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KEY FACTS
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Multicystic dysplastic kidney (MCDK)
Synonyms
- Renal cystic dysplasia
- Dysplastic kidneys
- Potter type II (bilateral MCDK)
- Included in spectrum of congenital abnormalities of kidney and urinary tract (CAKUT)
Definitions
- Noncommunicating cysts + dysplastic renal tissue
- MCDK is essentially nonfunctioning kidney
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
MR Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Faruque A et al: Multicystic dysplastic kidney - treat each case on its merits. J Pediatr Surg. 55(11):2497-503, 2020
- Lei TY et al: Whole-exome sequencing in the evaluation of fetal congenital anomalies of the kidney and urinary tract detected by ultrasonography. Prenat Diagn. 40(10):1290-9, 2020
- Rehman S et al: Embryology, Kidney, Bladder, and Ureter 2020
- Song R et al: Sequence variants in the renin-angiotensin system genes are associated with isolated multicystic dysplastic kidney in children. Pediatr Res. ePub, 2020
- Viswanathan A et al: Screening of renal anomalies in first-degree relatives of children diagnosed with non-syndromic congenital anomalies of kidney and urinary tract. Clin Exp Nephrol. ePub, 2020
- Cassart M et al: Prenatal evaluation and postnatal follow-up of ureteral ectopic insertion in multicystic dysplastic kidneys. Fetal Diagn Ther. 45(6):373-80, 2019
- Gimpel C et al: Imaging of kidney cysts and cystic kidney diseases in children: An International Working Group consensus statement. Radiology. 290(3):769-82, 2019
- Ishiwa S et al: Association between the clinical presentation of congenital anomalies of the kidney and urinary tract (CAKUT) and gene mutations: an analysis of 66 patients at a single institution. Pediatr Nephrol. 34(8):1457-64, 2019
- Wong L et al: Diagnosis of fetal multicystic dysplastic kidney in the first trimester of pregnancy by 2-D and 3-D ultrasonography. J Obstet Gynaecol Can. 41(10):1397-98, 2019
- Balasundaram M et al: Predictors of poor neonatal outcomes in prenatally diagnosed multicystic dysplastic kidney disease. J Perinatol. 38(6):658-64, 2018
- Ji H et al: Magnetic resonance imaging for evaluation of foetal multicystic dysplastic kidney. Eur J Radiol. 108:128-32, 2018
- Maki E et al: Imaging and differential diagnosis of suprarenal masses in the fetus. J Ultrasound Med. 33(5):895-904, 2014
- Krill A et al: Evaluating compensatory hypertrophy: a growth curve specific for solitary functioning kidneys. J Urol. 188(4 Suppl):1613-7, 2012
- Hains DS et al: Management and etiology of the unilateral multicystic dysplastic kidney: a review. Pediatr Nephrol. 24(2):233-41, 2009
- Thomas DF: Prenatally diagnosed urinary tract abnormalities: long-term outcome. Semin Fetal Neonatal Med. 13(3):189-95, 2008
- Winyard P et al: Dysplastic kidneys. Semin Fetal Neonatal Med. 13(3):142-51, 2008
- Kalyoussef E et al: Segmental multicystic dysplastic kidney in children. Urology. 68(5):1121.e9-11, 2006
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References
Tables
Tables
KEY FACTS
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Multicystic dysplastic kidney (MCDK)
Synonyms
- Renal cystic dysplasia
- Dysplastic kidneys
- Potter type II (bilateral MCDK)
- Included in spectrum of congenital abnormalities of kidney and urinary tract (CAKUT)
Definitions
- Noncommunicating cysts + dysplastic renal tissue
- MCDK is essentially nonfunctioning kidney
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
MR Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Faruque A et al: Multicystic dysplastic kidney - treat each case on its merits. J Pediatr Surg. 55(11):2497-503, 2020
- Lei TY et al: Whole-exome sequencing in the evaluation of fetal congenital anomalies of the kidney and urinary tract detected by ultrasonography. Prenat Diagn. 40(10):1290-9, 2020
- Rehman S et al: Embryology, Kidney, Bladder, and Ureter 2020
- Song R et al: Sequence variants in the renin-angiotensin system genes are associated with isolated multicystic dysplastic kidney in children. Pediatr Res. ePub, 2020
- Viswanathan A et al: Screening of renal anomalies in first-degree relatives of children diagnosed with non-syndromic congenital anomalies of kidney and urinary tract. Clin Exp Nephrol. ePub, 2020
- Cassart M et al: Prenatal evaluation and postnatal follow-up of ureteral ectopic insertion in multicystic dysplastic kidneys. Fetal Diagn Ther. 45(6):373-80, 2019
- Gimpel C et al: Imaging of kidney cysts and cystic kidney diseases in children: An International Working Group consensus statement. Radiology. 290(3):769-82, 2019
- Ishiwa S et al: Association between the clinical presentation of congenital anomalies of the kidney and urinary tract (CAKUT) and gene mutations: an analysis of 66 patients at a single institution. Pediatr Nephrol. 34(8):1457-64, 2019
- Wong L et al: Diagnosis of fetal multicystic dysplastic kidney in the first trimester of pregnancy by 2-D and 3-D ultrasonography. J Obstet Gynaecol Can. 41(10):1397-98, 2019
- Balasundaram M et al: Predictors of poor neonatal outcomes in prenatally diagnosed multicystic dysplastic kidney disease. J Perinatol. 38(6):658-64, 2018
- Ji H et al: Magnetic resonance imaging for evaluation of foetal multicystic dysplastic kidney. Eur J Radiol. 108:128-32, 2018
- Maki E et al: Imaging and differential diagnosis of suprarenal masses in the fetus. J Ultrasound Med. 33(5):895-904, 2014
- Krill A et al: Evaluating compensatory hypertrophy: a growth curve specific for solitary functioning kidneys. J Urol. 188(4 Suppl):1613-7, 2012
- Hains DS et al: Management and etiology of the unilateral multicystic dysplastic kidney: a review. Pediatr Nephrol. 24(2):233-41, 2009
- Thomas DF: Prenatally diagnosed urinary tract abnormalities: long-term outcome. Semin Fetal Neonatal Med. 13(3):189-95, 2008
- Winyard P et al: Dysplastic kidneys. Semin Fetal Neonatal Med. 13(3):142-51, 2008
- Kalyoussef E et al: Segmental multicystic dysplastic kidney in children. Urology. 68(5):1121.e9-11, 2006
