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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Mounier-Kuhn syndrome (MKS)
Synonyms
- Tracheobronchomegaly
- Congenital tracheobronchomegaly
Definitions
- Rare disorder likely secondary to congenital defect or atrophy of elastic and smooth muscle components of trachea and mainstem bronchi with resultant significant central airway dilatation
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Krustins E: Mounier-Kuhn syndrome: a systematic analysis of 128 cases published within last 25 years. Clin Respir J. 10(1):3-10, 2016
- Payandeh J et al: A clinical classification scheme for tracheobronchomegaly (Mounier-Kuhn syndrome). Lung. 193(5):815-22, 2015
- Krustins E et al: Mounier-Kuhn syndrome or congenital tracheobronchomegaly: a literature review. Respir Med. 107(12):1822-8, 2013
- Celik B et al: Mounier-Kuhn syndrome: a rare cause of bronchial dilation. Tex Heart Inst J. 38(2):194-6, 2011
- Marom EM, Goodman PC, McAdams HP. Diffuse abnormalities of the trachea and main bronchi. AJR 2001;176;(3):713-7.
- Woodring et al: Acquired tracheomegaly in adults as a complication of diffuse pulmonary fibrosis. AJR 1989;152: 743-7.
- Shin MS et al: Tracheobronchomegaly (Mounier-Kuhn syndrome): CT diagnosis. AJR Am J Roentgenol. 150(4):777-9, 1988
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Mounier-Kuhn syndrome (MKS)
Synonyms
- Tracheobronchomegaly
- Congenital tracheobronchomegaly
Definitions
- Rare disorder likely secondary to congenital defect or atrophy of elastic and smooth muscle components of trachea and mainstem bronchi with resultant significant central airway dilatation
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Krustins E: Mounier-Kuhn syndrome: a systematic analysis of 128 cases published within last 25 years. Clin Respir J. 10(1):3-10, 2016
- Payandeh J et al: A clinical classification scheme for tracheobronchomegaly (Mounier-Kuhn syndrome). Lung. 193(5):815-22, 2015
- Krustins E et al: Mounier-Kuhn syndrome or congenital tracheobronchomegaly: a literature review. Respir Med. 107(12):1822-8, 2013
- Celik B et al: Mounier-Kuhn syndrome: a rare cause of bronchial dilation. Tex Heart Inst J. 38(2):194-6, 2011
- Marom EM, Goodman PC, McAdams HP. Diffuse abnormalities of the trachea and main bronchi. AJR 2001;176;(3):713-7.
- Woodring et al: Acquired tracheomegaly in adults as a complication of diffuse pulmonary fibrosis. AJR 1989;152: 743-7.
- Shin MS et al: Tracheobronchomegaly (Mounier-Kuhn syndrome): CT diagnosis. AJR Am J Roentgenol. 150(4):777-9, 1988
