The utility of ultrasound and magnetic resonance imaging versus surgery for the characterization of müllerian anomalies in the pediatric and adolescent population. J Pediatr Adolesc Gynecol. 25(3):181-4, 2012
                                                                      3. Marcal L et al: Mullerian duct anomalies: MR imaging. Abdom Imaging. 36(6):756-64, 2011
                                                                      4. Mane SB et al: Our 10-year experience of variable Müllerian anomalies and its management. Pediatr Surg Int. 26(8):795-800, 2010
                                                                      5. Vallerie AM et al: Update in Müllerian anomalies: diagnosis, management, and outcomes. Curr Opin Obstet Gynecol. 22(5):381-7, 2010
                                                                      6. Chandler TM et al: Mullerian duct anomalies: from diagnosis to intervention. Br J Radiol. 82(984):1034-42, 2009
                                                                      7. Junqueira BL et al: Müllerian duct anomalies and mimics in children and adolescents: correlative intraoperative assessment with clinical imaging. Radiographics. 29(4):1085-103, 2009
                                                                      8. Capito C et al: Pitfalls in the diagnosis and management of obstructive uterovaginal duplication: a series of 32 cases. Pediatrics. 122(4):e891-7, 2008
                                                                      9. Orazi C et al: Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. sonographic and MR findings in 11 cases. Pediatr Radiol. 37(7):657-65, 2007
                                                                      10. Troiano RN et al: Mullerian duct anomalies: imaging and clinical issues. Radiology. 233(1):19-34, 2004
                                                                      11. Elford KJ et al: The forgotten female: Pediatric and adolescent gynecological concerns and their reproductive consequences. J Pediatr Adolesc Gynecol. 15(2):65-77, 2002
                                                                      12. Lang IM et al: MR imaging of paediatric uterovaginal anomalies. Pediatr Radiol. 29(3):163-70, 1999