Included in spectrum of congenital abnormalities of kidney and urinary tract (CAKUT)
Definitions
Noncommunicating cysts + dysplastic renal tissue
MCDK is essentially nonfunctioning kidney
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
MR Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Faruque A et al: Multicystic dysplastic kidney - treat each case on its merits. J Pediatr Surg. 55(11):2497-503, 2020
Lei TY et al: Whole-exome sequencing in the evaluation of fetal congenital anomalies of the kidney and urinary tract detected by ultrasonography. Prenat Diagn. 40(10):1290-9, 2020
Rehman S et al: Embryology, Kidney, Bladder, and Ureter 2020
Song R et al: Sequence variants in the renin-angiotensin system genes are associated with isolated multicystic dysplastic kidney in children. Pediatr Res. ePub, 2020
Viswanathan A et al: Screening of renal anomalies in first-degree relatives of children diagnosed with non-syndromic congenital anomalies of kidney and urinary tract. Clin Exp Nephrol. ePub, 2020
Cassart M et al: Prenatal evaluation and postnatal follow-up of ureteral ectopic insertion in multicystic dysplastic kidneys. Fetal Diagn Ther. 45(6):373-80, 2019
Gimpel C et al: Imaging of kidney cysts and cystic kidney diseases in children: An International Working Group consensus statement. Radiology. 290(3):769-82, 2019
Ishiwa S et al: Association between the clinical presentation of congenital anomalies of the kidney and urinary tract (CAKUT) and gene mutations: an analysis of 66 patients at a single institution. Pediatr Nephrol. 34(8):1457-64, 2019
Wong L et al: Diagnosis of fetal multicystic dysplastic kidney in the first trimester of pregnancy by 2-D and 3-D ultrasonography. J Obstet Gynaecol Can. 41(10):1397-98, 2019
Balasundaram M et al: Predictors of poor neonatal outcomes in prenatally diagnosed multicystic dysplastic kidney disease. J Perinatol. 38(6):658-64, 2018
Ji H et al: Magnetic resonance imaging for evaluation of foetal multicystic dysplastic kidney. Eur J Radiol. 108:128-32, 2018
Maki E et al: Imaging and differential diagnosis of suprarenal masses in the fetus. J Ultrasound Med. 33(5):895-904, 2014
Krill A et al: Evaluating compensatory hypertrophy: a growth curve specific for solitary functioning kidneys. J Urol. 188(4 Suppl):1613-7, 2012
Hains DS et al: Management and etiology of the unilateral multicystic dysplastic kidney: a review. Pediatr Nephrol. 24(2):233-41, 2009
Winyard P et al: Dysplastic kidneys. Semin Fetal Neonatal Med. 13(3):142-51, 2008
Kalyoussef E et al: Segmental multicystic dysplastic kidney in children. Urology. 68(5):1121.e9-11, 2006
Related Anatomy
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References
Tables
Tables
KEY FACTS
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Multicystic dysplastic kidney (MCDK)
Synonyms
Renal cystic dysplasia
Dysplastic kidneys
Potter type II (bilateral MCDK)
Included in spectrum of congenital abnormalities of kidney and urinary tract (CAKUT)
Definitions
Noncommunicating cysts + dysplastic renal tissue
MCDK is essentially nonfunctioning kidney
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
MR Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Faruque A et al: Multicystic dysplastic kidney - treat each case on its merits. J Pediatr Surg. 55(11):2497-503, 2020
Lei TY et al: Whole-exome sequencing in the evaluation of fetal congenital anomalies of the kidney and urinary tract detected by ultrasonography. Prenat Diagn. 40(10):1290-9, 2020
Rehman S et al: Embryology, Kidney, Bladder, and Ureter 2020
Song R et al: Sequence variants in the renin-angiotensin system genes are associated with isolated multicystic dysplastic kidney in children. Pediatr Res. ePub, 2020
Viswanathan A et al: Screening of renal anomalies in first-degree relatives of children diagnosed with non-syndromic congenital anomalies of kidney and urinary tract. Clin Exp Nephrol. ePub, 2020
Cassart M et al: Prenatal evaluation and postnatal follow-up of ureteral ectopic insertion in multicystic dysplastic kidneys. Fetal Diagn Ther. 45(6):373-80, 2019
Gimpel C et al: Imaging of kidney cysts and cystic kidney diseases in children: An International Working Group consensus statement. Radiology. 290(3):769-82, 2019
Ishiwa S et al: Association between the clinical presentation of congenital anomalies of the kidney and urinary tract (CAKUT) and gene mutations: an analysis of 66 patients at a single institution. Pediatr Nephrol. 34(8):1457-64, 2019
Wong L et al: Diagnosis of fetal multicystic dysplastic kidney in the first trimester of pregnancy by 2-D and 3-D ultrasonography. J Obstet Gynaecol Can. 41(10):1397-98, 2019
Balasundaram M et al: Predictors of poor neonatal outcomes in prenatally diagnosed multicystic dysplastic kidney disease. J Perinatol. 38(6):658-64, 2018
Ji H et al: Magnetic resonance imaging for evaluation of foetal multicystic dysplastic kidney. Eur J Radiol. 108:128-32, 2018
Maki E et al: Imaging and differential diagnosis of suprarenal masses in the fetus. J Ultrasound Med. 33(5):895-904, 2014
Krill A et al: Evaluating compensatory hypertrophy: a growth curve specific for solitary functioning kidneys. J Urol. 188(4 Suppl):1613-7, 2012
Hains DS et al: Management and etiology of the unilateral multicystic dysplastic kidney: a review. Pediatr Nephrol. 24(2):233-41, 2009