Bookmarks
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Mounier-Kuhn syndrome (MKS)
Synonyms
- Tracheobronchomegaly
- Congenital tracheobronchomegaly
Definitions
- Defect or atrophy of elastic and smooth muscle components of trachea and mainstem bronchi with resultant significant central airway dilatation
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Satia I et al: Tracheobronchomegaly, cough and recurrent chest infection: Mounier-Kuhn syndrome. ERJ Open Res. 6(2), 2020
- Akgedik R et al: Mounier-Kuhn syndrome (tracheobronchomegaly): an analysis of eleven cases. Clin Respir J. 12(3):885-9, 2018
- Pacheco GG et al: Mounier-Kuhn syndrome mimicking lymphangioleiomyomatosis. Chest. 153(2):e19-23, 2018
- Krustins E: Mounier-Kuhn syndrome: a systematic analysis of 128 cases published within last 25 years. Clin Respir J. 10(1):3-10, 2016
- Payandeh J et al: A clinical classification scheme for tracheobronchomegaly (Mounier-Kuhn syndrome). Lung. 193(5):815-22, 2015
- Celik B et al: Mounier-Kuhn syndrome: a rare cause of bronchial dilation. Tex Heart Inst J. 38(2):194-6, 2011
Related Anatomy
Loading...
Related Differential Diagnoses
Loading...
References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Mounier-Kuhn syndrome (MKS)
Synonyms
- Tracheobronchomegaly
- Congenital tracheobronchomegaly
Definitions
- Defect or atrophy of elastic and smooth muscle components of trachea and mainstem bronchi with resultant significant central airway dilatation
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
- Satia I et al: Tracheobronchomegaly, cough and recurrent chest infection: Mounier-Kuhn syndrome. ERJ Open Res. 6(2), 2020
- Akgedik R et al: Mounier-Kuhn syndrome (tracheobronchomegaly): an analysis of eleven cases. Clin Respir J. 12(3):885-9, 2018
- Pacheco GG et al: Mounier-Kuhn syndrome mimicking lymphangioleiomyomatosis. Chest. 153(2):e19-23, 2018
- Krustins E: Mounier-Kuhn syndrome: a systematic analysis of 128 cases published within last 25 years. Clin Respir J. 10(1):3-10, 2016
- Payandeh J et al: A clinical classification scheme for tracheobronchomegaly (Mounier-Kuhn syndrome). Lung. 193(5):815-22, 2015
- Celik B et al: Mounier-Kuhn syndrome: a rare cause of bronchial dilation. Tex Heart Inst J. 38(2):194-6, 2011
