Inflammatory demyelinating disease distinct from multiple sclerosis (MS) and AQP4(+) neuromyelitis optica spectrum disorder (NMOSD)
Optic neuritis, transverse myelitis, AQP4-IgG seronegative inflammatory CNS demyelinating disorders with NMOSD-like phenotype; in children, acute disseminated encephalomyelitis (ADEM)
IMAGING
General Features
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Chen JJ et al: Clinical phenotype, radiological features, and treatment of myelin oligodendrocyte glycoprotein-immunoglobulin G (MOG-IgG) optic neuritis. Curr Opin Neurol. 33(1):47-54, 2020
Cobo-Calvo A et al: Clinical spectrum of central nervous system myelin oligodendrocyte glycoprotein autoimmunity in adults. Curr Opin Neurol. 32(3):459-66, 2019
Dubey D et al: Clinical, radiologic, and prognostic features of myelitis associated with myelin oligodendrocyte glycoprotein autoantibody. JAMA Neurol. 76(3):301-9, 2019
Reindl M et al: Myelin oligodendrocyte glycoprotein antibodies in neurological disease. Nat Rev Neurol. 15(2):89-102, 2018
Ungureanu A et al: Myelin oligodendrocyte glycoprotein antibodies in neuromyelitis optica spectrum disorder. Rev Neurol (Paris). 174(10):675-9, 2018
Inflammatory demyelinating disease distinct from multiple sclerosis (MS) and AQP4(+) neuromyelitis optica spectrum disorder (NMOSD)
Optic neuritis, transverse myelitis, AQP4-IgG seronegative inflammatory CNS demyelinating disorders with NMOSD-like phenotype; in children, acute disseminated encephalomyelitis (ADEM)
IMAGING
General Features
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Chen JJ et al: Clinical phenotype, radiological features, and treatment of myelin oligodendrocyte glycoprotein-immunoglobulin G (MOG-IgG) optic neuritis. Curr Opin Neurol. 33(1):47-54, 2020
Cobo-Calvo A et al: Clinical spectrum of central nervous system myelin oligodendrocyte glycoprotein autoimmunity in adults. Curr Opin Neurol. 32(3):459-66, 2019
Dubey D et al: Clinical, radiologic, and prognostic features of myelitis associated with myelin oligodendrocyte glycoprotein autoantibody. JAMA Neurol. 76(3):301-9, 2019
Reindl M et al: Myelin oligodendrocyte glycoprotein antibodies in neurological disease. Nat Rev Neurol. 15(2):89-102, 2018
Ungureanu A et al: Myelin oligodendrocyte glycoprotein antibodies in neuromyelitis optica spectrum disorder. Rev Neurol (Paris). 174(10):675-9, 2018
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